Levoatriocardinal vein and partial anomalous pulmonary vein drainage in left-sided obstructive CHDs: diagnostic and surgical implications

AbstractWe report two cases with levoatriocardinal vein and partial anomalous pulmonary venous drainage in left-sided obstructive lesions. This association may be difficult to recognise by echocardiography. Cardiac CT and MRI were crucial to define the diagnosis and to tailor the best therapeutic option.

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Scimitar sign in the absence of anomalous pulmonary venous drainage: a case report

European Heart Journal - Case Reports ◽

10.1093/ehjcr/ytz050 ◽

2019 ◽

Vol 3 (2) ◽

Author(s):

Paulo Henrique Manso ◽

Valéria de Melo Moreira ◽

Vera Demarchi Aiello

Keyword(s):

Ct Scan ◽

Pulmonary Vein ◽

Pulmonary Veins ◽

Vena Cava ◽

Venous Drainage ◽

Scimitar Syndrome ◽

Collateral Vessel ◽

Anomalous Pulmonary Venous Drainage ◽

Anomalous Pulmonary Vein ◽

Chest X Ray

Abstract Background Scimitar syndrome consists of anomalous pulmonary vein drainage to the inferior vena cava. Its name derives from the image this anomalous pulmonary vein creates on a chest radiograph. We describe a case of normal venous pulmonary vein drainage that also presented the scimitar sign due to an aorto-collateral vessel. Case summary A 15-month-old girl presented with mild dyspnoea and fever. Control chest X-ray showed an image of cardiac dextroposition, hypoplastic right lung, and the ‘scimitar sign’. Although the transthoracic echocardiogram confirmed the initial suspicion of anomalous pulmonary venous drainage, the computed tomography (CT) scan showed normal right pulmonary veins connected to the left atrium and revealed that an aorto-collateral vessel caused the scimitar sign. Discussion Although the patient had several typical alterations of the scimitar syndrome, the pulmonary venous connection was normal, and the scimitar sign was due to an aorto-collateral vessel. It might be difficult to describe venous pulmonary connections on the basis of echocardiography, so an angio CT scan proved to be a valuable tool in this scenario.

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Turner Syndrome and Partial Anomalous Pulmonary Venous Drainage

PEDIATRICS ◽

10.1542/peds.87.4.584b ◽

1991 ◽

Vol 87 (4) ◽

pp. 584-585

Author(s):

WILLIAM C. KIRBY

Keyword(s):

Turner Syndrome ◽

Pulmonary Vein ◽

Venous Drainage ◽

Clinical Findings ◽

Turner’S Syndrome ◽

Anomalous Pulmonary Venous Drainage ◽

Venous Anomalies ◽

Anomalous Pulmonary Vein ◽

Anomalous Venous Drainage ◽

Anecdotal Information

In Reply.— We certainly agree with Dr Noonan's comments regarding the association of partial anomalous venous drainage (PAPVD) and Turner's syndrome. We also have anecdotal information about several additional patients with Turner syndrome and PAPVD. Knowledge of such patients does not define further the overall incidence of these venous anomalies in the population of patients with 45,XO karyotype. Our study demonstrates that patients with only a single anomalous pulmonary vein may have quite subtle clinical findings.

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