scholarly journals Imaging findings in an infant with congenital pulmonary venolobar syndrome (scimitar syndrome)

2012 ◽  
Vol 16 (1) ◽  
pp. 16-18
Author(s):  
Tracy Westgarth-Taylor ◽  
Tracy Kilborn

Congenital venolobar syndrome (CVLS) is a rare complex malformation that includes hypoplasia of the lung, partial anomalous pulmonary venous drainage and in a quarter of patients, associated cardiac anomalies. We present the chest radiograph and multidetector CT findings in a case of congenital venolobar syndrome in an infant.

2009 ◽  
Vol 24 (2) ◽  
pp. 142-146 ◽  
Author(s):  
Mahmoud Goudarzi ◽  
Sofia Sabouri ◽  
Nader Fayazi ◽  
Abbas Arjmand Shabestari ◽  
Mehrdad Bakhshayesh Karam ◽  
...  

Author(s):  
Sara Thorne ◽  
Sarah Bowater

This chapster discusses anomalies of systemic venous drainage and anomalies of pulmonary venous drainage. It discusses superior vena cava (SVC) anomalies, inferior vena cava (IVC), total anomalous pulmonary venous drainage (TAPVD), partial anomalous pulmonary venous drainage (PAPVD), and scimitar syndrome.


2019 ◽  
Vol 3 (2) ◽  
Author(s):  
Paulo Henrique Manso ◽  
Valéria de Melo Moreira ◽  
Vera Demarchi Aiello

Abstract Background Scimitar syndrome consists of anomalous pulmonary vein drainage to the inferior vena cava. Its name derives from the image this anomalous pulmonary vein creates on a chest radiograph. We describe a case of normal venous pulmonary vein drainage that also presented the scimitar sign due to an aorto-collateral vessel. Case summary A 15-month-old girl presented with mild dyspnoea and fever. Control chest X-ray showed an image of cardiac dextroposition, hypoplastic right lung, and the ‘scimitar sign’. Although the transthoracic echocardiogram confirmed the initial suspicion of anomalous pulmonary venous drainage, the computed tomography (CT) scan showed normal right pulmonary veins connected to the left atrium and revealed that an aorto-collateral vessel caused the scimitar sign. Discussion Although the patient had several typical alterations of the scimitar syndrome, the pulmonary venous connection was normal, and the scimitar sign was due to an aorto-collateral vessel. It might be difficult to describe venous pulmonary connections on the basis of echocardiography, so an angio CT scan proved to be a valuable tool in this scenario.


1987 ◽  
Vol 43 (2) ◽  
pp. 207-211 ◽  
Author(s):  
Serafin Y. DeLeon ◽  
Samuel S. Gidding ◽  
Michel N. Ilbawi ◽  
Farouk S. Idriss ◽  
Alexander J. Muster ◽  
...  

2021 ◽  
pp. 1-3
Author(s):  
Miguel Vieira Martins ◽  
Duarte S Martins ◽  
Graça Oliveira

Abstract Diaphragmatic eventration is an anomaly of the diaphragm. In Scimitar syndrome, a curved-shaped anomalous pulmonary venous drainage is seen. Association between these conditions is rare. We present a newborn with diaphragmatic eventration, whose diagnosis of Scimitar syndrome was made after surgical repair. Scimitar syndrome is a congenital disorder often associated with other heart and lungs anomalies. Diagnosis can be fortuitous but with important prognostic features.


Total anomalous pulmonary venous drainage (TAPVD) 134Partial anomalous pulmonary venous drainage (PAPVD) 136Scimitar syndrome 138• All 4 pulmonary veins drain into R heart.• Either drain directly into RA or via a common vein into a systemic vein:•Supracardiac course draining to SVC, azygous or innominate vein....


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