scholarly journals Surgical Treatment of Ebstein's Anomaly

2017 ◽  
Vol 65 (08) ◽  
pp. 639-648 ◽  
Author(s):  
Rüdiger Lange ◽  
Melchior Burri
Keyword(s):  
Surgical Treatment ◽  
Right Ventricular ◽  
Surgical Repair ◽  
Surgical Techniques ◽  
Right Ventricular Failure ◽  
Ebstein’S Anomaly ◽  
Ventricular Failure ◽  
Ebstein's Anomaly ◽  
History Of ◽  
Surgical Options

AbstractSurgical repair of the tricuspid valve is a milestone in the medical history of patients with Ebstein's anomaly. The timely alleviation of the insufficiency has an important impact on the prognosis. In this review, we describe features of the disease relevant to surgical correction and the evolution of surgical techniques over six decades. We compare the results of different repair and replacement techniques. Additionally, we discuss concomitant antiarrhythmic surgery and bailout strategies for postoperative right ventricular failure. Finally, we review the surgical options in symptomatic neonates with Ebstein's disease.

scholarly journals Management of Pregnancy in 31-Year-Old Woman with Persistent Atrial Flutter After Cone Reconstruction for Ebstein’s Anomaly

2020 ◽  
Vol 1 (1) ◽  
pp. 17
Author(s):  
Eliana Susilowati
Keyword(s):  
Heart Disease ◽  
Atrial Flutter ◽  
Tricuspid Regurgitation ◽  
Signs And Symptoms ◽  
Right Ventricular Failure ◽  
Ebstein’S Anomaly ◽  
Ventricular Failure ◽  
Ebstein Anomaly ◽  
Ebstein's Anomaly ◽  
History Of

There is a growing number of mothers suffering innate heart disease which could potentially risk their gestation period. Ebstein’s anomaly refers to a rare innate disease in the heart which accounts for less than 1% of most cases of innate heart disease, and only 5% of the patients surviving beyond 50 years of age. Cone reconstruction (CR) is an option for the repairment of tricuspid valve in patients with Ebstein anomaly. However, persistent arrhytmia, such as AFL, is possible to occur after CR. This case report aims to opt suitable pregnancy management of patients with persistent atrial flutter (AFL) after Cone reconstruction for Ebstein’s Anomaly. We report a 31 year-old woman who consulted for pregnancy planning due to history of Ebstein’s Anomaly, and had undergone successful cone reconstruction. No recorded history of AFL is reported. Physical examination finding was tricuspid regurgitation murmur without signs and symptoms of right ventricular failure. Electrocardiography showed counter-clockwise typical AFL. Echocardiography finding demonstrated post Cone reconstruction (CR), mild tricuspid regurgitation, and EF of 76%.

scholarly journals Preoperative predictability of right ventricular failure following surgery for Ebstein’s anomaly

2018 ◽  
Vol 55 (6) ◽  
pp. 1187-1193 ◽  
Author(s):  
Kariem Mrad Agua ◽  
Melchior Burri ◽  
Julie Cleuziou ◽  
Elisabeth Beran ◽  
Christian Meierhofer ◽  
...  
Keyword(s):  
Right Ventricular ◽  
Right Ventricular Failure ◽  
Ebstein’S Anomaly ◽  
Ventricular Failure ◽  
Ebstein's Anomaly

Ebstein's Anomaly: Surgical Treatment with Tricuspid Replacement Without Right Ventricular Plication

1981 ◽  
Vol 31 (3) ◽  
pp. 277-280 ◽  
Author(s):  
José M. Caralps ◽  
Alejandro Aris ◽  
José O. Bonnin ◽  
Heriberto Solanes ◽  
Miguel Torner
Keyword(s):  
Surgical Treatment ◽  
Right Ventricular ◽  
Ebstein’S Anomaly ◽  
Ebstein's Anomaly

Dealing with Ebstein's anomaly

2013 ◽  
Vol 24 (2) ◽  
pp. 191-200 ◽  
Author(s):  
Lianne M. Geerdink ◽  
Livia Kapusta
Keyword(s):  
Diagnostic Methods ◽  
Ebstein’S Anomaly ◽  
Common Disease ◽  
Surgical Interventions ◽  
Ebstein's Anomaly ◽  
Current Classification ◽  
History Of ◽  
Surgical Options ◽  
Symptoms And Signs

AbstractEbstein's anomaly is a complex congenital disorder of the tricuspid valve. Presentation in neonatal life and (early) childhood is common. Disease severity and clinical features vary widely and require a patient-tailored treatment. In this review, we describe the natural history of children and adolescents with Ebstein's anomaly, including symptoms and signs presenting at diagnosis. Current classification strategies of Ebstein's anomaly are discussed. We report on diagnostic methods for establishing the severity of disease that might enhance decision on the timing of surgical intervention. Furthermore, we describe different surgical options for severely ill neonates and multiple surgical interventions after infancy. Only with ample knowledge and understanding of the above, this complex and diverse group of patients can be correctly treated in order to improve not only duration, but also quality of life.

scholarly journals Successful Use of Pulmonary Vasodilators in Acute Chest Syndrome Complicated by Persistent Right Ventricular Failure

2019 ◽  
Vol 2019 ◽  
pp. 1-5
Author(s):  
Jacqueline T. DesJardin ◽  
Lucas S. Zier
Keyword(s):  
Cardiogenic Shock ◽  
Right Ventricular ◽  
Pain Control ◽  
Right Ventricular Failure ◽  
Acute Chest Syndrome ◽  
Cell Disease ◽  
Ventricular Failure ◽  
Pulmonary Vasodilators ◽  
Control And Prevention ◽  
History Of

Pulmonary hypertension (PH) is a known consequence of sickle cell disease (SCD) and is associated with increased mortality and more frequent episodes of acute chest syndrome (ACS). Pulmonary pressures are known to increase during ACS, and right ventricular (RV) failure has been described as a significant cause of mortality in this condition. Management of ACS includes exchange transfusion, pain control, and prevention of hypovolemia and hypoxemia. However, in patients with a history of precapillary PH in whom ACS is complicated by persistent RV failure and cardiogenic shock, RV afterload reduction with pulmonary vasodilators may be an effective treatment strategy. Here, we present a case of a young man with SCD-associated PH and ACS who was successfully managed with inhaled and oral pulmonary vasodilators in the setting of persistent elevations in pulmonary vascular resistance leading to acute RV failure and cardiogenic shock.

scholarly journals New onset severe right ventricular failure associated with COVID-19 in a young infant without previous heart disease

2020 ◽  
Vol 30 (9) ◽  
pp. 1346-1349 ◽  
Author(s):  
Moises Rodriguez-Gonzalez ◽  
Patricia Rodríguez-Campoy ◽  
Maria Sánchez-Códez ◽  
Irene Gutiérrez-Rosa ◽  
Ana Castellano-Martinez ◽  
...  
Keyword(s):  
Heart Disease ◽  
Right Ventricular ◽  
Young Infant ◽  
Right Ventricular Failure ◽  
Future Research ◽  
Recent Experience ◽  
Ventricular Failure ◽  
History Of ◽  
Inflammatory Syndrome ◽  
New Onset

AbstractWe present our recent experience with a 6-month-old infant with a personal history of short bowel syndrome that presented with fever, cyanosis, and cardiogenic shock secondary to severe pulmonary hypertension and right ventricular failure without pulmonary thromboembolism. He did not present signs of toxin-mediated disease or Kawasaki disease. He was finally diagnosed with SARS-CoV-2 infection. If this presentation is confirmed in future research, the severe cardiovascular impairment in children with COVID-19 could be also attributable to the primary pulmonary infection, not only to a multisystem inflammatory syndrome but also in children without heart disease.

scholarly journals Medical and Surgical Treatment of Acute Right Ventricular Failure

2010 ◽  
Vol 56 (18) ◽  
pp. 1435-1446 ◽  
Author(s):  
Tim Lahm ◽  
Charles A. McCaslin ◽  
Thomas C. Wozniak ◽  
Waqas Ghumman ◽  
Yazid Y. Fadl ◽  
...  
Keyword(s):  
Surgical Treatment ◽  
Right Ventricular ◽  
Right Ventricular Failure ◽  
Ventricular Failure ◽  
Acute Right Ventricular Failure
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