Anomalies of pulmonary venous drainage

Total anomalous pulmonary venous drainage (TAPVD) 134Partial anomalous pulmonary venous drainage (PAPVD) 136Scimitar syndrome 138• All 4 pulmonary veins drain into R heart.• Either drain directly into RA or via a common vein into a systemic vein:•Supracardiac course draining to SVC, azygous or innominate vein....

2019 ◽  
Vol 3 (2) ◽  
Author(s):  
Paulo Henrique Manso ◽  
Valéria de Melo Moreira ◽  
Vera Demarchi Aiello

Abstract Background Scimitar syndrome consists of anomalous pulmonary vein drainage to the inferior vena cava. Its name derives from the image this anomalous pulmonary vein creates on a chest radiograph. We describe a case of normal venous pulmonary vein drainage that also presented the scimitar sign due to an aorto-collateral vessel. Case summary A 15-month-old girl presented with mild dyspnoea and fever. Control chest X-ray showed an image of cardiac dextroposition, hypoplastic right lung, and the ‘scimitar sign’. Although the transthoracic echocardiogram confirmed the initial suspicion of anomalous pulmonary venous drainage, the computed tomography (CT) scan showed normal right pulmonary veins connected to the left atrium and revealed that an aorto-collateral vessel caused the scimitar sign. Discussion Although the patient had several typical alterations of the scimitar syndrome, the pulmonary venous connection was normal, and the scimitar sign was due to an aorto-collateral vessel. It might be difficult to describe venous pulmonary connections on the basis of echocardiography, so an angio CT scan proved to be a valuable tool in this scenario.


Chest Imaging ◽  
2019 ◽  
pp. 533-537
Author(s):  
Kristopher W. Cummings

Abnormalities of pulmonary venous return in adults result from anomalous drainage of one or more pulmonary veins into a systemic vein, resulting in a left-to-right shunt. Partial anomalous pulmonary venous return (PAPVR) is most commonly encountered in adults in the upper lobes. PAPVR in the right upper lobe is commonly associated with a sinus venous atrial septal defect, whereas in the right lower lobe it is commonly encountered in association with other anomalies in Scimitar syndrome. Left upper lobe PAPVR is usually isolated. In some instances, patients can develop pulmonary over-circulation and hypertension, necessitating intervention. This chapter emphasizes CT and MR features key to recognizing and diagnosing these anomalies.


Author(s):  
Sara Thorne ◽  
Sarah Bowater

This chapster discusses anomalies of systemic venous drainage and anomalies of pulmonary venous drainage. It discusses superior vena cava (SVC) anomalies, inferior vena cava (IVC), total anomalous pulmonary venous drainage (TAPVD), partial anomalous pulmonary venous drainage (PAPVD), and scimitar syndrome.


2015 ◽  
Vol 37 (2) ◽  
pp. 290-294 ◽  
Author(s):  
Hyun-Jin Jung ◽  
Ji Hyun Bang ◽  
Chun-Soo Park ◽  
Jeong-Jun Park ◽  
Yu-Mi Im ◽  
...  

2012 ◽  
Vol 16 (1) ◽  
pp. 16-18
Author(s):  
Tracy Westgarth-Taylor ◽  
Tracy Kilborn

Congenital venolobar syndrome (CVLS) is a rare complex malformation that includes hypoplasia of the lung, partial anomalous pulmonary venous drainage and in a quarter of patients, associated cardiac anomalies. We present the chest radiograph and multidetector CT findings in a case of congenital venolobar syndrome in an infant.


Sign in / Sign up

Export Citation Format

Share Document