scholarly journals Characteristics of Autoimmune Pulmonary Alveolar Proteinosis Complicated with Other Interstitial Pneumonia

2020 ◽  
Author(s):  
M. Kondo ◽  
T. Hanawa ◽  
K. Isono ◽  
N. Honda ◽  
A. Kurokawa ◽  
...  
Keyword(s):  
Interstitial Pneumonia ◽  
Pulmonary Alveolar Proteinosis ◽  
Alveolar Proteinosis

GENETIC DISORDERS OF SURFACTANT PROTEINS

2021 ◽  
Vol 100 (5) ◽  
pp. 82-89
Author(s):  
M.A. Zhestkova ◽  
◽  
D.Yu. Ovsyannikov ◽  
Keyword(s):  
Differential Diagnosis ◽  
Interstitial Pneumonia ◽  
Lung Diseases ◽  
Neonatal Period ◽  
Pulmonary Alveolar Proteinosis ◽  
Genetic Disorders ◽  
Interstitial Lung Diseases ◽  
Surfactant Proteins ◽  
Nonspecific Interstitial Pneumonia ◽  
Alveolar Proteinosis

The literature review provides up-to-date information on rare interstitial lung diseases, manifesting both in children, starting from the neonatal period, and in adults, – genetic disorders of surfactant proteins B, C, ATP-binding cassette protein A3 (ABCA3), manifested by such histopathological patterns, as chronic pneumonitis of infants, pulmonary alveolar proteinosis, desquamative interstitial pneumonia , nonspecific interstitial pneumonia. Information on epidemiology, genetics, pathogenesis, clinical picture, diagnosis and differential diagnosis, treatment of these diseases is given.

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