Two Surgical Cases of Acute Aortic Dissection in Pregnancy with Marfan Syndrome

2007 ◽  
Vol 15 (5) ◽  
pp. e63-e65 ◽  
Author(s):  
Hidetaka Wakiyama ◽  
Michihiro Nasu ◽  
Hiroshi Fujiwara ◽  
Aki Kitamura ◽  
Yukikatsu Okada
Keyword(s):  
Aortic Dissection ◽  
Marfan Syndrome ◽  
Acute Aortic Dissection ◽  
Deep Hypothermia ◽  
Aortic Root Replacement ◽  
The Other ◽  
Normal Delivery ◽  
First Case ◽  
Type A Dissection ◽  
In Pregnancy

We describe 2 surgical cases of acute aortic type A dissection during pregnancy in women with Marfan syndrome. Both of them underwent emergency aortic root replacement under deep hypothermia; one patient was in her 21st week of pregnancy and the other was treated 1 day after a normal delivery. The patients experienced fair postoperative courses, but intrauterine fetus death was confirmed in the first case.

scholarly journals Acute Aortic Dissection in Pregnancy in a Woman with Undiagnosed Marfan Syndrome

2012 ◽  
Vol 2012 ◽  
pp. 1-3 ◽  
Author(s):  
Mandana Master ◽  
Gavin Day
Keyword(s):  
Aortic Dissection ◽  
Marfan Syndrome ◽  
Acute Aortic Dissection ◽  
Congenital Abnormalities ◽  
Surgical Repair ◽  
Phenotypic Expression ◽  
Sudden Onset ◽  
Lower Segment Caesarean Section ◽  
Type B Dissection ◽  
Type A Dissection

We report a case of acute aortic dissection in a lady of 28 weeks of gestation with undiagnosed Marfan syndrome. The patient had been seen in our antenatal clinics. Her history documented in her pregnancy record was negative for genetic/congenital abnormalities. There was no family history documented. Subsequently, at 28 weeks of gestation, the patient presented with sudden onset chest, jaw, and back pain. Further history revealed that her father had died at the age of 27 of an aortic dissection. Echocardiography showed aortic root dissection with occlusion of aortic branches. She subsequently underwent an emergency lower segment caesarean section followed by surgical repair of type A dissection. A simultaneous type B dissection was managed conservatively. On later examination, our patient fulfilled the diagnostic criteria for phenotypic expression of Marfan syndrome. Genetic testing also confirmed that she has a mutation of the fibrillin (FBN 1) gene associated with the disease.

Moderate vs Deep Hypothermia in Type A Acute Aortic Dissection Repair: Insights from IRAD

2021 ◽  
Author(s):  
Stevan S. Pupovac ◽  
Jonathan M. Hemli ◽  
Joseph E. Bavaria ◽  
Himanshu J. Patel ◽  
Santi Trimarchi ◽  
...  
Keyword(s):  
Aortic Dissection ◽  
Acute Aortic Dissection ◽  
Type A ◽  
Deep Hypothermia

scholarly journals The Characteristics of Acute Aortic Dissection among Young Chinese Patients: A Comparison between Marfan Syndrome and Non-Marfan Syndrome Patients

2009 ◽  
Vol 50 (2) ◽  
pp. 239 ◽  
Author(s):  
Shih-Hung Tsai ◽  
Yen-Yue Lin ◽  
Chin-Wang Hsu ◽  
Yu-Long Chen ◽  
Min-Tser Liao ◽  
...  
Keyword(s):  
Aortic Dissection ◽  
Marfan Syndrome ◽  
Acute Aortic Dissection ◽  
Chinese Patients

STABILISE Technique for a Non-A Non-B Acute Aortic Dissection in Marfan Syndrome

2021 ◽  
Vol 70 ◽  
pp. 569.e5-569.e10
Author(s):  
Raphael J. Soler ◽  
Michel A. Bartoli ◽  
Jeremy Bourenne ◽  
Alberto Riberi ◽  
David Lagier ◽  
...  
Keyword(s):  
Aortic Dissection ◽  
Marfan Syndrome ◽  
Acute Aortic Dissection

scholarly journals Acute aortic dissection in a patient with Marfan syndrome during advanced pregnancy

2019 ◽  
Vol 35 (2) ◽  
pp. 499-502
Author(s):  
Beti Kostadinovska ◽  
Aleksandar Nikolic ◽  
Dimche Slaveski ◽  
Milan Milojevic
Keyword(s):  
Aortic Dissection ◽  
Marfan Syndrome ◽  
Acute Aortic Dissection
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