scholarly journals A Triad of Unilateral Renal Dysgenesis with Ipsilateral Seminal Vesical and Ejaculatory Duct Obstruction: An Uncommon Urogenital Congenital Anomaly, Zinner Syndrome—A Case Report

2021 ◽  
Author(s):  
Rajani Gorantla ◽  
Sameera Allu ◽  
Ankamma Rao
Keyword(s):  
Congenital Anomaly ◽  
Renal Agenesis ◽  
Early Adulthood ◽  
Ejaculatory Duct ◽  
First Trimester ◽  
Reproductive Activity ◽  
Urogenital System ◽  
Unilateral Renal Agenesis ◽  
Duct Obstruction ◽  
Ejaculatory Duct Obstruction

AbstractZinner syndrome is a rare congenital anomaly of the urogenital system resulting from an in utero insult during the first trimester. This entity comprises a triad of unilateral renal agenesis/dysgenesis with ipsilateral seminal vesical and ejaculatory duct obstruction. This combination of urinary and genital abnormalities occurs because of the closely related embryological origin of these structures from the distal mesonephric (Wolffian) duct. Nearly 200 cases of seminal vesical cysts with ipsilateral renal agenesis have been reported in the literature. The affected person generally presents in early adulthood when the reproductive activity commences. In this report, we present a case of a 22-year-old male with complaints of painful ejaculation.

scholarly journals Zinner Syndrome

2021 ◽  
Author(s):  
Abakar Djidda ◽  
Fatima-Ezzahrae Badi ◽  
Mouna Sabiri ◽  
Samia Elmanjra ◽  
Samira Lezar ◽  
...  
Keyword(s):  
Young Patient ◽  
Seminal Vesicle ◽  
Renal Agenesis ◽  
Ejaculatory Duct ◽  
Developmental Anomaly ◽  
Unilateral Renal Agenesis ◽  
Duct Obstruction ◽  
Seminal Vesicle Cyst ◽  
Mesonephric Duct ◽  
Ejaculatory Duct Obstruction

Zinner syndrome is a developmental anomaly of the urogenital tract. This condition is defined by the triad of unilateral renal agenesis, ipsilateral seminal vesicle cyst and ipsilateral ejaculatory duct obstruction. The syndrome is due to malformation of the mesonephric duct during embryogenesis. The condition used to be rare but is now frequently encountered due to the advent of MRI and CT. MRI confirms the diagnosis by revealing the seminal vesicle cyst and its contents, and the ejaculatory duct obstruction, while CT confirms renal agenesis. We report the case of a young patient with Zinner syndrome.

A wide spectrum of rare clinical variants of Zinner syndrome

2021 ◽  
Vol 14 (1) ◽  
pp. e239254
Author(s):  
Harkirat Singh Talwar ◽  
Ankur Mittal ◽  
Tushar Aditya Narain ◽  
Vikas Kumar Panwar
Keyword(s):  
Congenital Malformations ◽  
Renal Agenesis ◽  
Wide Spectrum ◽  
Ejaculatory Duct ◽  
Seminal Vesicles ◽  
Duct Obstruction ◽  
Cyst Excision ◽  
Maintenance Haemodialysis ◽  
Clinical Variants ◽  
Ejaculatory Duct Obstruction

Congenital malformations of the seminal vesicles (SVs) are rare and are associated with abnormalities of the ipsilateral urinary tracts as embryologically both the ureteral buds and SVs arise from the mesonephric ducts. The triad of SV cysts, ipsilateral renal agenesis and ejaculatory duct obstruction is known as the Zinner syndrome. We, herein, present three very rare presentations of Zinner syndrome. Case 1 presented with haematuria, and was found to have a large SV cyst with stones and underwent a robotic cyst excision. Case 2 presented with primary infertility, and was found to have a variant of Zinner syndrome. Case 3 was a known case of chronic kidney disease on maintenance haemodialysis who presented with fever and oliguria. He was found to have Zinner syndrome and underwent aspiration of SV abscess. To the best of our knowledge, such varying presentations of Zinner syndrome have been rarely reported thus far.

Zinner syndrome: two cases and review of the literature

2021 ◽  
Vol 14 (6) ◽  
pp. e243002
Author(s):  
Valerio Di Paola ◽  
Riccardo Gigli ◽  
Angelo Totaro ◽  
Riccardo Manfredi
Keyword(s):  
Distal Part ◽  
Renal Agenesis ◽  
Ejaculatory Duct ◽  
Growth Failure ◽  
Early Embryogenesis ◽  
Abnormal Development ◽  
Review Of The Literature ◽  
Initial Report ◽  
Unilateral Renal Agenesis ◽  
Ejaculatory Duct Obstruction

Zinner syndrome (ZS) is a rare congenital malformation due to abnormal development of the urogenital tract. It is caused by a growth failure of the distal part of the Müllerian duct in early embryogenesis. It is characterised by the triad of unilateral renal agenesis, ipsilateral seminal vesicle cyst and ipsilateral ejaculatory duct obstruction. Over the years, several cases have been reported in the literature since the initial report by Zinner in 1914. This syndrome is frequently misdiagnosed because it may present different patterns and the symptoms may be not specific. In this paper, we present two patients with two different patterns of presentation of Zinner syndrome.

scholarly journals Rare Cause of Painful Ejaculation – Zinner’s Syndrome: A Case Report

2020 ◽  
Vol 3 ◽  
pp. 1
Author(s):  
Devimeenal Jaganathan ◽  
Gopinathan Kathirvelu ◽  
Suriyaprakash Nagarajan ◽  
Usha Nandhini Ganesan
Keyword(s):  
Seminal Vesicle ◽  
Renal Agenesis ◽  
Ejaculatory Duct ◽  
Resonance Imaging ◽  
Unilateral Renal Agenesis ◽  
Common Complaint ◽  
Radiologic Imaging ◽  
Rare Congenital Abnormality ◽  
Ejaculatory Duct Obstruction ◽  
Zinner’S Syndrome

Zinner’s syndrome is a rare congenital abnormality consisting of unilateral renal agenesis, ipsilateral seminal vesicle cyst, and ipsilateral ejaculatory duct obstruction. The mutual embryological origins of the seminal vesicle and the ureteral bud from the Wolffian duct result in both anomalous seminal vesicle and urinary tracts. Most cases have nonspecific symptoms such as prostatism, urinary urgency, dysuria, painful ejaculation, and perineal discomfort. The usual presentation is between the third and fourth decades of life, with infertility being the most common complaint. Ultrasound and magnetic resonance imaging can easily detect this condition. We present here an extremely rare developmental anomaly involving the Wolffian ducts, which would remain undiagnosed but for radiologic imaging.

Zinner Syndrome with Ectopic Ureter Remnant

2021 ◽  
Vol 17 ◽  
Author(s):  
Ara Ko ◽  
Sung Bin Park ◽  
Hyun Jeong Park ◽  
Eun Sun Lee
Keyword(s):  
Seminal Vesicle ◽  
Ejaculatory Duct ◽  
Outlet Obstruction ◽  
Ectopic Ureter ◽  
Cystic Dilatation ◽  
Unilateral Renal Agenesis ◽  
Rare Congenital Abnormality ◽  
Mesonephric Duct ◽  
Clinical Triad ◽  
Ejaculatory Duct Obstruction

: Zinner syndrome is a rare congenital abnormality defined by a clinical triad of unilateral renal agenesis, ipsilateral seminal vesicle cyst, and ipsilateral ejaculatory duct obstruction. Most patients are asymptomatic, but if the cystic dilatation of the seminal vesicle becomes significant, it can result in urinary symptoms such as dysuria and urinary retention. This rare developmental anomaly related to the mesonephric duct can also present with other abnormalities. Here, we report our experience of Zinner syndrome with bladder outlet obstruction and an ectopic ureter remnant.

Diagnosis and Treatment of Ejaculatory Duct Obstruction in Male Infertility

2001 ◽  
Vol 39 (1) ◽  
pp. 24-29 ◽  
Author(s):  
Yaşar Özgök ◽  
Yaşar Özgök ◽  
Özgür Tan ◽  
Özgür Tan ◽  
Mete Kilciler ◽  
...  
Keyword(s):  
Male Infertility ◽  
Ejaculatory Duct ◽  
Diagnosis And Treatment ◽  
Duct Obstruction ◽  
Ejaculatory Duct Obstruction
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