The Sensorineural Hearing Loss Related to a Rare Infratentorial Developmental Venous Angioma: A Case Report and Review of Literature

2021 ◽  
Author(s):  
Kaveh Ebrahimzadeh ◽  
Hesameddin Hoseini Tavassol ◽  
Seyed Ali Mousavinejad ◽  
Mohammad Ansari ◽  
Reyhaneh Kazemi ◽  
...  
Keyword(s):  
Hearing Loss ◽  
Sensorineural Hearing Loss ◽  
Brain Parenchyma ◽  
Sensorineural Hearing ◽  
Normal Brain ◽  
Developmental Venous Anomaly ◽  
Facial Paresis ◽  
Rare Presentation ◽  
Compression Effect ◽  
Cerebellar Peduncle

Abstract Background Developmental venous anomaly (DVA) is a benign venous abnormality draining normal brain parenchyma. It is mostly asymptomatic; however, rare complications such as hemorrhage may lead to symptomatic conditions. Headache and seizure are the most common symptoms. Hearing loss is an extremely rare presentation of DVA. To our knowledge, only five cases of DVA, presenting with hearing loss, had been reported so far. Case Presentation We report the case of a 27-year-old woman who presented with a sensorineural hearing loss followed by facial paresis. Magnetic resonance imaging (MRI) and computed tomography (CT) angiography revealed hematoma with adjacent converging veins showing a typical “caput medusa” sign in the left middle cerebellar peduncle, in favor of DVA. Due to the compression effect of hematoma, she underwent surgery. Hearing loss and facial paresis improved significantly during the postoperative follow-up. Conclusion Although DVA is mostly benign and asymptomatic, complications such as hemorrhage rarely occur. Hearing loss is an extremely rare presentation that can be attributable to the compression effect on the cranial nerve VII to VIII complex. In the case of compression effect or progression of symptoms, surgical intervention is necessary. A good clinical outcome could be expected postoperatively.

scholarly journals Malaria induced sudden sensorineural hearing loss: a rare presentation

2019 ◽  
Vol 5 (6) ◽  
pp. 1701
Author(s):  
Adewale D. Agbaakin ◽  
Ayodele M. Akinola ◽  
Adetola Rachael Adeyeye ◽  
Chinonso B. Nkemjika
Keyword(s):  
Hearing Loss ◽  
Sensorineural Hearing Loss ◽  
Sudden Hearing Loss ◽  
Blood Film ◽  
Sudden Sensorineural Hearing Loss ◽  
Sensorineural Hearing ◽  
High Concentration ◽  
Rare Presentation ◽  
Profound Hearing Loss ◽  
Essentially Normal

<p>Sudden Hearing loss has been rarely reported as a presenting symptom of malaria fever. It’s even more rare to have a bilateral profound sudden sensorineural hearing loss. A 19 years old female student presented with fever, body weakness, hearing loss with tinnitus. Laboratory investigations done were essentially normal except blood film for malaria parasite which showed a high concentration of the parasite in blood on both occasions. Otoacoustics emission test was passed bilaterally while auditory steady state response showed profound hearing loss bilaterally. Normal hearing was restored within 48 hrs of commencement of anti-malaria drugs and low dose steroids. </p>

Metachronous Sudden Sensorineural Hearing Loss: Patient Characteristics and Treatment Outcomes

2020 ◽  
Vol 162 (3) ◽  
pp. 337-342
Author(s):  
Timothy Cooper ◽  
Ronak Dixit ◽  
Candace E. Hobson ◽  
Barry E. Hirsch ◽  
Andrew A. McCall
Keyword(s):  
Hearing Loss ◽  
Sensorineural Hearing Loss ◽  
Cochlear Implantation ◽  
Case Series ◽  
Sudden Sensorineural Hearing Loss ◽  
Sensorineural Hearing ◽  
Retrospective Case ◽  
Rare Presentation ◽  
Profound Hearing Loss ◽  
The Mean

Objectives Idiopathic sudden sensorineural hearing loss (ISSNHL) is a distressing condition that can significantly affect quality of life. Unilateral ISSNHL, occurring first in 1 ear and then the contralateral ear at a separate and discrete time, is a rare presentation that we refer to as metachronous ISSNHL. Our objective was to characterize the presentation of metachronous ISSNHL and report on management and hearing outcomes. Study Design Retrospective case series. Setting Otology clinic at an academic tertiary referral center. Subjects and Methods Patients ≥18 years old presenting with metachronous ISSNHL between April 2008 to November 2017 were identified through review of the clinic electronic medical record. Metachronous ISSNHL was defined as unilateral ISSNHL occurring in temporally discrete episodes (>6 months apart) affecting both ears. Patients with identifiable causes for sudden hearing loss were excluded. Patient demographics, comorbidities, management, and audiologic outcomes were recorded. Results Eleven patients with metachronous ISSNHL were identified out of 558 patients with ISSNHL. In patients with metachronous ISSNHL, the mean ± standard deviation age at the time of ISSNHL in the second ear was 58.6 ± 15.2 years (range, 31-77 years). The mean interval between episodes was 9.6 ± 7.5 years (range, 1-22 years). Patients were treated with systemic and intratympanic steroids with variable hearing recovery; 5 patients with resultant bilateral severe to profound hearing loss underwent successful cochlear implantation. Conclusion Metachronous ISSNHL is uncommon. Treatment is similar to ISSNHL, and cochlear implantation can successfully restore hearing in individuals who do not experience recovery.

Recovery of sensorineural hearing loss following operative management of a posterior fossa arachnoid cyst

2009 ◽  
Vol 4 (2) ◽  
pp. 121-124 ◽  
Author(s):  
Mayur Jayarao ◽  
Anand K. Devaiah ◽  
Lawrence S. Chin
Keyword(s):  
Hearing Loss ◽  
Sensorineural Hearing Loss ◽  
Posterior Fossa ◽  
Arachnoid Cyst ◽  
Complete Resolution ◽  
Signs And Symptoms ◽  
Operative Management ◽  
Sensorineural Hearing ◽  
Arachnoid Cysts ◽  
Rare Presentation

Arachnoid cysts are benign, intraarachnoid cysts filled with cerebrospinal fluid that are usually encountered in the middle cranial fossa. If present in the posterior fossa, they usually produce nonspecific signs and symptoms such as headaches, dizziness and vertigo. We report the rare presentation of a young girl with right-sided sensorineural hearing loss and tinnitus secondary to a right cerebellopontomedullary arachnoid cyst. The patient underwent a suboccipital retrosigmoid (retromastoid) craniectomy with fenestration of the arachnoid cyst. Subsequently, the patient experienced improvement in hearing with near-complete resolution of sensorineural hearing loss. To the authors' knowledge, postoperative near-complete resolution of hearing loss secondary to posterior fossa arachnoid cysts in a pediatric patient has not been previously reported. The authors also review the literature with respect to posterior fossa arachnoid cysts and discuss their clinical features, diagnosis, and management.

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