Complete duplication of the bladder, urethra and external genitalia in a male neonate with an imperforate anus

2005 ◽  
Vol 12 (7) ◽  
pp. 702-704 ◽  
Author(s):  
HEINRICH R VOIGT ◽  
SCHALK W WENTZEL
Keyword(s):  
Imperforate Anus ◽  
External Genitalia ◽  
Male Neonate ◽  
Complete Duplication

scholarly journals A rare case of perineal hamartoma associated with cryptorchidism and imperforate anus: case report

2014 ◽  
Vol 12 (2) ◽  
pp. 234-236
Author(s):  
Kleiton Gabriel Ribeiro Yamaçake ◽  
Amilcar Martins Giron ◽  
Uenis Tannuri ◽  
Miguel Srougi
Keyword(s):  
Case Report ◽  
Physical Examination ◽  
Imperforate Anus ◽  
Rare Case ◽  
Coloanal Anastomosis ◽  
Histopathological Examination ◽  
Congenital Clubfoot ◽  
Anorectal Anomaly ◽  
Male Neonate ◽  
Nonpalpable Testis

A full-term male neonate with anorectal anomaly and external perineal anomalies was referred to our service. Physical examination showed an epithelized perineal mass with cutaneous orifices, which had urine fistulization, hipotrofic perineal musculature, bilateral congenital clubfoot, hipospadic urethra, criptorquidy bilateral with nonpalpable testis and imperforate anus. A colostomy was constructed immediately after birth. The child underwent excision of perineal mass, bilateral orchidopexy, Duplay neourethroplasty and coloanal anastomosis at 3 months of age. The histopathological examination of the perineal mass revealed a hamartoma.

scholarly journals A Fetus with Imperforate Anus Developing Pulmonary Hypoplasia Triggered by Transient Urethral Obstruction

2021 ◽  
Vol 2021 ◽  
pp. 1-5
Author(s):  
Masatake Toshimitsu ◽  
Takayuki Iriyama ◽  
Seisuke Sayama ◽  
Kan Suzuki ◽  
Satsuki Kakiuchi ◽  
...  
Keyword(s):  
Imperforate Anus ◽  
Pulmonary Hypoplasia ◽  
Urethral Obstruction ◽  
Rare Entity ◽  
Fetal Ultrasonography ◽  
High Type ◽  
First Case ◽  
Pass Through ◽  
Male Neonate ◽  
Lower Urinary

Pulmonary hypoplasia is a rare entity in a fetus with imperforate anus. The fetus was diagnosed with high-type imperforate anus with rectourethral fistula based on the dilated fetal bowel and the presence of bowel calcification at 19 weeks of gestation. As gestation advanced, fetal ultrasonography demonstrated development of pulmonary hypoplasia, progressive bowel dilation, and persistent oligohydramnios from 28 weeks of gestation despite a fluid-filled bladder without hydroureter or hydronephrosis. To prevent further worsening of pulmonary hypoplasia caused by thoracic compression due to bowel dilation and oligohydramnios, a male neonate was delivered by cesarean section at 32 weeks of gestation. The neonate showed respiratory failure requiring full respiratory support. Although a catheter did not pass through the urethra into the bladder at birth, cystourethrography revealed the patency of fistula and stenosed lower urinary tract. Prenatal and postnatal findings strongly suggested that the meconium in the colon might have passed into the urethra in the penis, resulting in the physical blockage of urine outflow to the amniotic space which leads urine flow from the bladder to the colon through the fistula, which resulted in subsequent oligohydramnios and bowel dilation. To the best of our knowledge, this is the first case report of a fetus with imperforate anus developing pulmonary hypoplasia possibly due to urethral obstruction.

scholarly journals OEIS complex – a rare developmental anomaly

2017 ◽  
Vol 06 (04) ◽  
pp. 291-296
Author(s):  
Gaddam Vijaya Lakshmi ◽  
Jacob Abraham ◽  
Deena Sara Mathew
Keyword(s):  
Congenital Anomaly ◽  
Health Care ◽  
Imperforate Anus ◽  
External Genitalia ◽  
Developmental Anomaly ◽  
Congenital Defects ◽  
Surgical Interventions ◽  
Rare Congenital Anomaly ◽  
Live Births ◽  
Health Care Centers

AbstractOEIS complex is a rare congenital anomaly comprising of the following four components: Omphalocoele, Exstrophy of cloaca, Imperforate anus and Spinal defects. It fonns the extreme end of exstrophy-epispadias complex [BEC] of congenital defects. It is associated with anomalies of gastro-intestioaI, urinary and genital systems. External genitalia are bifid, if present. Etiology is not clear. It can be diagnosed by prenatal ultrasound on visualization of 'diaper type' of distribution of anomalies, along with malformations of the limbs. The condition causes severe psychosocial trauma to the parents and family members. In live births, surgical interventions in several stages, are perfonned by skilled expertise only at selected tertiary health care centers. Outcome is highly variable. Prenatal identification of the condition is necessary to give adequate counselling, and have proper planning of the delivery and postnatal management of the baby.

One-stage correction of high imperforate anus in the male neonate

1999 ◽  
Vol 34 (5) ◽  
pp. 834-836 ◽  
Author(s):  
Craig T. Albanese ◽  
Russell W. Jennings ◽  
John B. Lopoo ◽  
Barbara J. Bratton ◽  
Michael R. Harrison
Keyword(s):  
Imperforate Anus ◽  
One Stage ◽  
Male Neonate

Isolated lymphoedema of the external genitalia

1998 ◽  
Vol 1 (1) ◽  
pp. 53-56
Author(s):  
J. VAN DE WETERING DE ROOIJ ◽  
M. F. VAN DRIEL ◽  
P. H. ROBINSON ◽  
H. J. A. MENSINK
Keyword(s):  
External Genitalia

Studies of the oestrous cycle, oestrus and pregnancy in the koala (Phascolarctos cinereus)

Reproduction ◽  
2000 ◽  
pp. 49-57 ◽  
Author(s):  
SD Johnston ◽  
MR McGowan ◽  
P O'Callaghan ◽  
R Cox ◽  
V Nicolson
Keyword(s):  
Luteal Phase ◽  
Post Partum ◽  
Plasma Concentrations ◽  
External Genitalia ◽  
Oestrous Cycle ◽  
Phascolarctos Cinereus ◽  
Pregnant Females ◽  
Peripheral Plasma ◽  
The Mean ◽  
High Concentrations

As an integral part of the development of an artificial insemination programme in the captive koala, female reproductive physiology and behaviour were studied. The oestrous cycle in non-mated and mated koalas was characterized by means of behavioural oestrus, morphology of external genitalia and changes in the peripheral plasma concentrations of oestradiol and progestogen. The mean (+/- SEM) duration of the non-mated oestrous cycle and duration of oestrus in 12 koalas was 32.9 +/- 1.1 (n = 22) and 10.3 +/- 0.9 (n = 24) days, respectively. Although the commencement of oestrous behaviour was associated with increasing or high concentrations of oestradiol, there were no consistent changes in the morphology or appearance of the clitoris, pericloacal region, pouch or mammary teats that could be used to characterize the non-mated cycle. As progestogen concentrations remained at basal values throughout the interoestrous period, non-mated cycles were considered non-luteal and presumed anovulatory. After mating of the 12 koalas, six females gave birth with a mean (+/- SEM) gestation of 34.8 +/- 0.3 days, whereas the remaining six non-parturient females returned to oestrus 49.5 +/- 1. 0 days later. After mating, oestrous behaviour ceased and the progestogen profile showed a significant increase in both pregnant and non-parturient females, indicating that a luteal phase had been induced by the physical act of mating. Progestogen concentrations throughout the luteal phase of the pregnant females were significantly higher than those of non-parturient females. Parturition was associated with a decreasing concentration of progestogen, which was increased above that of basal concentrations until 7 days post partum.

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