DOZ047.58: The familial occurrence of congenital esophageal atresia with or without a fistula is an extremely rare pathology

2019 ◽  
Vol 32 (Supplement_1) ◽  
Author(s):  
R Smigiel ◽  
A Dzielendziak ◽  
K Toczewski ◽  
A Rozensztrauch ◽  
M Bloch ◽  
...  
Keyword(s):  
Esophageal Atresia ◽  
Pediatric Surgery ◽  
Oral Feeding ◽  
Younger Child ◽  
Congenital Esophageal Atresia ◽  
Early Postoperative Complications ◽  
Esophageal Anastomosis ◽  
Child Patients ◽  
Healthy Siblings ◽  
The One

Abstract We report on two siblings (boy and girl), which were treated for congenital esophageal atresia with the fistula, at the Department of Pediatric Surgery and Urology in Wroclaw, at an interval of two years. These children have two healthy siblings. Both newborns were born on time (38 and 42 week of pregnancy). Prenatally hydramnios was observed in younger child. They were postnatally diagnosed with congenital esophageal atresia with a distal fistula. Newborns were operated on the second day of life. Bronchoscopy and right-sided thoracoscopy were performed. Both patients had a short-gap esophageal atresia with a distal fistula. The fistula was proximally closed with sutures and divided distally. Subsequently, the one-layered esophageal anastomosis was performed. There were no early postoperative complications. Both patients underwent two esophageal dilatations. Siblings are tolerating oral feeding. Occasionally, parents observe choking in the older child. Patients remain under the constant care of a pediatric surgery clinic. Moreover, children were evaluated by clinical geneticist and exome sequencing (WES) study on the base of DNA isolated from lymphocytes and esophageal tissues were performed in both siblings.

Role of Fibrin Glue as a Sealant to Esophageal Anastomosis in Cases of Congenital Esophageal Atresia with Tracheoesophageal Fistula

2007 ◽  
Vol 31 (12) ◽  
pp. 2412-2415 ◽  
Author(s):  
Vijai D. Upadhyaya ◽  
Saroj C. Gopal ◽  
Ajay N. Gangopadhyaya ◽  
Dinesh K. Gupta ◽  
Shiv Sharma ◽  
...  
Keyword(s):  
Fibrin Glue ◽  
Esophageal Atresia ◽  
Tracheoesophageal Fistula ◽  
Congenital Esophageal Atresia ◽  
Esophageal Anastomosis

scholarly journals Infants with esophageal atresia and right aortic arch: Characteristics and outcomes from the Midwest Pediatric Surgery Consortium

2019 ◽  
Vol 54 (4) ◽  
pp. 688-692 ◽  
Author(s):  
Dave R. Lal ◽  
Samir K. Gadepalli ◽  
Cynthia D. Downard ◽  
Peter C. Minneci ◽  
Michelle Knezevich ◽  
...  
Keyword(s):  
Aortic Arch ◽  
Esophageal Atresia ◽  
Pediatric Surgery ◽  
Right Aortic Arch

Esophagitis with Eosinophil Infiltration Associated with Congenital Esophageal Atresia and Stenosis

2013 ◽  
Vol 161 (s2) ◽  
pp. 159-163 ◽  
Author(s):  
Yoshiyuki Yamada ◽  
Akira Nishi ◽  
Masahiko Kato ◽  
Fumiaki Toki ◽  
Hideki Yamamoto ◽  
...  
Keyword(s):  
Esophageal Atresia ◽  
Eosinophil Infiltration ◽  
Congenital Esophageal Atresia

scholarly journals A Rare Cause of Intestinal Obstruction in Infants: Ileum Duplication Cyst and Literature Review

2015 ◽  
Vol 2015 ◽  
pp. 1-3
Author(s):  
Mehmet Serif Arslan ◽  
Erol Basuguy ◽  
Hikmet Zeytun ◽  
Serkan Arslan ◽  
Bahattin Aydogdu ◽  
...  
Keyword(s):  
Literature Review ◽  
Intestinal Obstruction ◽  
Male Patient ◽  
Pediatric Surgery ◽  
Clinical Symptoms ◽  
Abdominal Distension ◽  
Duplication Cyst ◽  
Oral Feeding ◽  
Imaging Method ◽  
History Of

Cases of neonatal gastrointestinal system (GIS) obstruction are quite complex for pediatric surgery clinics. A rare cause of intestinal obstruction is the duplication cyst (DC). A three-day-old male patient presented at our clinic with a history of abdominal distension and bilious vomiting on the second day following birth. Although pathology had not yet been determined from observation and examination, surgery was performed when the patient could not tolerate oral feeding. An ileal DC forming an incomplete obstruction was observed. Ileoileal anastomosis was performed on the patient. Because DCs can present with different clinical symptoms, it is quite difficult to diagnose them in neonate patients. Lacking an imaging method that can provide an exact diagnosis, the diagnostic laparotomy is a suitable approach for both diagnosis and treatment to avoid delays in treatment.

scholarly journals Long-term neurodevelopment in children born with esophageal atresia: a systematic review

2021 ◽  
Author(s):  
Camille E van Hoorn ◽  
Chantal A ten Kate ◽  
Andre B Rietman ◽  
Leontien C C Toussaint-Duyster ◽  
Robert Jan Stolker ◽  
...  
Keyword(s):  
Cognitive Development ◽  
Motor Function ◽  
Esophageal Atresia ◽  
Current Knowledge ◽  
Neurodevelopmental Outcome ◽  
Cognitive Outcome ◽  
Term Outcome ◽  
Long Term Outcome ◽  
The One

Summary Background Although the survival rate of esophageal atresia (EA) has increased to over 90%, the risk of functional long-term neurodevelopmental deficits is uncertain. Studies on long-term outcomes of children with EA show conflicting results. Therefore, we provide an overview of the current knowledge on the long-term neurodevelopmental outcome of children with EA. Methods We performed a structured literature search in Embase, Medline Ovid, Web of Science, Cochrane CENTRAL, and Google scholar on November 8, 2020 with the keywords ‘esophageal atresia’, ‘long-term outcome’, ‘motor development’, ‘cognitive development’, and ‘neurodevelopment’. Results The initial search identified 945 studies, of which 15 were included. Five of these published outcomes of multiple tests or tested at multiple ages. Regarding infants, one of six studies found impaired neurodevelopment at 1 year of age. Regarding preschoolers, two of five studies found impaired neurodevelopment; the one study assessing cognitive development found normal cognitive outcome. Both studies on motor function reported impairment. Regarding school-agers, the one study on neurodevelopmental outcome reported impairment. Cognitive impairment was found in two out of four studies, and motor function was impaired in both studies studying motor function. Conclusions Long-term neurodevelopment of children born with EA has been assessed with various instruments, with contrasting results. Impairments were mostly found in motor function, but also in cognitive performance. Generally, the long-term outcome of these children is reason for concern. Structured, multidisciplinary long-term follow-up programs for children born with EA would allow to timely detect neurodevelopmental impairments and to intervene, if necessary.

DOZ047.36: Thoracoscopic esophageal internal axial traction for long- gap esophageal atresia

2019 ◽  
Vol 32 (Supplement_1) ◽  
Author(s):  
M Juricic ◽  
N Panait ◽  
G Podevin ◽  
A Bonnard ◽  
P Lopez ◽  
...  
Keyword(s):  
Esophageal Atresia ◽  
Operative Time ◽  
Median Number ◽  
Ethical Review ◽  
Multicenter Observational Study ◽  
Long Gap ◽  
Esophageal Anastomosis ◽  
Long Gap Esophageal Atresia ◽  
Axial Traction ◽  
Median Operative Time

Abstract Aim of the Study Long-gap esophageal atresia (LGEA) remains a surgical challenge. This study aimed to report the results of thoracoscopic esophageal axial internal traction in LGEA. Methods This multicenter observational study included retrospectively neonates who underwent primary thoracoscopic esophageal axial internal traction for LGEA between June 2017 and July 2018. LGEA was defined as the technical impossibility to perform a primary esophageal anastomosis. The Ethical Review Board of our institution approved the study. Main Results Eight neonates were included with a median gestational age at birth of 35 weeks [25; 37] and a median birth weight of 2266 g [890; 3800], 6 types I and 2 types II according to Ladd's classification. Initial median gap between 2 esophageal ends was 5 vertebral bodies [4.5; 7]. Internal traction was performed at a median age of 5 weeks of life [1; 17] with a median operative time of 87 minutes. Four patients required at least 2 internal traction procedures. After a mean traction time of 1.5 weeks [1; 13.5], esophageal anastomosis was successfully performed in 7 patients (5 thoracoscopies, 2 thoracotomies) with a median operative time of 165 minutes. One patient needed a colonic interposition. Five of these 7 patients required an esophageal endoscopic dilatation (median number: 4 [2; 6]). Median follow-up was 9.75 months [3; 16]. Conclusions Thoracoscopic esophageal axial internal traction for LGEA was a safe and feasible procedure that allowed an esophageal anastomosis in 7 of the 8 patients. Improvement of the procedure requires setting a common protocol concerning the timing of the first internal axial traction and the duration of traction before considering esophageal anastomosis.

DOZ047.53: Esophageal balloon dilatation for strictures developing after esophageal atresia surgery

2019 ◽  
Vol 32 (Supplement_1) ◽  
Author(s):  
C U Durakbasa ◽  
B Aksu ◽  
E Uzun ◽  
D Ugurlu ◽  
S Aydoner ◽  
...  
Keyword(s):  
Esophageal Atresia ◽  
Balloon Dilatation ◽  
Colonic Anastomosis ◽  
Median Number ◽  
Esophageal Replacement ◽  
Replacement Surgery ◽  
Anastomosis Site ◽  
Esophageal Anastomosis ◽  
Esophageal Balloon ◽  
Target Pressure

Abstract Aim The aim of this study is to evaluate the results of esophageal balloon dilatation (BD) for strictures after esophageal atresia (EA) surgery. Methods Flexible endoscopic BD was done under fluoroscopic and manometric control. The balloon placed in the stricture was inflated by contrast. The target pressure and the diameter were decided in compliance with the manufacturer's directions as well as fluoroscopic guidance. The balloon was kept inflated for 3 minutes. Prospectively collected data over 10 years were retrospectively evaluated. Cure was defined as no need for dilatation during the last 12 months. Results A total of 79 patients with variable diagnoses underwent 481 BD. Forty (51%) had strictures which developed after EA surgery. They underwent 175 (36%) BD (P < 0.05). There were 21 males and 19 females. The atresia was distal fistula type in 31 (77.5%) patients and isolated EA in nine (22.5%). The BD was done for primary esophago-esophageal anastomosis site in 37 patients. The remaining three patients with long gap EA had undergone previous replacement surgery and the BD was done for the proximal esophago-colonic anastomosis. The median age at the time of the first BD was 14 months with 17 (43%) patients below the age of 1 year. The maximal inflation diameter varied between 5–20 mm. Esophageal BD catheters were used in all except two occasions where 5 mm ureteral balloons were used. The median number of BD was four (n = 1–15). Thirty-four (85%) patients underwent more than one BD. A transmural perforation was encountered in one occasion (0.6%) and the patient eventually underwent esophageal replacement surgery with an uneventful outcome. There was no mortality. Fundoplication was done in nine patients. Thirty-three patients (82.5%) were regarded as ‘cure’. Conclusion Esophageal BD is employed for strictures caused by a variety of reasons. Patients with EA comprise a substantial number of cases needing BD and have strictures less resistant to dilatation. The technique employed in this study is advantageous because it enables direct endoscopic visualization of the stricture and both gradual and controlled increase of the dilatation pressure. BD is safe and efficient yet there is a risk of esophageal perforation as in the other dilatation techniques.

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