Spatial representation and attention in toddlers with Williams syndrome and Down syndrome

2003 ◽  
Vol 41 (8) ◽  
pp. 1037-1046 ◽  
Author(s):  
Janice H Brown ◽  
Mark H Johnson ◽  
Sarah J Paterson ◽  
Rick Gilmore ◽  
Elena Longhi ◽  
...  
2012 ◽  
Vol 40 (1) ◽  
pp. 106-138 ◽  
Author(s):  
YONATA LEVY ◽  
ARIELA EILAM

ABSTRACTThis is a naturalistic study of the development of language in Hebrew-speaking children with Williams syndrome (WS) and children with Down syndrome (DS), whose MLU extended from 1·0 to 4·4. Developmental curves over the entire span of data collection revealed minor differences between children with WS, children with DS, and typically developing (TD) controls of similar MLU. Development within one calendar year showed remarkable synchrony among the variables. However, age of language onset and pace of acquisition departed significantly from normal timing. It is argued that in view of the centrality of genetic timing and the network properties of cognition, normal schedules are crucial determinants of intact development. Consequently, with respect to neurodevelopmental syndromes, the so-called ‘language delay’ is indicative of deviance that is likely to impact development in critical ways.


2016 ◽  
Vol 55 ◽  
pp. 64-76 ◽  
Author(s):  
Henrik Danielsson ◽  
Lucy Henry ◽  
David Messer ◽  
Daniel P.J. Carney ◽  
Jerker Rönnberg

2020 ◽  
Vol 50 (12) ◽  
pp. 4553-4556 ◽  
Author(s):  
Hannah Harvey ◽  
Maria Ashworth ◽  
Olympia Palikara ◽  
Jo Van Herwegen

2020 ◽  
Vol 33 (5) ◽  
pp. 1080-1089 ◽  
Author(s):  
Jo Van Herwegen ◽  
Erica Ranzato ◽  
Annette Karmiloff‐Smith ◽  
Victoria Simms

2015 ◽  
Vol 59 (1) ◽  
pp. 25487 ◽  
Author(s):  
Marianne Nordstrøm ◽  
Benedicte Paus ◽  
Lene F. Andersen ◽  
Svein Olav Kolset

2016 ◽  
Vol 29 (4) ◽  
pp. 1189-1197 ◽  
Author(s):  
Karen J. Goldman ◽  
Cory Shulman ◽  
Yair Bar-Haim ◽  
Rany Abend ◽  
Jacob A. Burack

AbstractIndividuals with Williams syndrome and those with Down syndrome are both characterized by heightened social interest, although the manifestation is not always similar. Using a dot-probe task, we examined one possible source of difference: allocation of attention to facial expressions of emotion. Thirteen individuals with Williams syndrome (mean age = 19.2 years, range = 10–28.6), 20 with Down syndrome (mean age = 18.8 years, range = 12.1–26.3), and 19 typically developing children participated. The groups were matched for mental age (mean = 5.8 years). None of the groups displayed a bias to angry faces. The participants with Williams syndrome showed a selective bias toward happy faces, whereas the participants with Down syndrome behaved similarly to the typically developing participants with no such bias. Homogeneity in the direction of bias was markedly highest in the Williams syndrome group whose bias appeared to result from enhanced attention capture. They appeared to rapidly and selectively allocate attention toward positive facial expressions. The complexity of social approach behavior and the need to explore other aspects of cognition that may be implicated in this behavior in both syndromes is discussed.


1990 ◽  
Vol 2 (4) ◽  
pp. 367-391 ◽  
Author(s):  
Judy Reilly ◽  
Edward S. Klima ◽  
Ursula Bellugi

AbstractThe study of clearly identifiable patterns of atypical development can inform normal development in significant ways. Delayed or deviant development puts in high relief not only the sequence of development but also the individual components. This article presents the results of studies that compare adolescents with Williams syndrome, a rare metabolic neurodevelopmental disorder resulting in mental retardation, with cognitively matched adolescents with Down syndrome. We investigate the interaction between affect and language through storytelling. In contrast to the adolescents with Down syndrome, the Williams syndrome subjects tell coherent and complex narratives that make extensive use of affective prosody. Furthermore, stories from the Williams but not the Down subjects are infused with lexically encoded narrative evaluative devices that enrich the referential content of the stories. This contrast in expressivity between two matched atypical groups provides an unusual perspective on the underlying structure of the social cognitive domain.


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