Left ventricular characteristics during exercise in patients after Fontan's operation for tricuspid atresia

1988 ◽  
Vol 4 (1) ◽  
pp. 34-39 ◽  
Author(s):  
Chisato Kondoh ◽  
Michiaki Hiroe ◽  
Toshio Nakanishi ◽  
Makoto Nakazawa ◽  
Seimei Nakae ◽  
...  
Keyword(s):  
Left Ventricular ◽  
Tricuspid Atresia

Absent pulmonary valve in tricuspid atresia with left ventricular outflow tract obstruction and patent arterial duct

1997 ◽  
Vol 7 (1) ◽  
pp. 94-97 ◽  
Author(s):  
Robert P. Lemke ◽  
Neils G. Giddins ◽  
Jonah N.K. Odim
Keyword(s):  
Septal Defect ◽  
Pulmonary Valve ◽  
Ventricular Outflow Tract ◽  
Left Ventricular ◽  
Tricuspid Atresia ◽  
Absent Pulmonary Valve ◽  
Arterial Duct ◽  
Left Ventricular Outflow ◽  
Patent Arterial Duct ◽  
Absent Pulmonary Valve Syndrome

AbstractWe describe a neonate with tricuspid atresia, absent pulmonary valve, right ventricular hypoplasia, small venrricular septal defect, left ventricular ourflow tract obstruction and a patent arterial duct. These finding were diagnosed by echocardiography and confirmed by cardiac catherterization and postmortem examination. This is a unique report of a functionally single ventricle variant of absent pulmonary valve syndrome and biventricular outlet obstuction.

Absent Pulmonary Valve with Tricuspid Atresia or Severe Tricuspid Stenosis: Report of Three Cases and Review of the Literature

2000 ◽  
Vol 3 (4) ◽  
pp. 353-366 ◽  
Author(s):  
Silvio Litovsky ◽  
Michael Choy ◽  
Jeanny Park ◽  
Mark Parrish ◽  
Brenda Waters ◽  
...  
Keyword(s):  
Right Ventricular ◽  
Pulmonary Valve ◽  
Left Ventricular ◽  
Tricuspid Atresia ◽  
Ventricular Free Wall ◽  
Ventricular Septum ◽  
Free Wall ◽  
Absent Pulmonary Valve ◽  
Right Ventricular Free Wall ◽  
The Right

Absence of the pulmonary valve occurs usually in association with tetralogy of Fallot and occasionally with an atrial septal defect or as an isolated lesion. Very rarely it occurs with tricuspid atresia, intact ventricular septum, and dysplasia of the right ventricular free wall and of the ventricular septum. We present the clinical, anatomic, and histologic findings of a new case, and for the first time, the data from two patients with absent pulmonary valve and severe tricuspid stenosis, who exhibited similar histologic findings. We also reviewed the clinical and anatomic data of 24 previously published cases and compared them with the new cases. In all three new cases, the myocardium of the right ventricle was very abnormal. In the two cases with tricuspid stenosis, large segments of myocardium were replaced with sinusoids and fibrous tissue. In the case with tricuspid atresia, the right ventricular free wall contained only fibroelastic tissue. The ventricular septum in all three patients showed asymmetric hypertrophy and in two of the three patients, multiple sinusoids had replaced large segments of myocardial cells. The left ventricular free wall myocardium and the walls of the great arteries were unremarkable. Our data indicate that myocardial depletion involving the right ventricular free wall and the ventricular septum and its replacement by sinusoids and fibroelastic tissue occur not only in cases of absent pulmonary valve with tricuspid atresia but also in cases of absent pulmonary valve with tricuspid stenosis. The degree of myocardial depletion varies and is more severe when the tricuspid valve is atretic.

Radionuclide assessment of left ventricular function in patients with tricuspid atresia

1981 ◽  
Vol 47 ◽  
pp. 431 ◽  
Author(s):  
Joyce R. Harder ◽  
David L. Gilday ◽  
Margaret deSouza ◽  
Robert M. Freedom ◽  
Peter M. Olley ◽  
...  
Keyword(s):  
Left Ventricular Function ◽  
Ventricular Function ◽  
Left Ventricular ◽  
Tricuspid Atresia

ASSOCIATION OF TRANSPOSITION OF THE GREAT VESSELS AND RUDIMENTARY RIGHT VENTRICLE, WITH AND WITHOUT TRICUSPID ATRESIA

PEDIATRICS ◽  
1957 ◽  
Vol 19 (5) ◽  
pp. 851-857
Author(s):  
Althea Kessler ◽  
Paul Adams
Keyword(s):  
Right Ventricle ◽  
Clinical Findings ◽  
Left Ventricular ◽  
Tricuspid Atresia ◽  
Subaortic Stenosis ◽  
P Waves ◽  
Congestive Failure ◽  
Great Vessels ◽  
Atrial Shunt ◽  
The Right

A group of eight cases with three different combinations of congenital cardiac defects but similar clinical findings has been presented. The differential diagnosis from other types of congenital heart disease has been discussed. All had transposition of the great vessels and same obstruction to aortic outflow, either subaortic stenosis or a rudimentary right ventricle from which the aorta arose. Six cases had tricuspid atresia and two had rudimentary right ventricle without tricuspid atresia. The salient features were: 1) Early congestive failure. 2) Absent or minimal cyanosis. 3) Large heart and pulmonary congestion roentgenographically. 4) Electrocardiographic findings of peaked P waves and a pattern of left ventricular hypertrophy. 5) Angiocardiographic findings of a right to left atrial shunt, failure to visualize the right ventricle, early opacification of the left ventricle and pulmonary artery, and late and inadequate opacification of a small aorta.

scholarly journals Left ventricular function in tricuspid atresia: A radionuclide study

1986 ◽  
Vol 8 (4) ◽  
pp. 916-921 ◽  
Author(s):  
Roger A. Hurwitz ◽  
Randall L. Caldwell ◽  
Donald A. Girod ◽  
Henry Wellman
Keyword(s):  
Left Ventricular Function ◽  
Ventricular Function ◽  
Left Ventricular ◽  
Tricuspid Atresia ◽  
Radionuclide Study

Assessment of left ventricular mass and volume by cross-sectional echocardiography in newborns and infants with tricuspid atresia prior to surgical intervention

1993 ◽  
Vol 3 (1) ◽  
pp. 34-38
Author(s):  
Michael Vogel ◽  
Jan Skovaranek ◽  
Konrad Bühlmeyer
Keyword(s):  
Surface Area ◽  
Left Ventricular Mass ◽  
Body Surface Area ◽  
Body Surface ◽  
Left Ventricular Volume ◽  
Ventricular Volume ◽  
Left Ventricular ◽  
Tricuspid Atresia ◽  
Ventricular Mass ◽  
Normal Left Ventricular

SummaryBecause left ventricular mass may be important in judging feasibility of Fontan type of palliation in tricuspid atresia, this study was undertaken to generate data on left ventricular mass, volume and mass to volume ratio in newborns and infants with tricuspid atresia, native pulmonary stenosis and concordant ventriculoarterial connections prior to any surgical palliation to obtain values for “normal” left ventricular dimensions in tricuspid atresia. The left ventricle was evaluated in the apical two and four chamber view. From these two perpendicular imaging planes, we calculated mass as difference between epicardial and endocardial volume x 1.05 (specific gravity of heart muscle). Mass divided by volume at end-diastole yields the index: mass to volume. Data from 23 newborns and infants with tricuspid atresia were compared to data from 30 age-matched controls with normal hearts. In both patient and control groups, growth of the left ventricle was not linear but related to the 1.4 (volume) or 1.25 (mass) power of body surface area. The equation best describing relation between left ventricular volume and body surface area in normals is volume = 60.7(body surface area)1.4−0.2 ml; in patients with tricuspid atresia volume calculates as 96.7(body surface area)1.4+0.9 ml. In relation to normal infants, infants with tricuspid atresia had a left ventricular volume of 167 (135–206)% of normal and a left ventricular mass of 163 (132–201)% of normal. Left ventricular mass assessed in normals calculates as mass = 59.9(body surface area)1.25+1.3 grams; in patients with tricuspid atresia it calculates as mass= 117.5 (body surface area)1.25−0.9 grams. The index of left ventricular mass to volume in patients with tricuspid atresia measured 1.32, not significantly different from controls, in whom this index calculates as 1.34.

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