Anterior–Posterior Persistent Fetal Vasculature With Multiple Stalks: Persistent Vasa Hyaloidea Propria

2018 ◽  
Vol 2 (4) ◽  
pp. 240-243 ◽  
Author(s):  
Elizabeth J. Rossin ◽  
Deborah K. VanderVeen ◽  
Yoshihiro Yonekawa
Keyword(s):  
Fluorescein Angiography ◽  
Optic Disc ◽  
Vascular Network ◽  
Atypical Presentation ◽  
Posterior Portion ◽  
Ocular Development ◽  
Persistent Fetal Vasculature ◽  
Tunica Vasculosa Lentis ◽  
Anterior Posterior

An 8-week-old boy referred for an abnormal pupil was found to have an atypical presentation of persistent fetal vasculature (PFV) with multiple vascular stalks. Examination under anesthesia with fluorescein angiography (FA) revealed 2 perfused persistent hyaloid vessels, one extending from the optic disc and another from the inferonasal retina. These vessels meet anteriorly to form a vascular network at the lens, which is the remnant of the tunica vasculosa lentis. Although the posterior portion of PFV typically presents as a single stalk attached at the optic disc, this case features an atypical presentation of 2 distinct vascular stalks, which may expand our understanding of ocular development and pathogenesis of PFV. We hypothesize that the aberrant additional stalk may represent failure of the vasa hyaloidea propria (tributaries of the hyaloid artery) to regress.

scholarly journals Fluorescein Angiography in Persistent Fetal Vasculature

Ophthalmology ◽  
2017 ◽  
Vol 124 (4) ◽  
pp. 455 ◽  
Author(s):  
Karen W. Jeng-Miller ◽  
Anthony Joseph ◽  
Caroline R. Baumal
Keyword(s):  
Fluorescein Angiography ◽  
Persistent Fetal Vasculature

scholarly journals Exudative Type 3 Retinal Arteriovenous Malformation in a Pediatric Patient

2018 ◽  
Vol 9 (3) ◽  
pp. 504-509
Author(s):  
Helena Dens ◽  
Ingele Casteels
Keyword(s):  
Optical Coherence Tomography ◽  
Differential Diagnosis ◽  
Arteriovenous Malformation ◽  
Fluorescein Angiography ◽  
Optic Disc ◽  
Optical Coherence Tomography Angiography ◽  
Imaging Techniques ◽  
Optical Coherence ◽  
The Right ◽  
Type 3

We describe a 7-year-old girl who developed exudation nasally to the right optic disc due to retinal arteriovenous malformation. Fluorescein angiography, spectral domain optical coherence tomography, and optical coherence tomography angiography were performed. We give an overview of the different imaging techniques and discuss the differential diagnosis. Since there was no visual impairment, no treatment was started. A spontaneous decrease in edema and exudation was noted after 6 months.

scholarly journals Optic nerve head retinal artery macroaneurysm: Report of a case

2019 ◽  
Vol 7 ◽  
pp. 2050313X1986947
Author(s):  
Ramesh Venkatesh ◽  
Prachi Gurav
Keyword(s):  
Optic Nerve ◽  
Fluorescein Angiography ◽  
Optic Disc ◽  
Optic Nerve Head ◽  
Hypertensive Retinopathy ◽  
Fundus Examination ◽  
Elderly Male ◽  
Spontaneous Involution ◽  
Retinal Artery ◽  
Retinal Artery Macroaneurysm

A 61-year-old elderly male, hypertensive patient presented to the retina clinic with sudden drop in vision in the left eye for 6 days. His best-corrected visual acuity at presentation was counting fingers close to face. Fundus examination of the left eye revealed the presence of subretinal and preretinal haemorrhage at the macula along with hypertensive retinopathy changes in both eyes. Fluorescein angiography was done, which showed a retinal artery macroaneurysm at the optic nerve head. Optical coherence tomogram through the optic nerve head also confirmed the presence of retinal artery macroaneurysm. The patient was treated with injection of 0.4 cc of 100% C3F8 to displace the blood off the macula. At final follow-up visit at 2 months post treatment, his vision improved to 6/12, N8. Fundus examination showed a small residual altered blood nasal to the fovea. No treatment was however done to the retinal artery macroaneurysm due to its atypical location and chance of spontaneous involution. In conclusion, retinal artery macroaneurysm at the optic disc is extremely uncommon. Identification of the retinal artery macroaneurysm lesion is more difficult in glaucoma patients due to the large and deep optic cup. Fluorescein angiography remains the main investigative modality to confirm the diagnosis. Spontaneous involution still remains the mainstay of treatment in optic disc retinal artery macroaneurysm.

Visual prognosis of posterior and combined persistent fetal vasculature

2019 ◽  
Vol 30 (2) ◽  
pp. 284-288 ◽  
Author(s):  
Veronique Promelle ◽  
Sophie Bryselbout ◽  
Solange Milazzo
Keyword(s):  
Visual Acuity ◽  
Vascular System ◽  
Cataract Extraction ◽  
Visual Prognosis ◽  
Visual Outcomes ◽  
Persistent Fetal Vasculature ◽  
Single Center Study ◽  
Bilateral Impairment ◽  
Anterior Posterior

Introduction: The persistent fetal vasculature refers to congenital anomalies of the globe resulting from the abnormal persistence of the hyaloid vascular system. It can present as anterior, posterior, or combined form. The aim of this study was to report the visual outcomes of posterior and combined forms of persistent fetal vasculature. Methods: This retrospective, single-center study included every patient referred to our outpatient clinic with a posterior or combined form of persistent fetal vasculature. The primary endpoint was the visual acuity of the impaired eye, or of the best eye if bilateral, at the end of follow-up. Results: In total, 18 eyes of 14 patients (10 males) were included. The combined form was the most prevalent (12 of 18 eyes), and 4 of 14 patients had bilateral impairment. The range of assessed visual acuity was from 20/2000 to 20/25. The best visual acuity in patients having undergone a surgical procedure was 20/63 (cataract extraction = 3, combined phacovitrectomy = 1). In patients who had been treated for amblyopia with patching, without surgery, the best visual acuity measured was 20/100 (5 patients). Among patients who had neither surgery nor patching therapy, there was one 63-year-old patient with a 20/25 visual acuity; the other ones had a low visual acuity of less than 20/200. All included eyes presented with nystagmus, amblyopia, and/or strabismus at the end of follow-up. Conclusion: The posterior and combined forms of persistent fetal vasculature are of poor visual prognosis. The severe or occulting presentations require surgery to obtain the same visual outcomes as the moderate forms treated for amblyopia with patching therapy.

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