scholarly journals Stage 1 hybrid palliation for hypoplastic left heart syndrome—assessment of contemporary patterns of use: An analysis of The Society of Thoracic Surgeons Congenital Heart Surgery Database

2015 ◽  
Vol 149 (1) ◽  
pp. 195-202.e1 ◽  
Author(s):  
Tara Karamlou ◽  
David Overman ◽  
Kevin D. Hill ◽  
Amelia Wallace ◽  
Sara K. Pasquali ◽  
...  
Keyword(s):  
Hypoplastic Left Heart Syndrome ◽  
Congenital Heart ◽  
Heart Surgery ◽  
Congenital Heart Surgery ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Patterns Of Use ◽  
Stage 1 ◽  
Left Heart Syndrome ◽  
Hybrid Palliation

Hybrid Palliation in the Treatment of Hypoplastic Left Heart Syndrome

2016 ◽  
Vol 9 (1) ◽  
pp. 91-97
Author(s):  
Valerie Angela Shaffer ◽  
Patricia T. Alpert
Keyword(s):  
Primary Care ◽  
Hypoplastic Left Heart Syndrome ◽  
Nurse Practitioners ◽  
Congenital Heart ◽  
Ethical Issues ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Actual Case ◽  
Left Heart Syndrome ◽  
Hybrid Palliation

Purpose:To discuss hypoplastic left heart syndrome (HLHS) and inform nurse practitioners (NPs) working in primary care settings of this rare congenital heart deformity. This case study also examines the ethical issues advancements in medicine poses and illustrates issues NPs face when caring for a child with HLHS.Data Source:Large databases such as PubMed and CINAHL were accessed to obtain evidence-based articles for the specific heart condition and latest treatments. The data from the case was derived from an actual case, but the identity of the patient was changed to assure confidentiality.Conclusion:HLHS is a rare congenital heart deformity. Many treatment options are available, but a new treatment, the hybrid palliation, has offered new hope for many patients and their families.Implication for Practice:Patients with congenital heart conditions, including HLHS are living longer with new procedures being undertaken. The NP is likely to provide primary care to patients with congenital heart conditions, specifically HLHS. Patient care may be guided by awareness of this condition and the latest advancements in treatment.

Percutaneous Stage 1 Palliation for Hypoplastic Left Heart Syndrome

2021 ◽  
Author(s):  
Ashley M. Kiene ◽  
Benjamin Rush Waller ◽  
Christopher Knott Craig ◽  
Shyam Sathanandam
Keyword(s):  
Hypoplastic Left Heart Syndrome ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Stage 1 ◽  
Left Heart Syndrome

Anemia after Pediatric Congenital Heart Surgery

2021 ◽  
Author(s):  
Kim Anh La ◽  
Camille Jutras ◽  
George Gerardis ◽  
Rachel Richard ◽  
Geneviève Du Pont-Thibodeau
Keyword(s):  
Cardiac Surgery ◽  
Congenital Heart ◽  
Heart Surgery ◽  
Pediatric Intensive Care ◽  
Coarctation Of The Aorta ◽  
Congenital Heart Surgery ◽  
Hypoplastic Left Heart ◽  
Age At Surgery ◽  
Left Heart Syndrome ◽  
Average Hemoglobin

AbstractThe postoperative course of infants following congenital heart surgery is associated with significant blood loss and anemia. Optimal transfusion thresholds for cardiac surgery patients while in pediatric intensive care unit (PICU) remain a subject of debate. The goal of this study is to describe the epidemiology of anemia and the transfusion practices during the PICU stay of infants undergoing congenital heart surgery. A retrospective cohort study was performed in a PICU of a tertiary university-affiliated center. Infants undergoing surgery for congenital heart disease (CDH) before 6 weeks of age between February 2013 and June 2019 and who were subsequently admitted to the PICU were included. We identified 119 eligible patients. Mean age at surgery was 11 ± 7 days. Most common cardiac diagnoses were d-Transposition of the Great Arteries (55%), coarctation of the aorta (12.6%), and tetralogy of Fallot (11.8%). Mean hemoglobin level was 14.3 g/dL prior to surgery versus 12.1 g/dL at the PICU admission. Hemoglobin prior to surgery was systematically higher than hemoglobin at the PICU entry, except in infants with Hypoplastic Left Heart Syndrome. The average hemoglobin at PICU discharge was 11.7 ± 1.9 g/dL. Thirty-three (27.7%) patients were anemic at PICU discharge. Fifty-eight percent of patients received at least one red blood cell (RBC) transfusion during PICU stay. This study is the first to describe the epidemiology of anemia at PICU discharge in infants following cardiac surgery. Blood management of this distinctive and vulnerable population requires further investigation as anemia is a known risk factor for adverse neurodevelopment delays in otherwise healthy young children.

Hybrid Palliation for Hypoplastic Left Heart Syndrome: Association With Contemporary Outcomes

Circulation ◽  
2021 ◽  
Vol 144 (14) ◽  
pp. 1189-1191 ◽  
Author(s):  
Andrew B. Ho ◽  
Ines Hribernik ◽  
Daniel Shillaker ◽  
John Thomson ◽  
Abdul Salam ◽  
...  
Keyword(s):  
Hypoplastic Left Heart Syndrome ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Left Heart Syndrome ◽  
Hybrid Palliation ◽  
Syndrome Association

Hypoplastic Left Heart Syndrome: Natural History in a Geographically Defined Population

PEDIATRICS ◽  
1990 ◽  
Vol 85 (6) ◽  
pp. 977-983
Author(s):  
Cynthia D. Morris ◽  
Jacquelyn Outcalt ◽  
Victor D. Menashe
Keyword(s):  
Natural History ◽  
Hypoplastic Left Heart Syndrome ◽  
Congenital Heart ◽  
Heart Defects ◽  
Norwood Procedure ◽  
Secular Change ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
History Of ◽  
Left Heart Syndrome

Advances in surgical treatment of hypoplastic left heart syndrome with the Norwood procedure and cardiac transplantation have made essential the understanding of the natural history of hypoplastic left heart syndrome. In a geographically defined population, we ascertained the prevalence of hypoplastic left heart syndrome in children born in Oregon from 1971 through 1986. Clinical and anatomic data were extracted from the charts of the 98 affected children and the survival rate was calculated. Hypoplastic left heart syndrome occurred in 0.162 per 1000 live births in Oregon during this period. No syndrome complex was prevalent and 84% were free of other congenital malformations. However, there was an increased occurrence of congenital heart defects in first-degree relatives of probands with hypoplastic left heart syndrome. Of the affected children 15 ± 4% died on the first day of life, 70 ± 5% died within the first week, and 91 ± 3% died within 30 days. No secular change in survival occurred during the study. Palliation with the Norwood procedure was performed in 20 children. Although survival was significantly improved with this surgery (P = .01), the effect was observed principally through 30 days of life and only one of these children remains alive. Hypoplastic left heart syndrome is a lethal congenital heart defect in children and poses management and ethical dilemmas.

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