scholarly journals Choledochal Cyst Associated With Polycystic Kidney Disease: Report of a Case

HPB Surgery ◽  
1999 ◽  
Vol 11 (3) ◽  
pp. 185-190 ◽  
Author(s):  
T. Hasegawa ◽  
M. Kim ◽  
Y. Kitayama ◽  
K. Kitamura ◽  
T. Hiranaka
Keyword(s):  
Bile Duct ◽  
Kidney Disease ◽  
Common Bile Duct ◽  
Pancreatic Duct ◽  
Polycystic Kidney Disease ◽  
Choledochal Cyst ◽  
Amylase Level ◽  
Type I ◽  
Polycystic Kidney ◽  
Endoscopic Retrograde

We report a very rare case of type I choledochal cyst associated with a polycystic kidney disease. A 48- year-old female had been dependent on hemodialysis for chronic renal failure due to polycystic kidney disease and was incidentally diagnosed to have a dilated common bile duct by an ultrasonography. An endoscopic retrograde cholangiopancreatography showed a spindle-shaped, dilated common bile duct (type I choledochal cyst) without visualization of the pancreatic duct. She underwent a resection of the choledochal cyst. Intraoperative cholangiography showed no reflux of contrast medium into the pancreatic duct. Amylase level of the aspirated bile from the bile duct was not elevated. In the case of choledochal cyst combined with renal fibropolycystic disease, pancreaticobiliary maljunction may not contribute to the etiology of choledochal cyst. In such cases, management of choledochal cyst is still controversial and requires further discussion.

scholarly journals Autosomal Dominant Polycystic Kidney Disease with an Asymptomatic Type I Choledochal Cyst

2013 ◽  
Vol 85 (2) ◽  
pp. 205
Author(s):  
Seung Jee Ryu ◽  
Kyung Hoon Kim ◽  
Tae Wan Kim ◽  
Woo Ho Ban ◽  
Su Lim Lee ◽  
...  
Keyword(s):  
Kidney Disease ◽  
Polycystic Kidney Disease ◽  
Choledochal Cyst ◽  
Autosomal Dominant ◽  
Type I ◽  
Polycystic Kidney ◽  
Autosomal Dominant Polycystic Kidney

Bile duct cysts in a patient with autosomal dominant polycystic kidney disease

2004 ◽  
Vol 59 (1) ◽  
pp. 140-142 ◽  
Author(s):  
Tonya R Kolodziejski ◽  
Bassem Y Safadi ◽  
Yasuni Nakanuma ◽  
David E Milkes ◽  
Roy M Soetikno
Keyword(s):  
Bile Duct ◽  
Kidney Disease ◽  
Polycystic Kidney Disease ◽  
Autosomal Dominant ◽  
Polycystic Kidney ◽  
Autosomal Dominant Polycystic Kidney

Laparoscopic management of type VI choledochal cyst with common bile duct stone: report of a case and review of literature

2021 ◽  
Vol 14 (10) ◽  
pp. e244393
Author(s):  
G Revathi ◽  
Brijesh Kumar Singh ◽  
Yashwant Singh Rathore ◽  
Sunil Chumber
Keyword(s):  
Bile Duct ◽  
Common Bile Duct ◽  
Choledochal Cyst ◽  
Cystic Duct ◽  
Incidental Finding ◽  
Laparoscopic Approach ◽  
Biliary Colic ◽  
Type I ◽  
Laparoscopic Management ◽  
Cyst Excision

A young adult male presented with biliary colic and intermittent jaundice for 1 year. Abdomen findings were unremarkable. Routine investigations revealed a raised total bilirubin. On abdominal ultrasonography, common bile duct (CBD) dilatation with multiple stones was noted. On further imaging with magnetic resonance cholangiopancreatography, type I choledochal cyst (CDC) was suspected. A laparoscopic approach was planned. Intraoperatively, dilatation of cystic duct was noted which constitute type VI CDC. Partial malrotation of the gut and accessory right hepatic artery were also noted as incidental finding. Laparoscopic cholecystectomy with CBD exploration and removal of stones, biliary stent placement, cystic duct cyst excision and primary repair of CBD was done. Postoperatively, the patient improved symptomatically with a fall in bilirubin to normal range. We are describing the laparoscopic management of a rare case of type IV CDC which was diagnosed intraoperatively.

Endoscopic retrograde cholangio-pancreatography: a review for endoscopy nurses and assistants

2019 ◽  
Vol 17 (Sup8) ◽  
pp. S8-S14
Author(s):  
Muhammad Waqas Fazal ◽  
Maria Tan ◽  
Shyam Menon
Keyword(s):  
Bile Duct ◽  
Common Bile Duct ◽  
Pancreatic Duct ◽  
Clinical Outcomes ◽  
Endoscopic Retrograde Cholangiopancreatography ◽  
Patient Selection ◽  
Basic Knowledge ◽  
Endoscopic Retrograde ◽  
The Common

Endoscopic retrograde cholangiopancreatography (ERCP) facilitates endoscopic access to the common bile duct and pancreatic duct. It has become central to the management of a variety of benign and malignant pancreatobiliary disorders. ERCP remains a technically challenging procedure and patient selection and pre-assessment is critical to ensure good clinical outcomes. Staff assisting in ERCP should familiarise themselves with the underlying principles and basic knowledge pertaining to various aspects of ERCP.

scholarly journals Chronic obstructive pancreatitis due to a pancreatic cyst in a patient with autosomal dominant polycystic kidney disease

Gut ◽  
1998 ◽  
Vol 42 (1) ◽  
pp. 131-134 ◽  
Author(s):  
D Malka ◽  
P Hammel ◽  
V Vilgrain ◽  
J-F Fléjou ◽  
J Belghiti ◽  
...  
Keyword(s):  
Kidney Disease ◽  
Pancreatic Duct ◽  
Polycystic Kidney Disease ◽  
Main Pancreatic Duct ◽  
Autosomal Dominant ◽  
Pancreatic Cyst ◽  
Chronic Obstructive ◽  
Polycystic Kidney ◽  
Obstructive Pancreatitis ◽  
Autosomal Dominant Polycystic Kidney

Background—Autosomal dominant polycystic kidney disease, the most frequent inherited polycystic disease, is a systemic disorder characterised by the development of numerous and bilateral kidney cysts leading to chronic renal failure. Extrarenal cysts are located mainly in the liver but also in various organs including the pancreas. To our knowledge, complications of pancreatic cysts in this disease have never been reported.Patient—The first case of painful chronic obstructive pancreatitis due to a true pancreatic cyst in a patient with autosomal dominant polycystic kidney disease is reported. Abdominal transparietal and endoscopic ultrasonography, computed tomography, and endoscopic retrograde cholangiopancreatography showed a cystic lesion in the body of the pancreas associated with upstream dilatation of the main pancreatic duct. Intraoperative ultrasonography before and after cyst fluid aspiration, and pancreatography and pathological examination of the resected distal pancreas confirmed that both main pancreatic duct enlargement and chronic pancreatitis were caused by a benign cyst.Conclusion—Chronic obstructive pancreatitis should be added to the extrarenal complications of autosomal dominant polycystic kidney disease.

scholarly journals Dietary phosphate restriction attenuates polycystic kidney disease in mice

2020 ◽  
Vol 318 (1) ◽  
pp. F35-F42 ◽  
Author(s):  
Faith Omede ◽  
Shiqin Zhang ◽  
Cassandra Johnson ◽  
Emily Daniel ◽  
Yan Zhang ◽  
...  
Keyword(s):  
Gene Expression ◽  
Body Weight ◽  
Kidney Disease ◽  
Polycystic Kidney Disease ◽  
Type I ◽  
Tubular Injury ◽  
Polycystic Kidney ◽  
Restricted Diet ◽  
Kidney Fibrosis ◽  
Dietary Phosphate

Studies in rodents with reduced nephron mass have suggested a strong positive correlation between dietary phosphate consumption and CKD progression. Prior work by our group demonstrated that dietary phosphate restriction can prevent tubular injury and microcyst formation in rodents with glomerulonephritis. Tubular injury and cystic dilation of tubules are key contributors to kidney function decline in polycystic kidney disease (PKD). Here, we determined whether dietary phosphate restriction slows renal cyst growth and fibrosis in a mouse model of PKD. Pcy/pcy mice received a normal phosphate (0.54%) or a phosphate-restricted (0.02%) diet ( n = 10/group) from 7 to 20 wk of age. All of the other major dietary constituents, including protein source and content, were comparable between the two diets. At 20 wk, body weight, kidney weight-to-body weight ratio (KW/BW), cystic area, cyst number, and kidney fibrosis were quantified. Pcy/pcy mice fed a phosphate-restricted diet had lower serum phosphate, fibroblast growth factor 23, and parathyroid hormone levels, along with elevated serum calcium levels and increased kidney Klotho gene expression compared with mice that consumed the control diet. Dietary phosphate restriction resulted in a 25% lower KW/BW ratio and reduced the cyst number, cystic index, and gene expression for the tubular injury markers neutrophil gelatinase-associated lipocalin and interleukin-18. Mice fed the phosphate-restricted diet exhibited lower kidney expression for pathways involved in collagen deposition and myofibroblast activation (collagen type I-α1, phosphorylated SMAD3, and α-smooth muscle actin); however, histological differences in kidney fibrosis were not appreciated. Dietary phosphate restriction slows cystogenesis and inhibits the activation of key pathways in the generation of kidney fibrosis in PKD mice.

Polycystic kidney disease in a patient with the oral-facial-digital syndrome-Type I*

2008 ◽  
Vol 9 (2) ◽  
pp. 183-186 ◽  
Author(s):  
M. J. E. Harrod ◽  
J. Stokes ◽  
L. F. Peede ◽  
J. L. Goldstein
Keyword(s):  
Kidney Disease ◽  
Polycystic Kidney Disease ◽  
Type I ◽  
Syndrome Type ◽  
Polycystic Kidney
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