scholarly journals Tuli sensorineural pada penderita leukemia mielositik kronik

2015 ◽  
Vol 45 (2) ◽  
pp. 160
Author(s):  
Dyah Indrasworo ◽  
Hengky Wijaya Harto

Latar belakang: Leukemia adalah salah satu penyakit yang dapat menimbulkan gangguan pendengaran. Gangguan pendengaran pada penderita leukemia adalah kasus yang jarang terjadi, terutamabila gangguan pendengaran tersebut merupakan tanda awal dari proses penyakit leukemia. Tujuan:Pelaporan kasus jarang yaitu tuli sensorineural akibat leukemia mielositik kronik (LMK). Kasus:Dilaporkan laki-laki usia 26 tahun dengan tuli sensorineural bilateral yang diduga berhubungan denganLMK. Hiperviskositas dapat merupakan penyebab terjadinya gangguan pada fungsi pendengaran telingadalam. Hiperviskositas dan leukostasis pada arteri labirintin dan kapiler koklea merupakan patogenesisterjadinya tuli sensorineural pada LMK. Penatalaksanaan: Diagnosis tulisensorineural bilateralditegakkan dengan audiometri dan timpanometri sesudah pasien menjalani terapi leukapheresis. Penurunanpendengaran yang terjadi secara perlahan-lahan merupakan gejala yang terjadi akibat LMK pada kasusini. Kesimpulan: Terjadinya tuli sensorineural harus diwaspadai pada penderita LMK sebagai tandaawal dari penyakit yang mendasari. Hilangnya fungsi pendengaran bersifat permanen, sehingga dapatdisarankan pemasangan alat bantu dengar pada kasus tuli sensorineural  akibat LMK. Kata kunci : leukemia mielositik kronik, tuli sensorineural, hiperviskositas ABSTRACTBackground: Leukemia is one of the etiologic causes of hearing loss. Hearing loss in leukemia patients is rare, especially when the hearing loss presents as early sign of leukemia. Purpose: Reportinga rare case of sensorineural hearing loss in a chronic myelocytic leukemia (CML) patient. Case Report:We present a case of a 26-year-old man suffering from bilateral sensorineural hearing loss allegedlyassociated with CML. Hiperviscosity might be the cause of hearing dysfunction of the inner ear. Thepathogenesis of sensorineural hearing loss in CML patients involves hyperviscosity and leucostasis oflabyrinthine arteries and capillaries of the cochlea. Management: Bilateral sensorineural deafnessdiagnosis was confirmed by audiometry and tympanometry after patient underwent leucapheresis therapy.Gradual hearing loss was a symptom that occurred as a result of CML in this case. Conclusion: The occurrence of sensorineural hearing loss in patients with CML should be considered as an early sign of an underlying disease. Since the hearing loss is permanent, hearing aids are required in cases ofsensorineural hearing loss as a result of CML. Keywords : chronic myelocytic leukemia, sensorineural hearing loss, hyperviscosity

2019 ◽  
Vol 73 (3) ◽  
pp. 1-5 ◽  
Author(s):  
Witold Szyfter ◽  
Michał Karlik ◽  
Alicja Sekula ◽  
Simon Harris ◽  
Wojciech Gawęcki

Introduction: Surgical treatment of deafness by cochlear implants is used for more than 40 years, and during this period permanently, gradual and significant expansion of indications for this surgery has been observed. Material and methods: In our Department in the years 1994-2018 1480 cochlear implantations were performed, both in adults (647) and in children (883). In this study current indications and the rules for eligibility of patients based on 25 years of experience are presented. Results: Indications for cochlear implantation in adults are: 1) bilateral postlingual deafness, 2) bilateral sensorineural hearing loss - in pure tone audiometry > 70 dB HL (average 500-4000 Hz) and in speech audiometry in hearing aids understanding < 50% of words for the intensity of the stimulus 65 dB, in the absence of the benefits of hearing aids, 3) bilateral profound hearing loss for high frequency with good hearing for low frequency, in the absence of the benefits of hearing aids, 4) some cases of asymmetric hearing loss with intensive tinnitus in the deaf ear. An indication in children is bilateral sensorineural hearing loss > 80dB HL confirmed by hearing tests, after about 6 months of rehabilitation with the use of hearing aids. Discussion: Although cochlear implantation is used for more than 40 years, the indications for this treatment underlies constant modifications. They concern the age of eligible patients, implantation in patients with partially preserved hearing, as well as treatment for patients with difficult anatomical conditions. In many countries, bilateral implantations are commonly performed, and more and more centers recommend this treatment in the case of unilateral deafness or asymmetric hearing loss, especially with the accompanying tinnitus in the deaf ear.


2021 ◽  
pp. 019459982110273
Author(s):  
Samantha Anne ◽  
Kevin D. Brown ◽  
Donald M. Goldberg ◽  
Oliver F. Adunka ◽  
Margaret Kenna ◽  
...  

Among the various cochlear implant systems approved by the Food and Drug Administration, current labeling for pediatric usage encompasses (1) bilateral profound bilateral sensorineural hearing loss in children aged 9 to 24 months and bilateral severe to profound sensorineural hearing loss in children older than 2 years; (2) use of appropriately fitted hearing aids for 3 months (this can be waived if there is evidence of ossification); and (3) demonstration of limited progress with auditory, speech, and language development. Pediatric guidelines require children to have significantly worse speech understanding before qualifying for cochlear implantation. The early years of life have been shown to be critical for speech and language development, and auditory deprivation is especially detrimental during this crucial time. Level of evidence: 2.


Author(s):  
L. E. Golooanooa ◽  
E. V. Zhiunskaya ◽  
M. . Yu

164 patients with moderate to severe ehronie bilateral sensorineural hearing loss were asked to fill in the Glasgow hearing aid benefit profile. Its usefulness was showed in eases of diffieult hearing aid fitting.


Author(s):  
Maria Fernanda Capoani Garcia Mondelli ◽  
Aline Faure Cabreira ◽  
Izabella Lima de Matos ◽  
Maria Carolina Ferreira ◽  
Andressa Vital Rocha

Abstract Introduction Tinnitus is a disorder that affects 10 to 15% of de world's population. Sound therapy performed through hearing aids (HAs) with integrated sound generator (SG) is one of the forms of tinnitus treatment. Objective To analyze the effectiveness of four masking noises in relieving tinnitus in individuals with mild and moderate bilateral sensorineural hearing loss and their influence in speech perception. Methods The participants were 35 individuals with tinnitus and mild and moderate bilateral sensorineural hearing loss, divided into four groups. All groups underwent HA and SG adaptation, being regulated in the combined mode (HA and SG). In group 1 (G1), the white noise stimulus was applied, in group 2 (G2), pink noise was applied, in group 3 (G3), speech noise, and in group 4 (G4), the high tone was applied. All patients were subjected to the following procedures: audiological diagnosis, acuphenometry, tinnitus handicap inventory (THI), visual analogue scale (VAS), and hearing in noise test (HINT). The procedures were performed prior to and after hearing intervention, and after 3 months of use of HA and SG. Results All groups presented a statistically significant difference for the THI, VAS, and HINT pre and postintervention. In the case of the HINT, only pink noise presented a significant difference. However, in the comparation among groups there was no significant difference. Conclusion The present study made it possible to conclude that the four noises were equally effective in relieving tinnitus, with no statistically significant differences between the analyzed groups.


Author(s):  
S. I. Ereniev ◽  
O. V. Plotnikova

Biological age and rates of aging of patients with vibration disease and bilateral sensorineural hearing loss were studied. The biological age of patients exceeded the calendar age by an average of 7.36±0.36 years and the proper biological age by 10.79±0.72 years. The rate of biological aging of the examined patients was 1.14±0.08 times higher than the rate of aging of their healthy peers.


2013 ◽  
Vol 127 (7) ◽  
pp. 708-711 ◽  
Author(s):  
A C Hall ◽  
A C Leong ◽  
D Jiang ◽  
A Fitzgerald-O'Connor

AbstractBackground:Bilateral sensorineural hearing loss associated with recurrent urticarial skin lesions may be signs of underlying Muckle–Wells syndrome. Previous reports have described the hearing loss to be progressive in nature.Method:To our knowledge, this paper presents the first published case of sudden onset, bilateral sensorineural hearing loss associated with urticarial vasculitis due to underlying Muckle–Wells syndrome.Results:The patient underwent a cochlear implantation with a modest outcome.Conclusion:Cochlear implantation may help to rehabilitate sudden hearing loss associated with this condition, but early diagnosis may allow treatment with interleukin-1β inhibitors such as anakinra.


Author(s):  
Suat Kılıç ◽  
Malek H. Bouzaher ◽  
Michael S. Cohen ◽  
Judith E. C. Lieu ◽  
Margaret Kenna ◽  
...  

2007 ◽  
Vol 121 (11) ◽  
pp. 1041-1047 ◽  
Author(s):  
J J Klemens ◽  
E Mhoon ◽  
M Redleaf

AbstractIntroduction:We report our experience with bilateral, simultaneous tympanomastoidectomies and the results of an opinion survey of otologists.Methods:A chart review of 116 tympanomastoidectomies revealed 12 patients who underwent bilateral, simultaneous tympanomastoidectomies. An opinion survey generated 121 responses.Results:Of the 12 patients, none suffered any outcome which would have been avoided by staging the procedures. Twenty-three of 24 operated ears had the same or better hearing post-operatively. Of the survey respondents, 74 felt that performing bilateral, simultaneous tympanomastoidectomies was unsafe, largely because of the risk of bilateral sensorineural hearing loss.Discussion:Although bilateral, simultaneous tympanomastoidectomies carry double the risk of unilateral sensorineural hearing loss, compared with the unilateral procedure, the risk of bilateral sensorineural hearing loss is only 0.006–0.2 per cent, as derived mathematically from historical data. Respondents to the survey were mostly opposed to bilateral, simultaneous tympanomastoidectomies, but even those opposed gave indications for simultaneous procedures. This finding probably reflects an ambivalence about the theoretical risks of the operation versus the potential patient benefits. A decision tree for proceeding to the second case is presented.


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