Portosystemic Vascular Anomaly

2022 ◽  
pp. 278-286
Author(s):  
Sharon A. Center ◽  
John F. Randolph
Keyword(s):  
Vascular Anomaly

scholarly journals Hybrid treatment of fibroadipose vascular anomaly: A case report

Open Medicine ◽  
2020 ◽  
Vol 15 (1) ◽  
pp. 890-897
Author(s):  
Francesco Stillo ◽  
Federica Ruggiero ◽  
Antonio De Fiores ◽  
Rita Compagna ◽  
Bruno Amato
Keyword(s):  
Patient Satisfaction ◽  
Vascular Anomaly ◽  
Rare Type ◽  
Complete Excision ◽  
Hybrid Treatment ◽  
Constant Pain ◽  
Additional Surgery ◽  
Ethanol Embolization

AbstractBackgroundFirst identified in 2014, fibroadipose vascular anomaly (FAVA) is a very rare type of venous and lymphatic malformation. Marked by tough fibrofatty tissue in the extremities overtaking portions of the muscles, it is associated with constant pain and contracture of the affected extremity. There is a paucity of literature, and no guidelines on treatment procedure are available. This case highlights the role of hybrid treatment with primary ethanol percutaneous ethanol embolization and additional surgery for radicality in excision of FAVA lesions.Case summaryA 9-year-old girl with FAVA underwent the hybrid treatment. The achievements of complete excision, clinical response, and patient satisfaction in long-term follow-up were assessed. Following the hybrid treatment, the patient experienced significant improvement in pain. Concurrent symptoms of physical limitation, leg swelling, and skin hyperesthesia also improved. The clinical benefit, supported by postoperative physiotherapy, was well stabilized at 6-month follow-up, resulting in complete patient satisfaction at 12- and 36-month follow-ups. No major complications were encountered.ConclusionEthanol embolization plus surgery is a safe, effective, and long-term hybrid treatment of symptomatic FAVA lesions.

scholarly journals Laparoscopic treatment for celiac artery stenosis caused by median arcuate ligament compression with Adachi V type vascular anomaly: a case report

2021 ◽  
Vol 7 (1) ◽  
Author(s):  
Hiroshi Saito ◽  
Koichiro Sawada ◽  
Jyunichi Ogawa ◽  
Masashi Hashimoto ◽  
Masahiro Oshima ◽  
...  
Keyword(s):  
Epigastric Pain ◽  
Vascular Anomaly ◽  
Celiac Artery ◽  
Artery Stenosis ◽  
Laparoscopic Treatment ◽  
Median Arcuate Ligament ◽  
Case Presentation ◽  
Arcuate Ligament ◽  
Major Vascular Injury

Abstract Background Median arcuate ligament syndrome (MALS), which results from compression of the median arcuate ligament (MAL), is a rare cause of abdominal pain and weight loss. Treatment is dissection of the MAL; however, the laparoscopic procedure is not yet established and it involves the risk of major vascular injury, especially in cases with an anomaly. Case presentation A 47-year-old man was evaluated at the hospital for epigastric pain. Contrast computed tomography scan revealed stenosis of the celiac artery origin due to the MAL. An Adachi V type vascular anomaly was also observed. Laparoscopic treatment was performed to release pressure on the celiac artery. Laparoscopic ultrasonography was used to less invasively confirm the release of the MAL. Despite a concomitant Adachi V type vascular anomaly, surgery was safely performed using the laparoscopic magnification view and intraoperative ultrasonography. Follow-up ultrasonography confirmed the celiac artery stenosis has not recurred. Conclusions A rare case of MALS with an Adachi V type vascular anomaly is presented and the laparoscopic treatment is detailed.

scholarly journals Infantile haemangioma: 5-year experience at the vascular anomaly clinic

2021 ◽  
Vol 69 (1) ◽  
Author(s):  
Amr Abdelhamid AbouZeid ◽  
Iman A. Ragab ◽  
Shaimaa Abdelsattar Mohammad ◽  
Wael Ahmed Ghanem ◽  
Haytham Mohamed Nasser ◽  
...  
Keyword(s):  
Neck Region ◽  
Vascular Anomaly ◽  
Paediatric Population ◽  
Favourable Outcome ◽  
Tumour Regression ◽  
Main Body ◽  
Female Predominance ◽  
The Face ◽  
Spontaneous Involution ◽  
Infantile Haemangiomas

Abstract Background Infantile haemangiomas (IH) represent a common benign vascular tumour affecting the paediatric population. Infantile haemangiomas are characterised by a natural history differentiating it from other vascular anomalies. After a transient proliferative phase in early infancy, the tumour passes through a plateau phase before going into spontaneous involution. In this report, we tried to share our experience over the last 5 years in managing cases presenting with IH at a specialised vascular anomaly clinic. Main body of abstract This report included cases of IH who were attending the vascular anomaly clinic during the period 2015 through 2019. Data of all patients attending the clinic were retrospectively examined. Files of 103 cases with IH were available for review. The diagnosis of IH was usually straight forward owing to the typical history and characteristic findings at clinical examination. A significant female predominance was noticed. Generally, IH were more common in the head and neck region (70%). Active intervention was necessary in specific situations (eye occlusion, airway involvement, large lesions with skin ulcerations). Whenever intervention proved to be necessary, propranolol was chosen as the first line of treatment with a favourable response detected in about 90% of cases. Surgery was still a valid option (6%) for lesions amenable to resection; however, we must put in consideration that most lesions will spontaneously regress. Conclusion Infantile haemangiomas are common benign vascular tumours of infancy with relatively few complications. Cosmesis is a major concern especially for lesions affecting the face. Propranolol can induce tumour regression in most cases, and generally, a favourable outcome can be anticipated.

scholarly journals Validation of measurement scores for evaluating vascular anomaly skin lesions

2021 ◽  
Author(s):  
Shiho Yasue ◽  
Michio Ozeki ◽  
Saori Endo ◽  
Takuma Ishihara ◽  
Mana Nishiguchi‐Kurimoto ◽  
...  
Keyword(s):  
Vascular Anomaly ◽  
Skin Lesions

SUSPECTED CERVICAL SPINAL CORD VASCULAR ANOMALY IN AN AFRICAN WARTHOG (PHACOCHOERUS AFRICANUS)

2006 ◽  
Vol 37 (3) ◽  
pp. 393-396 ◽  
Author(s):  
Douglas P. Whiteside ◽  
Todd K. Shury ◽  
Sandra R. Black ◽  
Stephen Raverty
Keyword(s):  
Spinal Cord ◽  
Cervical Spinal Cord ◽  
Vascular Anomaly ◽  
Phacochoerus Africanus

Pedunculated vascular anomaly of the distal duodenum treated by endoscopic polypectomy

2013 ◽  
Vol 25 (6) ◽  
pp. 630-630
Author(s):  
Yoichiro Nuki ◽  
Motohiro Esaki ◽  
Takayuki Matsumoto
Keyword(s):  
Vascular Anomaly ◽  
Endoscopic Polypectomy

scholarly journals A vascular anomaly of the iliac artery in a patient with VATER association

2018 ◽  
Vol 6 (4) ◽  
pp. 694-697
Author(s):  
Takaaki Nakano ◽  
Tomoya Asaka ◽  
Masaaki Takemoto ◽  
Tomonori Imamura ◽  
Toshitaka Ito
Keyword(s):  
Iliac Artery ◽  
Vascular Anomaly ◽  
Vater Association

scholarly journals Peripheral Arteriovenous Malformations: Imaging and Endovascular Management Strategies

2021 ◽  
Author(s):  
Virender Malik ◽  
Harshith Kramadhari ◽  
Jawahar Rathod ◽  
Yadav W. Munde ◽  
Uday Bhanu Kovilapu
Keyword(s):  
Arteriovenous Malformation ◽  
Vascular Malformation ◽  
Management Strategies ◽  
Treatment Strategies ◽  
Vascular Anomaly ◽  
Classification Systems ◽  
Vascular Anomalies ◽  
Final Decision ◽  
Life Threatening

AbstractThe peripheral high-flow vascular malformation (HFVM) comprises arteriovenous malformation (AVM) and fistula (AVF), shows varied clinical presentation (ranging from subtle skin lesion to life-threatening congestive heart failure), and frequently poses diagnostic and therapeutic challenges. Importance of assigning a specific diagnosis to the vascular malformation cannot be overstated, as the treatment strategy is based on the type of vascular anomaly. Although the International Society for the Study of Vascular Anomalies (ISSVA) classification system is the most commonly accepted system for classifying congenital vascular anomalies in clinical practice, the Cho–Do et al classification is of utmost help in guiding optimal mode of treatment in peripheral AVM. Although transarterial approach remains the most commonly employed route for peripheral AVM embolization, the role of transvenous and direct percutaneous approach is ever increasing and the final decision on the approach depends on angioarchitecture of the AVM. In this article, we review various commonly employed classification systems for congenital vascular anomalies, and describe clinical features, imaging and treatment strategies for peripheral arteriovenous malformation (PAVM).

Hemorrhagic events associated with unfused or twig-like configuration of the Middle cerebral artery: A rare vascular anomaly with clinical relevance

2020 ◽  
pp. 159101992097043
Author(s):  
Rene Viso ◽  
Ivan Lylyk ◽  
Pablo Albiña ◽  
Javier Lundquist ◽  
Esteban Scrivano ◽  
...  
Keyword(s):  
Middle Cerebral Artery ◽  
Cerebral Artery ◽  
Clinical Relevance ◽  
Intraventricular Hemorrhage ◽  
Vascular Anomaly ◽  
Clinical Findings ◽  
Anterior Communicating Artery ◽  
Arterial Network ◽  
Ruptured Intracranial Aneurysm ◽  
Hemorrhagic Events

Introduction Twig-like middle cerebral artery configuration (Tw-MCA) is a rare and commonly misdiagnosed vascular anomaly characterized by a plexiform arterial network that replaces the normal M1 segment. The prevalence and clinical relevance of this anomaly is not fully established. Material and methods We sought to explore the prevalence of Tw-MCA in patients clinically referred to digital angiography in a single academic comprehensive endovascular center and evaluated the radiological and clinical findings among patients with hemorrhagic events. Results From 2011 to 2020, a total of 10,234 patients underwent a cerebral angiography at our institution. During this period, 9 (0.088%) Tw-MCAs were identified. Out of these, 5 patients (62.5%) were admitted due to an intracranial hemorrhage. Two patients had a ruptured intracranial aneurysm on the anterior communicating artery, one with multiple brain aneurysms; two patients presented an intraparenchymal hematoma (IPH) due to the presence of a periventricular anastomosis and one patient an intraventricular hemorrhage with unclear origin. Conclusion Tw-MCA is a very rare vascular anomaly associated with hemorrhagic events. Adequate identification of this anomaly is essential in order to avoid misdiagnosis as steno-occlusive disorders.

scholarly journals Absent Ductus Venosus Associated with Partial Liver Defect

2018 ◽  
Vol 2018 ◽  
pp. 1-4
Author(s):  
Kenji Horie ◽  
Hironori Takahashi ◽  
Daisuke Matsubara ◽  
Koichi Kataoka ◽  
Rieko Furukawa ◽  
...  
Keyword(s):  
Normal Development ◽  
Ultrasound Examination ◽  
Umbilical Vein ◽  
Vascular Anomaly ◽  
Male Infant ◽  
Ductus Venosus ◽  
Morphological Abnormality ◽  
Morgagni Hernia ◽  
The Right ◽  
Absent Ductus Venosus

Absent ductus venosus (ADV) is a rare vascular anomaly. We describe a fetus/neonate with ADV with a partial liver defect. A 41-year-old woman was referred to our institute because of fetal cardiomegaly detected by routine prenatal ultrasound, which revealed absence of ductus venosus with an umbilical vein directly draining into the right atrium, consistent with extrahepatic drainage type of ADV. She vaginally gave birth to a 3,096-gram male infant at 38 weeks of gestation. Detailed ultrasound examination revealed a defect of the hepatic rectangular leaf at half a month postnatally. He showed normal development at 1.5 years of age with the liver abnormality and a Morgagni hernia. Liver morphological abnormality should also be considered as a complication of ADV.

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