scholarly journals Ph-negative chronic myeloproliferative neoplasm (primary myelofibrosis)– as one of the reasons of the Budd-Chiari syndrome.

2012 ◽  
Vol 4 (1) ◽  
pp. e2012047
Author(s):  
Maria Dmitrievna Sanatko
Keyword(s):  
Myeloproliferative Neoplasm ◽  
Primary Myelofibrosis ◽  
Budd Chiari Syndrome ◽  
Chiari Syndrome ◽  
Neoplasm Primary

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scholarly journals S2825 Budd-Chiari Syndrome in Setting of Pregnancy and Myeloproliferative Neoplasm

2021 ◽  
Vol 116 (1) ◽  
pp. S1174-S1174
Author(s):  
Su Min Cho ◽  
Christopher Kim ◽  
Manuel A. Garza ◽  
Ejaz Janjua
Keyword(s):  
Myeloproliferative Neoplasm ◽  
Budd Chiari Syndrome ◽  
Chiari Syndrome

scholarly journals Granulocyte whole exome sequencing and endothelial JAK2V617F in patients with JAK2V617F positive Budd-Chiari Syndrome without myeloproliferative neoplasm

2016 ◽  
Vol 180 (3) ◽  
pp. 443-445 ◽  
Author(s):  
Ricardo Helman ◽  
Welbert de O. Pereira ◽  
Luciana C. Marti ◽  
Paulo V. Campregher ◽  
Renato Davi Puga ◽  
...  
Keyword(s):  
Exome Sequencing ◽  
Whole Exome Sequencing ◽  
Myeloproliferative Neoplasm ◽  
Budd Chiari Syndrome ◽  
Whole Exome ◽  
Chiari Syndrome

Case report: A 42-year-old man with Budd-Chiari syndrome due to a myeloproliferative neoplasm

2013 ◽  
Vol 34 (S 01) ◽  
Author(s):  
K Schneider ◽  
T Müller ◽  
S Kubicka ◽  
W Blank ◽  
A Heinzmann
Keyword(s):  
Case Report ◽  
Myeloproliferative Neoplasm ◽  
Budd Chiari Syndrome ◽  
Chiari Syndrome

Pre-operative and post-operative ultrasound evaluation of Budd Chiari syndrome due to coarctation of the inferior vena cava

1988 ◽  
Vol 39 (1) ◽  
pp. 154-158 ◽  
Author(s):  
V JAYANTHI ◽  
S VICTOR ◽  
B DHALA ◽  
A GAJARAJ ◽  
N MADANAGOPALAN
Keyword(s):  
Inferior Vena Cava ◽  
Inferior Vena ◽  
Vena Cava ◽  
Budd Chiari Syndrome ◽  
Ultrasound Evaluation ◽  
Chiari Syndrome ◽  
Operative Ultrasound

Challenging Anticoagulation Management in a Patient with Budd-Chiari Syndrome and Heparin-Induced Thombocytopenia

Swiss Surgery ◽  
2001 ◽  
Vol 7 (3) ◽  
pp. 141-144
Author(s):  
Gygax ◽  
Berdat ◽  
Carrel
Keyword(s):  
Chirurgische Behandlung ◽  
Budd Chiari Syndrome ◽  
Anticoagulation Management ◽  
Chiari Syndrome ◽  
Perioperative Antikoagulation

Wir berichten über einen Patienten mit Budd-Chiari Syndrom welcher unter intravenöser Antikoagulation eine Heparin induzierte Thrombozytopenie entwickelte. Die chirurgische Behandlung bestand aus einer dorsocranialen Leberresektion mit anschliessender hepato-atrialer Anastomose unter Verwendung der extrakorporellen Zirkulation. Die perioperative Antikoagulation wurde mittels Hirudin durchgeführt. Erstaunlicherweise wurde während der Operation eine Thrombusbildung im Kardiotomie-Reservoir der Herz-Lungenmaschine beobachtet, obwohl die intraoperativ gemessene Antikoagulationsparameter (ACT und aPTT) im therapeutischen Bereich waren. Mit einem zusätzlichen Bolus Hirudin in das extrakorporelles Circuit und dank Spülung des Reservoirs konnte die Operation ohne weitere thrombotische Ereignisse zu Ende geführt werden.

Budd-Chiari syndrome due to segmental obstruction of the inferior vena cava successfully managed with endovascular stenting

MedPharmRes ◽  
2018 ◽  
Vol 2 (3) ◽  
pp. 22-26
Author(s):  
Uyen Vo ◽  
Duc Quach ◽  
Luan Dang ◽  
Thao Luu ◽  
Luan Nguyen
Keyword(s):  
Inferior Vena Cava ◽  
Inferior Vena ◽  
Laboratory Data ◽  
Transaminase Level ◽  
Vena Cava ◽  
Budd Chiari Syndrome ◽  
Endovascular Stenting ◽  
Massive Ascites ◽  
Chiari Syndrome ◽  
History Of

Budd–Chiari syndrome (BCS), a rare and life-threatening disorder due to hepatic venous outflow obstruction, is occasionally associated with hypoproteinemia. We herein report the first case of BCS with segmental obstruction of the intrahepatic portion of inferior vena cava (IVC) and hepatic veins (HVs) successfully treated by endovascular stenting in Vietnam. A 32-year-old female patient presented with a 2-month history of massive ascites and leg swelling. She refused history of oral contraceptives use. Hepatosplenomegaly without tenderness was noted. Laboratory data showed polycythemia, mild hypoalbuminemia and hypoproteinemia, slightly high total bilirubin and normal transaminase level. The serum ascites albumin gradient was 1.9 g/dL and ascitic protein level was 1.1 g/dL. The other data were normal. BCS was suspected because of the discrepancy between mild liver failure and massive ascites; and the presence of hepatosplenomegaly and polycythemia. On abdominal magnetic resonance imaging, the segmental obstruction of three HVs and IVC was 2-3 cm long without thrombus. Cavogram revealed the severe segmental stenosis of intrahepatic portion of IVC with no visualized HV and extensive collateral veins. A Protégé stent was deployed to IVC. Leg swelling and ascites were completely resolved within 3 days after stenting. During 1-year follow-up, edema was not recurred and repeated laboratory results were all normal.

Case report of Budd-Chiari syndrome

1985 ◽  
Vol 21 (3) ◽  
pp. 473
Author(s):  
J H Lee ◽  
E K Kim ◽  
Y T Ko ◽  
Y Yoon ◽  
S W Lee ◽  
...  
Keyword(s):  
Case Report ◽  
Budd Chiari Syndrome ◽  
Chiari Syndrome

Diagnosis of Budd-Chiari Syndrome by Measuring the Diameter of Azygos-hemiazygos Vein on CT

1995 ◽  
Vol 32 (5) ◽  
pp. 763
Author(s):  
Moon Gyu Lee ◽  
Yong Ho Auh ◽  
Cheol Min Park ◽  
Gi Young Ko ◽  
Sang Hee Choi
Keyword(s):  
Budd Chiari Syndrome ◽  
Hemiazygos Vein ◽  
Chiari Syndrome
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