Absent Aortic Valve Associated with Double Outlet Right Ventricle and Aortopulmonary Window: Physiologic Implications of a Rare Malformation in both the Fetus and Neonate

2013 ◽  
Vol 9 (3) ◽  
pp. E98-E104 ◽  
Author(s):  
Arash A. Sabati ◽  
Pierre C. Wong ◽  
Linda Randolph ◽  
Jay D. Pruetz
Keyword(s):  
Aortic Valve ◽  
Right Ventricle ◽  
Double Outlet Right Ventricle ◽  
Aortopulmonary Window ◽  
Absent Aortic Valve ◽  
Rare Malformation ◽  
Fetus And Neonate

Double Outlet Right Ventricle with Absent Aortic Valve

CHEST Journal ◽  
1975 ◽  
Vol 68 (3) ◽  
pp. 381-382 ◽  
Author(s):  
Warren H. Toews ◽  
Randall H. Lortscher ◽  
Leslie L. Kelminson
Keyword(s):  
Aortic Valve ◽  
Right Ventricle ◽  
Double Outlet Right Ventricle ◽  
Absent Aortic Valve

A newborn with double-outlet right ventricle and aortopulmonary window associated with maternal phenylketonuria: a first case report

2010 ◽  
Vol 100 (3) ◽  
pp. 318-318 ◽  
Author(s):  
Rita Cabano ◽  
Giuseppina Lombardi ◽  
Savina Mannarino ◽  
Rosa Maria Cerbo ◽  
Paolo Manzoni ◽  
...  
Keyword(s):  
Case Report ◽  
Right Ventricle ◽  
Double Outlet Right Ventricle ◽  
Aortopulmonary Window ◽  
Maternal Phenylketonuria ◽  
First Case

Transcatheter Aortic Valve Implantation in Surgically Repaired Double Outlet Right Ventricle

2013 ◽  
Vol 9 (5) ◽  
pp. E153-E157 ◽  
Author(s):  
Amit Keswani ◽  
Anil Verma ◽  
Kristen Dann ◽  
Laurie Ventura ◽  
Victor Lucas ◽  
...  
Keyword(s):  
Aortic Valve ◽  
Right Ventricle ◽  
Transcatheter Aortic Valve Implantation ◽  
Double Outlet Right Ventricle ◽  
Transcatheter Aortic Valve ◽  
Aortic Valve Implantation ◽  
Valve Implantation

Surgical management of double outlet right ventricle with aortopulmonary window

2017 ◽  
Vol 32 (3) ◽  
pp. 203-205 ◽  
Author(s):  
Chao Hou ◽  
Vivendar Sihag ◽  
Yunfei Ling ◽  
Qi An
Keyword(s):  
Right Ventricle ◽  
Surgical Management ◽  
Double Outlet Right Ventricle ◽  
Aortopulmonary Window

scholarly journals Double outlet right ventricle and aortopulmonary window in a neonate with Bohring-Opitz (Oberklaid-Danks) syndrome: First case report

2019 ◽  
Vol 8 (3) ◽  
pp. 1279
Author(s):  
Bhupendra Verma ◽  
Abhishek Abhinay ◽  
Amrita Singh ◽  
Manu Kumar
Keyword(s):  
Case Report ◽  
Right Ventricle ◽  
Double Outlet Right Ventricle ◽  
Aortopulmonary Window ◽  
First Case

scholarly journals Aortopulmonary window and double outlet right ventricle: A rare combination

2014 ◽  
Vol 17 (3) ◽  
pp. 245 ◽  
Author(s):  
Sambhunath Das ◽  
Kalpna Irpachi ◽  
Rajat Kalra ◽  
Balram Airan
Keyword(s):  
Right Ventricle ◽  
Double Outlet Right Ventricle ◽  
Aortopulmonary Window ◽  
Rare Combination

scholarly journals P1445 DORv and window: a case of an uncorrected double outlet right ventricle with d-transposition of great arteries with concomitant aortopulmonary window in a 31-year-old female

2020 ◽  
Vol 21 (Supplement_1) ◽  
Author(s):  
R Enero ◽  
S Obillos ◽  
P Yao ◽  
E Dizon ◽  
V Choa ◽  
...  
Keyword(s):  
Pulmonary Artery ◽  
Right Ventricle ◽  
Main Pulmonary Artery ◽  
Double Outlet Right Ventricle ◽  
Left Ventricular ◽  
Aortopulmonary Window ◽  
Transposition Of Great Arteries ◽  
Severe Aortic Regurgitation ◽  
The Third ◽  
The Right

Abstract Funding Acknowledgements none Double outlet right ventricle (DORV) is a rare type of ventriculo-arterial connection occurring in about 1-3% of congenital heart defects. Moreover, transposition of the great arteries, wherein the aorta is anterior and to the right of the pulmonary artery (D-TGA), accounts for only 26% of cases of DORV. An aortopulmonary window, on the other hand, represents approximately only 0.2% of all congenital cardiac lesions. A case of DORV with D-TGA and pulmonary stenosis with a concomitant aortopulmonary window has never been reported, particularly in an adult in the third decade of life and without any history of surgical repair. We present the case of a 31-year-old female who had sought consult for left-sided weakness. On physical examination, a grade IV/VI systolic murmur was heard at the left anterior chest and cyanosis of the digits of the upper and lower extremities were noted. Transthoracic echocardiogram revealed a non-restrictive ventricular septal defect (VSD) and segmental approach showed atrial and visceral situs solitus, levocardia, and atrioventricular concordance. However, there was ventriculoarterial discordance with fusiform aneurysmal dilatation of the aorta, which was noted to be at the right of and anterior to the pulmonary artery. Both great vessels arose from the right ventricle. Other echocardiographic findings included dilated right atrium, dilated and hypertrophied right ventricle with volume and pressure overload, global left ventricular hypokinesia with mild systolic dysfunction, and moderate to severe aortic regurgitation. The above complex congenital anomalies were confirmed via transesophageal echocardiogram and cardiac magnetic resonance imaging (MRI). Furthermore, pulmonary valve stenosis and aortopulmonary window, that was 3.5 centimeters in length located at the level of the proximal ascending aorta and main pulmonary artery, were seen on the MRI. Various cardiac imaging modalities aided in cinching the diagnosis for this very rare complex congenital case in an adult reaching the third decade of life. Palliative care was deemed best for this patient due to the severity of her cardiac condition. Abstract P1445 Figure 1.

Surgical approach to a rare case of double-outlet right ventricle and aortopulmonary window

2015 ◽  
Vol 26 (1) ◽  
pp. 172-174 ◽  
Author(s):  
Robert D. Tunks ◽  
R. Dennis Steed ◽  
Andrew J. Lodge
Keyword(s):  
Right Ventricle ◽  
Surgical Approach ◽  
Rare Case ◽  
Neonatal Period ◽  
Double Outlet Right Ventricle ◽  
Interesting Case ◽  
Infants And Children ◽  
Aortopulmonary Window ◽  
First Report ◽  
In Infants And Children

AbstractAlthough the spectrum of physiology seen in infants and children with double-outlet right ventricle is broad, this anatomy in combination with an aortopulmonary window is extremely rare. We present an interesting case of an infant prenatally diagnosed with this rare CHD. To our knowledge, this is the first report of complete repair in the neonatal period for such a combination of defects.

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