Turner Syndrome and Partial Anomalous Pulmonary Venous Drainage

PEDIATRICS ◽  
1991 ◽  
Vol 87 (4) ◽  
pp. 584-585
Author(s):  
WILLIAM C. KIRBY
Keyword(s):  
Turner Syndrome ◽  
Pulmonary Vein ◽  
Venous Drainage ◽  
Clinical Findings ◽  
Turner’S Syndrome ◽  
Anomalous Pulmonary Venous Drainage ◽  
Venous Anomalies ◽  
Anomalous Pulmonary Vein ◽  
Anomalous Venous Drainage ◽  
Anecdotal Information

In Reply.— We certainly agree with Dr Noonan's comments regarding the association of partial anomalous venous drainage (PAPVD) and Turner's syndrome. We also have anecdotal information about several additional patients with Turner syndrome and PAPVD. Knowledge of such patients does not define further the overall incidence of these venous anomalies in the population of patients with 45,XO karyotype. Our study demonstrates that patients with only a single anomalous pulmonary vein may have quite subtle clinical findings.

scholarly journals Scimitar sign in the absence of anomalous pulmonary venous drainage: a case report

2019 ◽  
Vol 3 (2) ◽  
Author(s):  
Paulo Henrique Manso ◽  
Valéria de Melo Moreira ◽  
Vera Demarchi Aiello
Keyword(s):  
Ct Scan ◽  
Pulmonary Vein ◽  
Pulmonary Veins ◽  
Vena Cava ◽  
Venous Drainage ◽  
Scimitar Syndrome ◽  
Collateral Vessel ◽  
Anomalous Pulmonary Venous Drainage ◽  
Anomalous Pulmonary Vein ◽  
Chest X Ray

Abstract Background Scimitar syndrome consists of anomalous pulmonary vein drainage to the inferior vena cava. Its name derives from the image this anomalous pulmonary vein creates on a chest radiograph. We describe a case of normal venous pulmonary vein drainage that also presented the scimitar sign due to an aorto-collateral vessel. Case summary A 15-month-old girl presented with mild dyspnoea and fever. Control chest X-ray showed an image of cardiac dextroposition, hypoplastic right lung, and the ‘scimitar sign’. Although the transthoracic echocardiogram confirmed the initial suspicion of anomalous pulmonary venous drainage, the computed tomography (CT) scan showed normal right pulmonary veins connected to the left atrium and revealed that an aorto-collateral vessel caused the scimitar sign. Discussion Although the patient had several typical alterations of the scimitar syndrome, the pulmonary venous connection was normal, and the scimitar sign was due to an aorto-collateral vessel. It might be difficult to describe venous pulmonary connections on the basis of echocardiography, so an angio CT scan proved to be a valuable tool in this scenario.

Levoatriocardinal vein and partial anomalous pulmonary vein drainage in left-sided obstructive CHDs: diagnostic and surgical implications

2015 ◽  
Vol 26 (4) ◽  
pp. 811-814 ◽  
Author(s):  
Davide Marini ◽  
Gabriella Agnoletti ◽  
Carlo Pace Napoleone
Keyword(s):  
Pulmonary Vein ◽  
Cardiac Ct ◽  
Therapeutic Option ◽  
Venous Drainage ◽  
Anomalous Pulmonary Venous Drainage ◽  
Anomalous Pulmonary Vein ◽  
Ct And Mri

AbstractWe report two cases with levoatriocardinal vein and partial anomalous pulmonary venous drainage in left-sided obstructive lesions. This association may be difficult to recognise by echocardiography. Cardiac CT and MRI were crucial to define the diagnosis and to tailor the best therapeutic option.

Turner Syndrome

PEDIATRICS ◽  
1991 ◽  
Vol 87 (5) ◽  
pp. 745-745
Author(s):  
SOLOMON E. LEVIN ◽  
JEFF HARRISBERG ◽  
ALLAN KELLY
Keyword(s):  
Turner Syndrome ◽  
Coarctation Of The Aorta ◽  
Venous Drainage ◽  
Chromosomal Analysis ◽  
Anomalous Pulmonary Venous Drainage ◽  
Phenotypic Features

To the Editor.— We read with great interest the study of Moore et al1 in which they suggest that there may be a significant association of 45,X Turner syndrome and partial anomalous pulmonary venous drainage. We recently encountered a further case with this association lending support to their contention. Our patient was noted at birth to have the phenotypic features of Turner syndrome together with lymphedema. Chromosomal analysis confirmed the Karyotype 45 X0. At 4 months of age a diagnosis of coarctation of the aorta was made when her femoral pulses became impalpable.

Venous anomalies

2017 ◽  
Author(s):  
Sara Thorne ◽  
Sarah Bowater
Keyword(s):  
Inferior Vena Cava ◽  
Superior Vena Cava ◽  
Inferior Vena ◽  
Superior Vena ◽  
Vena Cava ◽  
Venous Drainage ◽  
Scimitar Syndrome ◽  
Anomalous Pulmonary Venous Drainage ◽  
Venous Anomalies

This chapster discusses anomalies of systemic venous drainage and anomalies of pulmonary venous drainage. It discusses superior vena cava (SVC) anomalies, inferior vena cava (IVC), total anomalous pulmonary venous drainage (TAPVD), partial anomalous pulmonary venous drainage (PAPVD), and scimitar syndrome.

Partial anomalous pulmonary venous drainage of the left upper pulmonary vein

2007 ◽  
Vol 96 (7) ◽  
pp. 511-513 ◽  
Author(s):  
Ingo Dähnert ◽  
Frank-Thomas Riede ◽  
Martin Kostelka
Keyword(s):  
Pulmonary Vein ◽  
Venous Drainage ◽  
Anomalous Pulmonary Venous Drainage

scholarly journals Role of Perioperative Echocardiographic in Surgical Correction of the Pulmonary Venous Anomalies

2016 ◽  
Vol 4 (1) ◽  
pp. 19-26
Author(s):  
Sunder Negi
Keyword(s):  
Pulmonary Vein ◽  
Superior Vena Cava ◽  
Superior Vena ◽  
Vena Cava ◽  
Venous Drainage ◽  
Surgical Correction ◽  
Patch Repair ◽  
Venous Anomalies ◽  
The Right

ABSTRACT Anomalous pulmonary venous drainage is the anomalous drainage of one or more than one pulmonary vein draining into right atrium, superior vena cava, inferior vena cava, coronary sinus, or innominate vein. Right-sided pulmonary vein anomalous drainage is usually associated with sinus venosus type atrial septal defect. Pericardial patch repair and rerouting of the right pulmonary vein are commonly performed operations for such cases. These operations involve a risk of obstruction to the flow of superior vena cava or rerouted pulmonary vein in the postoperative period. The defects are well visualized on the transesophageal echocardiography (TEE). We are reporting three cases operated for anomalous drainage of right-sided pulmonary vein, highlighting the perioperative echocardiographic features. How to cite this article Kumar A, Dutta V, Negi S, Puri GD. Role of Perioperative Echocardiographic in Surgical Correction of the Pulmonary Venous Anomalies. J Perioper Echocardiogr 2016;4(1):19-26.

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