scholarly journals P729 A shocking tumor

2020 ◽  
Vol 21 (Supplement_1) ◽  
Author(s):  
A Lorente Ros ◽  
M Pascual Izco ◽  
R Hinojar-Baydes ◽  
A Carvelli ◽  
J M Vieitez Florez ◽  
...  

Abstract Introduction Primary cardiac tumors are a relatively uncommon condition, which may appear both in asymptomatic patients or in a myriad of clinical presentations. Imaging techniques are crucial for its diagnosis, and a multi-modality approach may be useful in the evaluation of this masses. Case description A 57 year-old man with history of hypertension presented in the emergency department with acute pulmonary edema and cardiogenic shock. He was admitted to the coronary care unit, and on bedside echocardiography a mass on the tricuspid valve was observed. Upon clinical improvement, a cardiac CT and cardiac MRI was performed (figure 1). A solid mass with no calcium content and dependent exclusively on the anterior leaflet of the tricuspid valve was seen on CT-scan (fig 1, A and B). Thrombus on the right atrial appendage could also be appreciated. MRI confirmed the presence of a 18x19 mm mass with isointense signal on T1-turbo spin echo black-blood (fig 1, C) and cine steady-state free precession sequences, whereas an hyperintense signal was evident on T2 weighted images (T2-STIR; fig 1 D). In first pass sequences the central core was hypointense and late gadolinium enhancement showed peripheral enhancement with a non captating central core (fig 1, E). The patient underwent surgery and the anatomopathological results showed a tumor constituted by dense connective tissue, scarce cellular content and an avascular matrix of mucopolysaccharides, elastic fibers and fusiform cells consistent with the diagnosis of papillary fibroelastoma. Discussion The imaging characteristics of papillary fibroelastoma are not commonly reported on MRI. We present an unusually large right-sided fibroelastoma with a characteristic distribution of late gadolinium enhancement, which has not been consistently described on a fibroelastoma. Cardiac tumors are rare, and a non-invasive differential diagnosis is always a challenge. A multi-modality approach (echocardiography, cardiac-CT and cardiac MRI) as well as integration of relevant morphological information, including the location of the lesion and tissue characteristics was essential to the orientate the most plausible diagnosis. The distinctive images are presented. Abstract P729 Figure 1.

2021 ◽  
Vol 54 (2) ◽  
pp. 201-202
Author(s):  
Imran Hameed

SUMMARY A 5-day old female child with complaints of tachypnea, had TTE which revealed an echogenic mass on septal leaflet of Tricuspid valve. Based on echocardiographic features, it was diagnosed as Papillary fibroelastoma. CASE DESCRIPTION A 5-day old female child was referred for transthoracic echocardiographic study due to respiratory difficulty. The child was afebrile and had a respiratory rate of 60/min, heart rate 130 bpm, and blood pressure 80/50 mmHg. No murmur or added sound heard on CVS examination. TTE revealed a dense mass (Figure 1) attached to right atrial side of septal leaflet of Tricuspid valve by a small pedicle. The mass was mobile, prolapsing into right ventricle during diastole (Clips) without causing obstruction with size of 0.8 X 0.74 cm. Intracardiac masses attached to valves are usually Papillary fibroelastomas. Other possible differential diagnoses could be myxoma, vegetation, Lambl’s excrescence or secondary tumors etc. Based on the location and echo features of the mass (mobility, attachment to downstream side of valve, and frond like speckled appearance) the diagnosis of Papillary fibroelastoma was made.  LEARNING POINTS Cardiac tumors are rare and mostly benign. The three most common primary tumors of heart, in order of frequency, are myxomas, lipomas and papillary fibroelastomas respectively. PFE constitute 7% - 9% of all.1 PFE usually arise from valves of the heart and are mostly left-sided.2 They are mobile, range from 0.5 – 2 cm in size and have a frond-like appearance. On echo, they are dense with a speckled interior and shimmering surface.3 Being prone to embolization and thrombosis, their clinical course may not be benign, especially left sided. Clips Subcostal Clip: https://youtu.be/_xTZmx--WcA PS SAX View: https://youtu.be/lLh6D9Vn4Fw A4C View: https://youtu.be/_xZZvTIh0S8 A4C RV Directed View: https://youtu.be/vJRyHrevftA QUESTIONS WITH ANSWERS Question 1: What is the most common complication of papillary fibroelastoma? Question 2: The behavior of right and left sided papillary fibroelastomas could be markedly different, Y/N? Question 3: What is the most important feature of papillary fibroelastoma for embolization? Question 4: PFE preferentially affects females, Y/N?  Answers Question 1: Cerebral embolism Question 2: Yes Question 3: Mobility Question 4: No References Bouhzam N, Kurtz B, Doguet F, Eltchaninoff H, Bauer F. Incidental papillary fibroelastoma multimodal: imaging and surgical decisions in 2 patients. Tex Heart Inst J. 2012;39(5):731-5. Eidem BW, Cetta F, O’ Leary PW. Echocardiography in pediatric and adult congenital heart disease. Lippincott, Williams and Wilkins, Wolters Kluwer. 2010 p 355-361. Klarich KW, Enriquez-Sarano M, Gura GM, Edwards WD, Tajik AJ, Seward JB. Papillary fibroelastoma: echocardiographic characteristics for diagnosis and pathologic correlation. J Am Coll Cardiol. 1997;30(3):784-90.


2020 ◽  
Vol 6 (1) ◽  
Author(s):  
Anthony Ricco ◽  
Alexander Slade ◽  
Justin M. Canada ◽  
John Grizzard ◽  
Franklin Dana ◽  
...  

2010 ◽  
Vol 12 (S1) ◽  
Author(s):  
Rei Noguchi ◽  
Takatomo Nakajima ◽  
Yufuko Kasai ◽  
Eri Watanabe ◽  
Mitsuru Momose ◽  
...  

Sign in / Sign up

Export Citation Format

Share Document