scholarly journals Scimitar sign in the absence of anomalous pulmonary venous drainage: a case report

2019 ◽  
Vol 3 (2) ◽  
Author(s):  
Paulo Henrique Manso ◽  
Valéria de Melo Moreira ◽  
Vera Demarchi Aiello
Keyword(s):  
Ct Scan ◽  
Pulmonary Vein ◽  
Pulmonary Veins ◽  
Vena Cava ◽  
Venous Drainage ◽  
Scimitar Syndrome ◽  
Collateral Vessel ◽  
Anomalous Pulmonary Venous Drainage ◽  
Anomalous Pulmonary Vein ◽  
Chest X Ray

Abstract Background Scimitar syndrome consists of anomalous pulmonary vein drainage to the inferior vena cava. Its name derives from the image this anomalous pulmonary vein creates on a chest radiograph. We describe a case of normal venous pulmonary vein drainage that also presented the scimitar sign due to an aorto-collateral vessel. Case summary A 15-month-old girl presented with mild dyspnoea and fever. Control chest X-ray showed an image of cardiac dextroposition, hypoplastic right lung, and the ‘scimitar sign’. Although the transthoracic echocardiogram confirmed the initial suspicion of anomalous pulmonary venous drainage, the computed tomography (CT) scan showed normal right pulmonary veins connected to the left atrium and revealed that an aorto-collateral vessel caused the scimitar sign. Discussion Although the patient had several typical alterations of the scimitar syndrome, the pulmonary venous connection was normal, and the scimitar sign was due to an aorto-collateral vessel. It might be difficult to describe venous pulmonary connections on the basis of echocardiography, so an angio CT scan proved to be a valuable tool in this scenario.

scholarly journals PARTICULARITIES OF SCIMITAR SYNDROME IN ADULT PATIENTS

2021 ◽  
Vol 9 (5) ◽  
pp. 1274-1278
Author(s):  
Soumia Faid ◽  
◽  
Amine Maliki Alaoui ◽  
Nadif Maryam ◽  
Liban Ibrahim ◽  
...  
Keyword(s):  
Inferior Vena Cava ◽  
Right Atrium ◽  
Inferior Vena ◽  
Superior Vena ◽  
Pulmonary Veins ◽  
Vena Cava ◽  
Venous Drainage ◽  
Scimitar Syndrome ◽  
Chest X Ray ◽  
The Right

Scimitar syndrome or Felsons veno-lobar syndrome is a very rare congenital disease characterized by a combination of cardiopulmonary abnormalities, including partial right-sided pulmonary venous drainage to the inferior vena cava, the inferior cavo-atrial junction, or low on the right atrium. We report the case of a 53-year-old female patient who presented with recent gradually worsening dyspnea. The diagnosis was suspected on the chest x-ray and confirmed on Cardiac echography andComputed Tomography scan that showed a wide collector gathering the three right superior pulmonary veins that joins the lower part of the superior vena cava, thus joining the right atrium while the right inferior pulmonary vein is drained into the inferior vena cava. The patient was treated surgically by performing a derivation of the right superior pulmonary venous collector to the left atrium with a tricuspid annuloplasty with a good outcome.

Venous anomalies

2017 ◽  
Author(s):  
Sara Thorne ◽  
Sarah Bowater
Keyword(s):  
Inferior Vena Cava ◽  
Superior Vena Cava ◽  
Inferior Vena ◽  
Superior Vena ◽  
Vena Cava ◽  
Venous Drainage ◽  
Scimitar Syndrome ◽  
Anomalous Pulmonary Venous Drainage ◽  
Venous Anomalies

This chapster discusses anomalies of systemic venous drainage and anomalies of pulmonary venous drainage. It discusses superior vena cava (SVC) anomalies, inferior vena cava (IVC), total anomalous pulmonary venous drainage (TAPVD), partial anomalous pulmonary venous drainage (PAPVD), and scimitar syndrome.

Turner Syndrome and Partial Anomalous Pulmonary Venous Drainage

PEDIATRICS ◽  
1991 ◽  
Vol 87 (4) ◽  
pp. 584-585
Author(s):  
WILLIAM C. KIRBY
Keyword(s):  
Turner Syndrome ◽  
Pulmonary Vein ◽  
Venous Drainage ◽  
Clinical Findings ◽  
Turner’S Syndrome ◽  
Anomalous Pulmonary Venous Drainage ◽  
Venous Anomalies ◽  
Anomalous Pulmonary Vein ◽  
Anomalous Venous Drainage ◽  
Anecdotal Information

In Reply.— We certainly agree with Dr Noonan's comments regarding the association of partial anomalous venous drainage (PAPVD) and Turner's syndrome. We also have anecdotal information about several additional patients with Turner syndrome and PAPVD. Knowledge of such patients does not define further the overall incidence of these venous anomalies in the population of patients with 45,XO karyotype. Our study demonstrates that patients with only a single anomalous pulmonary vein may have quite subtle clinical findings.

scholarly journals Turkish Sword can Track the Way of Pulmonary Vein: A Concealed Finding

2020 ◽  
Vol 44 (1) ◽  
pp. 64-67
Author(s):  
Sharmin Sultana ◽  
Naharuma Aive Hyder Chowdhury ◽  
Abdul Momen ◽  
Mohammad Sharifuzzaman
Keyword(s):  
Heart Surgery ◽  
Pulmonary Veins ◽  
Open Heart Surgery ◽  
Vena Cava ◽  
Stable Condition ◽  
Scimitar Syndrome ◽  
Incorrect Diagnosis ◽  
Anomalous Pulmonary Venous Return ◽  
Chest X Ray ◽  
Proper Diagnosis

Scimitar syndrome is an unusual developmental anomaly causing partial anomalous pulmonary venous return (right sided pulmonary veins) with left-to-right shunt at inter atrial septal level. It occurs more commonly in females, with occasional familial occurrence. The clinical presentation is variable. Patient may remain asymptomatic or may present with heart failure. The objective of this clinical case report is to highlight this unusual anomaly to avoid incorrect diagnosis. A girl of 13 years presented with unusual symptom of nausea following taking meal and a systolic murmur. At first she was diagnosed as “ASD Secundum”. But her typical “Turkish sword” feature of chest x-ray helped to identify anomalous drainage of right pulmonary veins into inferior vena cava and make the diagnosis as “Scimitar syndrome”. It is a total corrective anomaly. She was operated through open heart surgery, recovered early and discharged with a stable condition without any complication. This case illustrates the importance of thorough medical history, careful evaluation of investigation for proper diagnosis, treatment procedure and complications of a rare anomaly. Bangladesh J Child Health 2020; VOL 44 (1) :64-67

Zespół szabli tureckiej u noworodka

2019 ◽  
Vol 23 (1) ◽  
Author(s):  
Anna Piórecka-Makuła ◽  
Małgorzta Gołąbek-Dylewska ◽  
Krzysztof Godlewski ◽  
Bożena Werner
Keyword(s):  
Vena Cava ◽  
Lower Lobe ◽  
Venous Drainage ◽  
Bronchial Tree ◽  
Scimitar Syndrome ◽  
Amplatzer Device ◽  
Collateral Artery ◽  
Chest X Ray ◽  
Aortopulmonary Collaterals ◽  
The Right

Scimitar syndrome is a rare, complex congenital anomaly characterized by partial anomalous pulmonary venous drainage into the inferior vena cava with hypoplasia of the right-sided lung, pulmonary artery and bronchial tree. Frequently aortopulmonary collaterals co-occur incrising pulmonary blood flow and hence the risk of pulmonary arterial hypertension. Surgical correction remains the gold-standard therapy. The autors present the case of a 23-days-old newborn after food aspiration, presenting respiratory symptoms: tachypnoe, tachycardia, respiratory effort with the use of accessory muscles, cough and crackles. The chest X-ray revealed the right lung consolidation. Laboratory markers of inflammatory process were negative. Aspiration pneumonia was diagnosed and the treatment was introduced. Despite the newborn presented respiratory distress with radiological changes. The echocardiography was performer and scimitar syndrome was suspected. The diagnosis was confirmed during cardiac catheterization in which aortopulmonary collateral artery running to the right lower lobe was demonstrated. The vessel was embolized with Amplatzer device.

Anomalies of pulmonary venous drainage

2011 ◽  
Keyword(s):  
Pulmonary Veins ◽  
Venous Drainage ◽  
Scimitar Syndrome ◽  
Innominate Vein ◽  
Anomalous Pulmonary Venous Drainage ◽  
Systemic Vein

Total anomalous pulmonary venous drainage (TAPVD) 134Partial anomalous pulmonary venous drainage (PAPVD) 136Scimitar syndrome 138• All 4 pulmonary veins drain into R heart.• Either drain directly into RA or via a common vein into a systemic vein:•Supracardiac course draining to SVC, azygous or innominate vein....

scholarly journals Common pulmonary vein atresia

2021 ◽  
pp. 1-3
Author(s):  
Thomas Glenn ◽  
Jose Honold ◽  
Beth F. Printz ◽  
Dana Mueller
Keyword(s):  
Differential Diagnosis ◽  
High Risk ◽  
Ct Scan ◽  
Pulmonary Vein ◽  
Cardiac Ct ◽  
Pulmonary Veins ◽  
Venous Drainage ◽  
Operative Repair ◽  
Risk Of Mortality ◽  
Common Pulmonary Vein

Abstract A 4-hour-old infant with profound cyanosis on an alprostadil infusion was urgently transferred to Rady Children’s Hospital with suspected CHD. Upon arrival, urgent echocardiography was performed but could not confirm the presence of discrete pulmonary veins or pulmonary venous drainage. Given the difficulty in delineating the anatomy, a cardiac CT scan was performed and demonstrated a nearly atretic common pulmonary vein with multiple small collaterals that drained to systemic veins. Due to the high risk of mortality associated with operative repair, the decision was made to proceed with compassionate withdrawal of care. The described anatomy of common pulmonary vein atresia remains rare, and to our knowledge, fewer than 40 cases have been reported in the literature. Albeit rare, common pulmonary vein atresia should be considered in the differential diagnosis of a severely cyanotic neonate.

Levoatriocardinal vein and partial anomalous pulmonary vein drainage in left-sided obstructive CHDs: diagnostic and surgical implications

2015 ◽  
Vol 26 (4) ◽  
pp. 811-814 ◽  
Author(s):  
Davide Marini ◽  
Gabriella Agnoletti ◽  
Carlo Pace Napoleone
Keyword(s):  
Pulmonary Vein ◽  
Cardiac Ct ◽  
Therapeutic Option ◽  
Venous Drainage ◽  
Anomalous Pulmonary Venous Drainage ◽  
Anomalous Pulmonary Vein ◽  
Ct And Mri

AbstractWe report two cases with levoatriocardinal vein and partial anomalous pulmonary venous drainage in left-sided obstructive lesions. This association may be difficult to recognise by echocardiography. Cardiac CT and MRI were crucial to define the diagnosis and to tailor the best therapeutic option.

“Double whammy”: anomalous pulmonary and systemic venous drainage in a patient with scimitar syndrome

2013 ◽  
Vol 23 (5) ◽  
pp. 738-739
Author(s):  
Robert W. Elder ◽  
Brian E. Kogon ◽  
Anurag Sahu
Keyword(s):  
Inferior Vena Cava ◽  
Female Patient ◽  
Unusual Case ◽  
Inferior Vena ◽  
Pulmonary Veins ◽  
Vena Cava ◽  
Venous Drainage ◽  
Scimitar Syndrome

AbstractAnomalously draining right pulmonary veins are expected with scimitar syndrome, but systemic venous abnormalities are rare. We present an unusual case of a female patient with scimitar and an interrupted inferior vena cava.

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