SYRINGOCYSTADENOMA PAPILLIFERUM – A RARE CASE REPORT

Syringocystadenoma papilliferum is a rare benign adnexal tumor of apocrine or eccrine glands. It is a childhood tumor with a relatively higher incidence at birth. The common sites of occurrence are the face and scalp. The propensity of the nodular lesion is towards the trunk, but here in our case, we present a case of nodular syringocystadenoma papilliferum of the scalp. The tumor can arise de novo or from pre-existing naevus sebaceous. The tumor rarely has a malignant course, most often basal cell carcinoma. Herein, we present an adolescent with the nodular type of syringocystadenoma papilliferum of the scalp, treated with surgical excision.

Syringocystadenoma Papilliferum of the Scalp in an Adult Male

Syringocystadenoma papilliferum is a rare skin tumour developing from eccrine or apocrine sweat gland. Though it usually appears in early life, it may occur in adult also. The clinical variants are plaques, linear and nodular. Head-neck region is affected most. Associations with naevus sebaceous, basal cell carcinoma or even squamous cell carcinoma have been described. Diagnosis is suspected clinically and confirmed by histopathology. Rapid growth, bleeding and ulceration indicate possible malignant transformation. Excision biopsy followed by reconstruction of the primary defect is the treatment of choice. Journal of Surgical Sciences (2018) Vol. 22 (2) : 139-141

Yellow or orange colouration

This chapter discusses yellow or orange discolouration of the skin, which is uncommon in children. It can occur due to accumulation of carotene in the skin, usually from infant diets containing too much carotene. Rarely, metabolic causes such as chronic renal failure or xanthomas are a cause. Xanthomas are accumulation of lipids or fat in the skin and are usually due to hereditary conditions when it manifests in children. Chronic renal failure makes the skin appear pale and yellowish mainly due to the associated anaemia and sometimes from the accumulation of metabolites in the skin. Naevi (e.g. naevus sebaceous) and rare genetic conditions (e.g. pseudoxanthoma elasticum) may exhibit a yellow/orange colour, as may palmoplantar keratoderma, as seen in some rare genetic disorders.