scholarly journals Performance of Children With Donnai-Barrow Syndrome After Cochlear Implantation: A Case Report

Cureus ◽  
2022 ◽  
Author(s):  
Mohammed Yousef Alyousef ◽  
Alanoud A Abuhaimed ◽  
Dania M Alkelabi ◽  
Maram AlKahtani ◽  
Einas M Yousef ◽  
...  
2012 ◽  
Vol 126 (11) ◽  
pp. 1172-1175 ◽  
Author(s):  
Y M Feng ◽  
Y Q Wu ◽  
J Wang ◽  
S K Yin

AbstractObjective:We report the case of a successful cochlear implantation in a patient with severe cochlear hypoplasia.Case report:The outcome of cochlear implantation is generally less favourable for patients with cochlear hypoplasia than for those with a normal cochlear structure. In the reported patient, part of the electrode array was inserted into the internal auditory canal. Nevertheless, the benefits following cochlear implantation seemed to outweigh the risks for this patient.Conclusion:Cochlear hypoplasia is not necessarily a contraindication for cochlear implantation.


Author(s):  
D.J. Mawman ◽  
R.T. Ramsden ◽  
M. O�Driscoll ◽  
T. Adams ◽  
S.R. Saeed

2008 ◽  
Vol 123 (7) ◽  
pp. 811-816 ◽  
Author(s):  
A D Mace ◽  
M S Ferguson ◽  
M Offer ◽  
K Ghufoor ◽  
M J Wareing

AbstractObjective:To present the first published case of a child with bilateral profound sudden sensorineural hearing loss found in association with sickle cell anaemia, and to demonstrate the importance of early recognition, investigation and empirical treatment of sudden sensorineural hearing loss.Method:Case report and review of world literature.Case report:The authors present the case of a seven-year-old child with known sickle cell anaemia, who presented with bilateral profound sensorineural hearing loss developing over a period of five days. There was a history of ophthalmological disease in the preceding weeks, and inflammatory markers were raised. The differential diagnosis included a vaso-occlusive or inflammatory aetiology such as Cogan's syndrome, and treatment for both was instigated. Hearing thresholds did not recover, and the patient underwent cochlear implantation 12 weeks later.Conclusion:Sudden sensorineural hearing loss has a variable aetiology and is rare in children. Immediate treatment for all possible aetiologies is essential, along with targeted investigations and early referral for cochlear implantation if no recovery is demonstrated.


2011 ◽  
Vol 125 (7) ◽  
pp. 741-744 ◽  
Author(s):  
Y-M Feng ◽  
Y-Q Wu ◽  
H-Q Zhou ◽  
H-B Shi

AbstractObjective:We report a patient who underwent cochlear implantation in an ear with long-term deafness, after an acoustic neuroma had been removed surgically from the other, hitherto good ear and the cochlear nerve had subsequently been resected to relieve severe tinnitus.Method:Case report.Results:The patient could not tolerate the cochlear implant, because of a moderate headache due to the stimulation level necessary for environmental sound discrimination.Conclusion:Cochlear implantation in patients with long-term deafness should be considered carefully, even if deafness is monaural.


2012 ◽  
Vol 126 (4) ◽  
pp. 414-417 ◽  
Author(s):  
E Muzzi ◽  
P Boscolo-Rizzo ◽  
R Santarelli ◽  
M A Beltrame

AbstractObjective:To report a series of pitfalls and complications in a case of cochlear implantation.Method:Case report.Results:An 11-year-old boy affected by auditory neuropathy underwent cochlear implantation. Intra-operative assessment was apparently consistent with correct insertion of the electrode array into the cochlea. However, subsequent high resolution computed tomography revealed that the entire electrode array was curled up within the vestibule. Revision surgery was complicated by cerebrospinal fluid leakage. A straight probe was repeatedly inserted into the internal auditory canal, before conversion to a canal wall down procedure and appropriate positioning of the electrode array.Conclusion:In this case, mild anteriorisation of the facial nerve created an awkward insertion angle for the electrode array via the retro-facial route, which may have triggered the described series of adverse events.


2013 ◽  
Vol 127 (8) ◽  
pp. 802-804 ◽  
Author(s):  
M S Gürbüz ◽  
M Orakdöğen ◽  
M Z Berkman ◽  
M O Yüksel

AbstractObjective:To report a case of subdural haematoma occurring as an extremely rare and life-threatening complication of cochlear implantation, and to explore the causative association between intracranial haemorrhage and cochlear implantation surgical techniques. This association has not previously been reviewed in depth.Case report:A three-year-old boy was diagnosed with a large subdural haematoma, one week after cochlear implantation. After emergency evacuation of the haematoma, the patient made an excellent recovery and was discharged from hospital without any neurological deficit.Results:Mechanisms of injury are discussed and the literature reviewed, focusing on the possible causes of intracranial haemorrhage identified after cochlear implantation. Notably, bone drilling had been used in all reported cases, and the probable causative injury had always occurred after such drilling.Conclusion:The issue of bone drilling during cochlear implantation is raised, and alternative methods of implant housing suggested, in order to avoid intracranial haemorrhage.


2015 ◽  
Vol 129 (9) ◽  
pp. 919-922
Author(s):  
A A Alsanosi

AbstractObjective:To report a rare case of simultaneous bilateral cochlear implantation in a five-month-old child with Usher syndrome.Method:Case report.Results:A five-month-old boy with Usher syndrome and congenital profound bilateral deafness underwent simultaneous bilateral cochlear implantation. The decision to perform implantation in such a young child was based on his having a supportive family and the desire to foster his audiological development before his vision deteriorated. The subject experienced easily resolvable intra- and post-operative adverse events, and was first fitted with an externally worn audio processor four weeks after implantation. At 14 months of age, his audiological development was age-appropriate.Conclusion:Simultaneous bilateral cochlear implantation is possible, and even advisable, in children as young as five months old when performed by an experienced implantation team.


2016 ◽  
Vol 17 (4) ◽  
pp. 207-210
Author(s):  
Neelam Vaid ◽  
Joyshankar J. Jana ◽  
Ajay Kothadiya ◽  
Shweta Deshpande ◽  
Sanjay Vaid

2016 ◽  
Vol 130 (7) ◽  
pp. 691-695 ◽  
Author(s):  
W L Neo ◽  
N Durisala ◽  
E C Ho

AbstractBackground:Sensorineural hearing loss is a recognised complication of cryptococcal meningitis. The mechanism of hearing loss in patients with cryptococcal meningitis is different from that in bacterial meningitis.Case report:An immune-competent man with cryptococcal meningitis presented with sudden onset, bilateral, severe to profound sensorineural hearing loss and vestibular dysfunction. He was initially evaluated for cochlear implantation. However, he had a significant recovery; he no longer required surgery and was able to cope without a hearing aid.Conclusion:Typically, cochlear implantation is performed with some urgency in patients with hearing loss post-bacterial meningitis, because of the risk of labyrinthitis ossificans. However, this process has not been described in patients with cryptococcal meningitis. Furthermore, patients with hearing loss associated with cryptococcal meningitis have shown varying degrees of reversibility. In this case report, hearing loss from cryptococcal meningitis is compared with that from bacterial meningitis, and the need for cochlear implantation in patients with cryptococcal meningitis is discussed.


1996 ◽  
Vol 89 (10) ◽  
pp. 1195-1199 ◽  
Author(s):  
Tomo YAMAGUCHI ◽  
Tetsuo HIMI ◽  
Yasuaki HARABUCHI ◽  
Makoto HAMAMOTO ◽  
Yuji YOKOYAMA ◽  
...  

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