scholarly journals Vanishing gastroschisis with jejunal atresia and extreme short bowel syndrome: A case series

2021 ◽  
Vol 10 ◽  
pp. 7
Author(s):  
Naresh Pawar ◽  
Pramila Sharma ◽  
Punit Singh Parihar ◽  
Manika Boipai
Keyword(s):  
Abdominal Wall ◽  
Short Bowel Syndrome ◽  
Anterior Abdominal Wall ◽  
Abdominal Wall Defect ◽  
Case Series ◽  
Rare Condition ◽  
Wall Defect ◽  
Short Bowel ◽  
Jejunal Atresia ◽  
Tailored Approach

Background: Vanishing gastroschisis may occur due to spontaneous partial or complete closure of anterior abdominal wall defect around the viscera, leading to small bowel ischemia and resultant entry/exit level atresia and extremely short length of the remaining bowel. The prognosis is very poor, even after aggressive surgery, and requires prolonged total parenteral nutrition. Case Series: We report two female neonates, one with closed and another with closing vanishing gastroschisis, associated with jejunal atresia and extreme short bowel syndrome. In both patients, the antenatal scans showed gastroschisis without the evidence of vanishing gastroschisis. In both neonates, palliative surgeries were done. Both patients died after a few days due to short bowel syndrome and sepsis. Conclusion: When antenatally detected gastroschisis presents with closed or closing anterior abdominal wall defect, (vanishing gastroschisis), the parents/caregivers must be counseled about the poor prognosis of this condition. A tailored approach to either palliation or aggressive therapy is essential in this rare condition.

scholarly journals Prenatal Diagnosis of a Vanishing Gastroschisis With Subsequent Neonatal Bowel Complications: A Case Study

2018 ◽  
Vol 35 (2) ◽  
pp. 158-161
Author(s):  
Katherine Vignes ◽  
A. Kinney Hiett ◽  
John M. Draus ◽  
John R. Barton
Keyword(s):  
Abdominal Wall ◽  
Short Bowel Syndrome ◽  
Abdominal Wall Defect ◽  
Neonatal Morbidity ◽  
Detection Rates ◽  
Wall Defect ◽  
Short Bowel ◽  
Antenatal Detection ◽  
Bowel Atresia

Background: Gastroschisis is a well-known birth defect in which bowel protrudes through a perforation in the fetal abdominal wall. High antenatal detection rates typically lead to good outcomes with modern neonatal treatments. Case: We describe a rare phenomenon in which gastroschisis appears to resolve antenatally, with associated bowel dilation and polyhydramnios. No evidence of an abdominal wall defect was seen at birth, but imaging was suggestive of bowel atresia. Surgical exploration showed a microcolon and most of the small bowel was absent. An extensive surgical repair was required, which resulted in short bowel syndrome. Conclusion: Gastroschisis that undergoes apparent resolution on sonography can be associated with necrosis due to strangulation of the exteriorized bowel and short bowel syndrome. This is associated with high neonatal morbidity and mortality.

DIAGNOSTIC CRITERIA FOR VISCEROABDOMINAL DISPROPORTION SYNDROME IN GASTROSCHISIS

2021 ◽  
Vol 100 (6) ◽  
pp. 53-59
Author(s):  
D.A. Plokhikh ◽  
◽  
D.E. Beglov ◽  
K.A. Kovalkov ◽  
◽  
...  
Keyword(s):  
Abdominal Wall ◽  
Analytical Study ◽  
Anterior Abdominal Wall ◽  
Abdominal Wall Defect ◽  
Intestinal Wall ◽  
Cross Sectional ◽  
Anatomical Structures ◽  
Wall Defect ◽  
Intestinal Tube ◽  
Significant Factors

The objectives of this study were to determine the frequency and search for additional criteria for the diagnosis of visceroabdominal disproportion syndrome (VADS) in newborns with gastroschisis. Materials and methods of research: prospective controlled observational cross-sectional analytical study was carried out in 61 newborns with gastroschisis, admitted from June 2009 to July 2021. To search for the most significant factors indicating the presence of VADS, the following parameters were recorded in the studied patients: the size of the defect in the anterior abdominal wall, the composition of eventrated organs, the presence of a conglomerate of intestinal loops, the diameter of the intestinal tube, the thickness of the intestinal wall, the degree of visceroabdominal disproportion (VAD). Results: VAD was detected in 50 (82%) newborns with gastroschisis. In 10 (17%) cases, VAD was mild, in 27 (44%) – moderate, and in 13 (21%) patients – severe. A moderate direct relationship was found between the size of the anterior abdominal wall defect (r=0.29, p=0.022), intestinal tube diameter (r=0.56; p=0.001) and the severity of VAD. There was a strong direct correlation between the thickness of the intestinal wall, and the frequency and severity of VAD (r=0.93, p=0.001). A direct association was found between the presence of a conglomerate of intestinal loops in the eventrated organs and the frequency of VAD (p=0.002). There was no statistically significant relationship between the number of eventrated anatomical structures with the frequency and degree of VAD (p=0.36). Conclusion: to determine VADS, it is advisable to diagnose the following pathological conditions in patients with gastroschisis: thickening of the intestinal wall, dilatation of the intestinal tube, the presence of a conglomerate of tightly welded eventrated organs, the severity of which is directly proportional to the degree of disproportion.

scholarly journals Management of Anterior Abdominal Wall Defect Using a Pedicled Tensor Fascia Lata Flap: A Case Report

2012 ◽  
Vol 2012 ◽  
pp. 1-3 ◽  
Author(s):  
K. D. Ojuka ◽  
F. Nangole ◽  
M. Ngugi
Keyword(s):  
Abdominal Wall ◽  
Road Traffic ◽  
Anterior Abdominal Wall ◽  
Abdominal Wall Defect ◽  
Fascia Lata ◽  
Tensor Fascia Lata ◽  
Wall Defect ◽  
Degloving Injury ◽  
Tensor Fascia Lata Flap ◽  
Degloving Injuries

Degloving injuries to anterior abdominal wall are rare due to the mechanism of injury. Pedicled tensor fascia lata is known to be a versatile flap with ability to reach the lower anterior abdomen. A 34-year-old man who was involved in a road traffic accident presented with degloving injury and defect at the left inguinal region, sigmoid colon injury, and scrotal bruises. At investigation, he was found to have pelvic fracture. The management consisted of colostomy and tensor fascia lata to cover the defect at reversal. Though he developed burst abdomen on fifth postoperative day, the flap healed with no complications.

scholarly journals HYDRANENCEPHALY WITH ANTERIOR ABDOMINAL WALL DEFECT- A CASE REPORT

2019 ◽  
Vol 6 (38) ◽  
pp. 2603-2605
Author(s):  
Ritu Saloi ◽  
Roonmoni Deka ◽  
Santanu Kumar Sarma
Keyword(s):  
Case Report ◽  
Abdominal Wall ◽  
Anterior Abdominal Wall ◽  
Abdominal Wall Defect ◽  
Wall Defect

scholarly journals Vaginal birth vs caesarean delivery: impact on gastroschisis anatomy in newborns (a 33-year experience)

2021 ◽  
pp. 15-19
Author(s):  
O.K. Sliepov ◽  
N.Y. Zhylka ◽  
V.L. Veselskyi ◽  
N.Y. Skrypchenko ◽  
T.V. Avramenko ◽  
...  
Keyword(s):  
Caesarean Section ◽  
Abdominal Wall ◽  
Caesarean Delivery ◽  
Anterior Abdominal Wall ◽  
Abdominal Wall Defect ◽  
Abdominal Cavity ◽  
Delivery Mode ◽  
Wall Defect ◽  
Abdominal Organs ◽  
Group I

Background. Despite the existence of numerous studies on the optimal delivery mode in gastroschisis (GS), their results remain controversial. Therefore, the presented study is focused on establishing the delivery mode impact on GS anatomy in newborns.Research objective. The study was conducted to determine the impact of the delivery mode on the features of GS anatomy in newborns.Materials and methods. A retrospective analysis of medical records of 135 pregnant women and 135 their newborns with GS born between 1987 and 2020 was conducted. All newborns are divided into 3 groups. Newborns delivered by caesarean section are included in group I (n = 80); children born exclusively naturally are included in groups II (n = 25) and III (n = 30). The following anatomical features of GS in newborns were studied: localization and size of the anterior abdominal wall defect, confluence with the abdominal cavity, the nature and frequency of the eventrated organs.Results. The size of the anterior abdominal wall defect was significantly smaller in children with GS delivered by caesarean section (3.02 ± 0.58 cm; p < 0.01) than in children born naturally (4.17 ± 0.3 cm in group II, 4.7 ± 0.29 cm in group III). The frequency of retroperitoneal organs eventration was significantly less (20.0%; p < 0.01) in caesarean delivery grope than in II and III groups (52% and 63.3%, respectively). There was no significant difference in frequency of other abdominal organs eventration, localization of the anterior abdominal wall defect and confluence with the abdominal cavity. Level of evidence – III. Conclusions. The mode of delivery affects the size of abdominal wall defect and frequency of the abdominal organs eventration in newborns with GS.

Gastroschisis-can be prevented?

2017 ◽  
Vol 6 (8) ◽  
pp. 3679
Author(s):  
Mahesweta Guru ◽  
Shefali Patil
Keyword(s):  
Abdominal Wall ◽  
Anterior Abdominal Wall ◽  
Abdominal Wall Defect ◽  
Tube Feeding ◽  
Wall Defect ◽  
Abdominal Wall Repair ◽  
Male Baby ◽  
The Right ◽  
Umbilical Cord Insertion ◽  
Ryle’S Tube

Gastroschisis is a congenital anterior abdominal wall defect, adjacent and usually to the right of the umbilical cord insertion. Gastroschisis has no covering sac and no associated syndromes. This differentiates it from an omphalocele, which usually is covered by a membranous sac. G4P3L1D2 by date 37 weeks by scan 37 weeks (17.2) Ultrasonography S/O Gastrochisis delivered a male baby of 2.4kg and was shifted to the NICU. The exposed contents were given cellulose dressing. On post-natal day 2 baby was taken for abdominal wall repair. Baby was started on Ryle’s tube feeding and was further managed by the neonatologist. 

scholarly journals Giant Omphalocele with skeletal deformities: a case report

2018 ◽  
Vol 5 (3) ◽  
pp. 1142
Author(s):  
Rajkumar M. Meshram ◽  
Amruta Phatak ◽  
Arvind Bhurke ◽  
Chetan Chaudhari
Keyword(s):  
Abdominal Wall ◽  
Anterior Abdominal Wall ◽  
Abdominal Wall Defect ◽  
Lower Limbs ◽  
Chromosomal Anomalies ◽  
Wall Defect ◽  
The Family ◽  
High Incidence ◽  
Uneventful Pregnancy ◽  
Very High

Omphalocele is an anterior abdominal wall defect at the base of the umbilical cord, with herniation of the abdominal contents which are covered by a membrane and associated with a very high incidence of structural and chromosomal anomalies including heart defect, vesical, genital or diaphragmatic malformations. A 1000 gm preterm neonate was born vaginally, to a non-consanguineously married primi mother with uneventful pregnancy. On examination baby had a large anterior abdominal wall defect covered by a thin membrane with widely open and bulging anterior fontanellae. Eyes, ears and lips were well developed but eyelids were fused. Liver, spleen and intestine were visible under a thin transparent membrane. Rib cage was formed, and ribs were palpable but lower limbs were directed posteriorly and genitalia was ambiguous. Baby was in gasping condition and died within 30 minutes after birth. Prenatal accurate diagnosis by providing adequate antenatal care and ultrasonogram would permit an opportunity to counsel the family and to prepare for optimal postnatal care.

scholarly journals Pentology of Cantrell: a rare case report with review of literature

2018 ◽  
Vol 7 (7) ◽  
pp. 2962
Author(s):  
Rajesh Tile ◽  
Supriya Jamkhandi
Keyword(s):  
Abdominal Wall ◽  
Anterior Abdominal Wall ◽  
Abdominal Wall Defect ◽  
External Genitalia ◽  
Unknown Etiology ◽  
Review Of Literature ◽  
Wall Defect ◽  
Rare Congenital Disorder ◽  
Antenatal Ultrasonography ◽  
Rare Case Report

Pentology of Cantrell a rare congenital disorder of unknown etiology consists of pentad of: defect in the diaphragm, abdominal wall defect, deficiency of the pericardium and intracardiac defects. The hallmark diagnostic findings being ectopia cordis and omphalocoele. The exact pathogenesis is not clear, and the prognosis of this lethal condition depends on the severity of anterior abdominal wall defect and associated cardiac anamoly. Antenatal ultrasonography is a reliable tool of diagnosis and allow for termination of pregnancy if done before 20weeks of pregnancy. First described by Cantrell in 1958, very few cases have been reported till now in the literature. Authors describe here a case of a neonate delivered at 32weeks of gestation weighing 2.3kg at their hospital with typical features of Cantrells’ Pentology associated with a rare interesting finding of absent external genitalia and presence of lumbar meningocoele.

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