Angiomyolipoma(AML) is one of the most common benign renal tumors.
Classical AML is benign, but it can be locally invasive, extending into
perirenal fat, or in rare cases, invading the renal collecting system,
renal vein or inferior vena cava and right atrium. About 10% of
patients clinically diagnosed with renal AML have tuberous sclerosis
complex. Tuberous sclerosis complex can be diagnosed by genetic
diagnosis or clinical manifestation. We report a rare case of a
35-year-old woman who was diagnosed with tuberous sclerosis complex
caused by TSC2 gene mutation, which was characterized by multiple
angiomyolipoma in the right kidney and extended growth to the inferior
vena cava and right atrium. Intracardiac extension is often observed in
the malignant tumor and only seldom seen in benign tumors. Our case
reminds the rare possibility of intracardiac extension in renal AML,
which may potentially result in fatal complications if not appropriately
managed.
Rare Case of Lung Adenocarcinoma Invading the Inferior Vena Cava with Neoplastic Thrombus Extending into the Right Atrium