A case of neutrophilic dermatoses including pyoderma gangrenosum as a continuous disease spectrum to SAPHO syndrome

2018 ◽  
Vol 43 (7) ◽  
pp. 829-831
Author(s):  
Y. Sone ◽  
T. Namiki ◽  
S. Tokoro ◽  
K. Miura ◽  
H. Yokozeki
Keyword(s):  
Pyoderma Gangrenosum ◽  
Sapho Syndrome ◽  
Disease Spectrum ◽  
Neutrophilic Dermatoses

A Case of Pyoderma Gangrenosum as Skin Manifestation of SAPHO Syndrome in an IBD Patient

2018 ◽  
Vol 113 (Supplement) ◽  
pp. S1171-S1172
Author(s):  
Mitchell Kang ◽  
Seyedehsan Navabi ◽  
Allison J. Baragona ◽  
Carl Manzo ◽  
Andrew Tinsley ◽  
...  
Keyword(s):  
Pyoderma Gangrenosum ◽  
Sapho Syndrome ◽  
Skin Manifestation

scholarly journals An unusual pediatric clinical case of atypical pyoderma gangrenosum

2020 ◽  
Vol 48 (4) ◽  
pp. 263-270
Author(s):  
T. G. Sedova ◽  
V. D. Elkin ◽  
A. A. Zhukova
Keyword(s):  
Crohn’S Disease ◽  
Crohn's Disease ◽  
Oral Mucosa ◽  
Pyoderma Gangrenosum ◽  
Clinical Case ◽  
Clinical Manifestations ◽  
Diagnostic Errors ◽  
Unknown Etiology ◽  
Neutrophilic Dermatoses ◽  
Pyostomatitis Vegetans

Pyoderma gangrenosum (PG) belongs to the group of neutrophilic dermatoses with unknown etiology and poorly understood pathogenesis. In children, PG is primarily associated with inflammatory bowel diseases (Crohn's disease and ulcerative colitis). By now, about 355 PG cases have been described worldwide, including 15 children with the involvement of oral mucosa. Clinical manifestations of the disease are diverse and depend on the form, stage and associated conditions. Such a rare PG as pyodermatitis-pyostomatitis vegetans manifests by combined lesions of the oral mucosa and skin. The authors present historical data on the investigation of the disease, its etiology, pathogenesis, risk factors, and clinical picture. A description of a rare clinical case of severe form of atypical PG, namely, pyodermatitis-pyostomatitis vegetans in a 10-year-old child, is presented. The unique character of the case is related to the variety of clinical manifestations and the clinical course complicated by the development of keloid and partial scar-related flexion contracture of the upper and lower extremities, the formation of microstoma and cachexia. The association of pyodermatitis-pyostomatitis vegetans with Crohn's disease was found. The lack of awareness of the clinical symptoms of this rare disease has led to diagnostic errors and late diagnosis.

Pyoderma gangrenosum and Sweet syndrome: the prototypic neutrophilic dermatoses

2015 ◽  
Vol 178 (3) ◽  
pp. 595-602 ◽  
Author(s):  
D. Wallach ◽  
M.-D. Vignon-Pennamen
Keyword(s):  
Pyoderma Gangrenosum ◽  
Sweet Syndrome ◽  
Neutrophilic Dermatoses

Neutrophilic Dermatoses: Pyoderma Gangrenosum

2014 ◽  
pp. 767-771
Author(s):  
Gideon P. Smith ◽  
Andrew G. Franks
Keyword(s):  
Pyoderma Gangrenosum ◽  
Neutrophilic Dermatoses

scholarly journals A Case of the Co-Existence of Subcorneal Pustular Dermatosis and Pyoderma Gangrenosum and a Review of the Literature

2018 ◽  
Vol 6 (7) ◽  
pp. 1271-1274 ◽  
Author(s):  
Maria Ferrillo ◽  
Alessia Villani ◽  
Gabriella Fabbrocini ◽  
Massimo Mascolo ◽  
Matteo Megna ◽  
...  
Keyword(s):  
Pyoderma Gangrenosum ◽  
Strong Association ◽  
Systemic Diseases ◽  
Review Of The Literature ◽  
Right Hand ◽  
Strong Indicator ◽  
Neutrophilic Dermatoses ◽  
Subcorneal Pustular Dermatosis ◽  
History Of

BACKGROUND: Subcorneal pustular dermatosis, also known as Sneddon-Wilkinson disease, can be classified as one of the neutrophilic dermatoses together with pyoderma gangrenosum. The development of both SPD and PG in the same patient has rarely been reported and may be a strong indicator of IgA dysglobulinemiaCASE REPORT: We report the case of a 34-year-old woman with a 2-year history of relapsing pustular eruptions mainly affecting the abdomen, gluteus region, elbows, and the extremities. Four years after the onset of subcorneal pustular dermatosis (SPD), she developed pyoderma gangrenosum (PG) on her right hand. In literature, the coexistence of SPD and PG in the same patient has already been described. This co-occurrence might indicate a certain predisposition for immune dysregulation.CONCLUSION: Although the two NDs are often associated with systemic diseases, these patients should be followed up for any malignancy because of the strong association between these disorders.

Synovitis, acne, pustulosis, hyperostosis, osteitis (SAPHO) syndrome and acne fulminans: are they part of the same disease spectrum?

2009 ◽  
Vol 34 (7) ◽  
pp. e241-e243 ◽  
Author(s):  
S. L. Chua ◽  
J. E. Angus ◽  
J. Ravenscroft ◽  
W. Perkins
Keyword(s):  
Sapho Syndrome ◽  
Disease Spectrum ◽  
Acne Fulminans

Diagnosis and treatment of the neutrophilic dermatoses (pyoderma gangrenosum, Sweet's syndrome)

2011 ◽  
Vol 24 (2) ◽  
pp. 273-284 ◽  
Author(s):  
Tushar S. Dabade ◽  
Mark D. P. Davis
Keyword(s):  
Pyoderma Gangrenosum ◽  
Diagnosis And Treatment ◽  
Sweet’S Syndrome ◽  
Sweet's Syndrome ◽  
Neutrophilic Dermatoses
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