Atypical Partial Anomalous Pulmonary Venous Drainage of the Left Upper Pulmonary Vein Through a Compressed Vertical Vein Between the Aorta and the Pulmonary Artery

Abstract Background Scimitar syndrome consists of anomalous pulmonary vein drainage to the inferior vena cava. Its name derives from the image this anomalous pulmonary vein creates on a chest radiograph. We describe a case of normal venous pulmonary vein drainage that also presented the scimitar sign due to an aorto-collateral vessel. Case summary A 15-month-old girl presented with mild dyspnoea and fever. Control chest X-ray showed an image of cardiac dextroposition, hypoplastic right lung, and the ‘scimitar sign’. Although the transthoracic echocardiogram confirmed the initial suspicion of anomalous pulmonary venous drainage, the computed tomography (CT) scan showed normal right pulmonary veins connected to the left atrium and revealed that an aorto-collateral vessel caused the scimitar sign. Discussion Although the patient had several typical alterations of the scimitar syndrome, the pulmonary venous connection was normal, and the scimitar sign was due to an aorto-collateral vessel. It might be difficult to describe venous pulmonary connections on the basis of echocardiography, so an angio CT scan proved to be a valuable tool in this scenario.

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Partial anomalous pulmonary venous drainage of the superior left pulmonary vein into the innominate vein resulting in right ventricular failure

The American Journal of Medicine ◽

10.1016/s0002-9343(02)01137-3 ◽

2002 ◽

Vol 113 (2) ◽

pp. 168-169 ◽

Cited By ~ 11

Author(s):

Francis Q Almeda ◽

Sameer Barkatullah ◽

Sandeep Nathan ◽

Clifford J Kavinsky

Keyword(s):

Right Ventricular ◽

Pulmonary Vein ◽

Venous Drainage ◽

Right Ventricular Failure ◽

Innominate Vein ◽

Ventricular Failure ◽

Anomalous Pulmonary Venous Drainage ◽

Left Pulmonary Vein

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Partial anomalous pulmonary venous drainage of the left upper pulmonary vein

Clinical Research in Cardiology ◽

10.1007/s00392-007-0518-8 ◽

2007 ◽

Vol 96 (7) ◽

pp. 511-513 ◽

Cited By ~ 6

Author(s):

Ingo Dähnert ◽

Frank-Thomas Riede ◽

Martin Kostelka

Keyword(s):

Pulmonary Vein ◽

Venous Drainage ◽

Anomalous Pulmonary Venous Drainage

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Editorial Comment on the articles of W. Mądry and M.A. Karolczak Totally anomalous pulmonary venous drainage – supracardiac type: ultrasound assessment of anatomically determined stenosis of the vertical vein collecting pulmonary venous return and Ultrasound diagnosis of pulmonary sling with proximal stenosis of left pulmonary artery and patent arterial duct

Journal of Ultrasonography ◽

10.15557/jou.2013.0024 ◽

2013 ◽

Vol 13 (53) ◽

pp. 233-234

Author(s):

Maria Respondek‑Liberska ◽

Keyword(s):

Pulmonary Artery ◽

Editorial Comment ◽

Venous Return ◽

Venous Drainage ◽

Left Pulmonary Artery ◽

Ultrasound Diagnosis ◽

Pulmonary Sling ◽

Vertical Vein ◽

Ultrasound Assessment ◽

Patent Arterial Duct

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Turner Syndrome and Partial Anomalous Pulmonary Venous Drainage

PEDIATRICS ◽

10.1542/peds.87.4.584b ◽

1991 ◽

Vol 87 (4) ◽

pp. 584-585

Author(s):

WILLIAM C. KIRBY

Keyword(s):

Turner Syndrome ◽

Pulmonary Vein ◽

Venous Drainage ◽

Clinical Findings ◽

Turner’S Syndrome ◽

Anomalous Pulmonary Venous Drainage ◽

Venous Anomalies ◽

Anomalous Pulmonary Vein ◽

Anomalous Venous Drainage ◽

Anecdotal Information

In Reply.— We certainly agree with Dr Noonan's comments regarding the association of partial anomalous venous drainage (PAPVD) and Turner's syndrome. We also have anecdotal information about several additional patients with Turner syndrome and PAPVD. Knowledge of such patients does not define further the overall incidence of these venous anomalies in the population of patients with 45,XO karyotype. Our study demonstrates that patients with only a single anomalous pulmonary vein may have quite subtle clinical findings.

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Cross-sectional echocardiographic imaging of supracardiac total anomalous pulmonary venous drainage to a vertical vein in a patient with holt-oram syndrome

Journal of Pediatric Surgery ◽

10.1016/s0022-3468(82)80364-3 ◽

1982 ◽

Vol 17 (1) ◽

pp. 98

Author(s):

Randall W. Powell

Keyword(s):

Venous Drainage ◽

Cross Sectional ◽

Anomalous Pulmonary Venous Drainage ◽

Vertical Vein

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Coronary-Bronchial artery fistula with partial absence of a pulmonary artery: Association with partial anomalous pulmonary venous drainage

Journal of the American College of Cardiology ◽

10.1016/s0735-1097(83)80177-6 ◽

1983 ◽

Vol 2 (2) ◽

pp. 369-373 ◽

Cited By ~ 9

Author(s):

John U. Doherty ◽

Warren K. Laskey ◽

Henry Wagner ◽

Larry W. Stephenson ◽

William J. Rashkind

Keyword(s):

Pulmonary Artery ◽

Bronchial Artery ◽

Venous Drainage ◽

Anomalous Pulmonary Venous Drainage

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Partial anomalous pulmonary venous drainage repair concomitant with bilateral semilunar valve replacements and pulmonary artery reconstruction for an adult female 20 years after initial truncus arteriosus repair

Cardiology in the Young ◽

10.1017/s1047951117002736 ◽

2018 ◽

Vol 28 (3) ◽

pp. 514-515

Author(s):

Toshiyuki Iwaya ◽

Koichi Sughimoto ◽

Kagami Miyaji

Keyword(s):

Pulmonary Artery ◽

Pulmonary Valve ◽

Right Ventricular Outflow Tract ◽

Venous Drainage ◽

Ventricular Outflow Tract ◽

Anomalous Pulmonary Venous Drainage ◽

Right Pulmonary Artery ◽

Pulmonary Artery Reconstruction ◽

The Right ◽

Artery Reconstruction

AbstractWe describe the case of a 21-year-old patient who underwent repairs for multiple lesions including aortic and pulmonary valve replacements, right ventricular outflow tract reconstruction, revision of the right pulmonary artery route, and a repair of partial anomalous pulmonary venous drainage, which was diagnosed during this fourth sternotomy. For these patients with adult CHD, it is most important to address all underlying factors as much as possible at the redo surgery.

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