scholarly journals A variant of Goldenhar syndrome

2017 ◽  
Vol 4 (3) ◽  
pp. 1115
Author(s):  
Akanksha Jaiswal ◽  
Thumjaa Annamalai ◽  
Nirupama M ◽  
Shafath Ahmed M ◽  
Ramya V
Keyword(s):  
Hearing Loss ◽  
Facial Nerve ◽  
Sensorineural Hearing Loss ◽  
Nerve Palsy ◽  
Facial Nerve Palsy ◽  
Cardiac Anomaly ◽  
Goldenhar Syndrome ◽  
Renal Anomaly ◽  
Side Face ◽  
The Right

We report a case of 10 months old child with a variant of Goldenhar syndrome in the form of microtia of right ear, microsomia of the right-side face, right facial nerve palsy with cardiac anomaly, renal anomaly and sensorineural hearing loss on the right side which were rare associations prompted to report this case.

Congenital internal auditory canal stenosis

2003 ◽  
Vol 117 (10) ◽  
pp. 784-787 ◽  
Author(s):  
Seung Kuk Baek ◽  
Sung Won Chae ◽  
Hak Hyun Jung
Keyword(s):  
Hearing Loss ◽  
High Resolution ◽  
Facial Nerve ◽  
Ct Scan ◽  
Sensorineural Hearing Loss ◽  
Temporal Bone ◽  
Nerve Palsy ◽  
Facial Nerve Palsy ◽  
Internal Auditory Canal ◽  
Canal Stenosis

Congenital internal auditory canal stenosis is a rare cause of sensorineural hearing loss in children. A retrospective analysis including clinical manifestation and radiological findings was made for seven patients who were diagnosed with congenital internal auditory canal stenosis from 1996 to 2002. Chief presenting symptoms were hearing loss, facial nerve palsy, dizziness, and tinnitus. Hearing loss including deafness was found in five cases, vestibular function loss in four cases, and profound functional loss of facial nerve in two cases. In all cases, the diameter of the internal auditory canal was less than 2 mm on high-resolution temporal bone computed tomography (CT) scan. Two cases revealed bilateral internal auditory canal stenosis, and others were unilaterally involved cases. Congenital internal auditory canal stenosis can be an important cause of sensorineural hearing loss, facial nerve palsy, and vestibular dysfunction. High resolution temporal bone CT scan and magnetic resonance (MR) imaging were important tools for diagnosis.

scholarly journals A Rare Case of Vertebrobasilar Dolichoectasia Presenting with Ipsilateral Facial Paresis and Concomitant Severe Sensorineural Hearing Loss

2014 ◽  
Vol 29 (1) ◽  
pp. 20-22
Author(s):  
Mee Ling Tang ◽  
Govindaraju Revadi ◽  
Raman Rajagopalan ◽  
Sushil Brito-Mutunayagam
Keyword(s):  
Hearing Loss ◽  
Facial Nerve ◽  
Sensorineural Hearing Loss ◽  
Basilar Artery ◽  
Nerve Palsy ◽  
Facial Nerve Palsy ◽  
Sensorineural Hearing ◽  
Prior History ◽  
Vertebrobasilar Dolichoectasia ◽  
Nerve Paresis

Objective: To report a case of vertebrobasilar dolichoectasia presenting with ipsilateral facial nerve paresis and concomitant severe sensorineural hearing loss.   Methods:                Design: Case Report                Setting: Secondary Government Hospital                Patient: One   Results:  We report a case of vertebrobasilar dolichoectasia with concomitant ipsilateral facial nerve paresis and severe sensorineural hearing loss in an elderly female.  She presented to us with left facial nerve palsy House-Brackmann Grade III with prior history of ipsilateral sensorineural hearing loss.  MRI of the brain showed normal inner ear structures, but revealed a dilated and tortuous basilar artery with compression on the left medulla and possible branches of anterior inferior cerebellar artery as it coursed superiorly, and possible partial thrombosis of proximal basilar artery.    Conclusion:  Concommitant facial nerve paresis and sensorineural hearing loss can be the clinical presentations of this rare but important condition.  MRI is vital in diagnosing vertebrobasilar dolichoectasia.   Keywords: Vertebrobasilar dolichoectasia, facial nerve palsy, sensorineural hearing loss, basilar artery

scholarly journals Bilateral Internal Auditory Canal (IAC) Duplication with Congenital Sensorineural Hearing Loss (SNHL)-A Case Report

2021 ◽  
Vol 20 (4) ◽  
Author(s):  
Nik Adilah Nik Othman ◽  
Nur Saadah Mohamad ◽  
Ahmad Aizuddin Mohamad Jamali ◽  
Mohd Shafie Abdullah ◽  
Mohd Khairi Md Daud
Keyword(s):  
Hearing Loss ◽  
Down Syndrome ◽  
Facial Nerve ◽  
Sensorineural Hearing Loss ◽  
Nerve Palsy ◽  
Facial Nerve Palsy ◽  
Internal Auditory Canal ◽  
Sensorineural Hearing ◽  
Image Finding ◽  
Suitable Treatment

Duplication of the internal auditory canal is a rare entity. It can be unilateral or bilateral involvement and usually found during an investigation of sensorineural hearing loss or facial nerve palsy. We report this image finding in a child with Down syndrome with bilateral profound sensorineural hearing loss. There was no facial nerve palsy. We highlight the rarity of this image finding and the importance of imaging for detection of middle and inner ear abnormality in a case of congenital sensorineural hearing loss as it helps in decision making for the suitable treatment. Keywords: Duplicate IAC; Bilateral Duplicate IAC; sensorineural hearing loss; Down syndrome

Hearing loss

2018 ◽  
Author(s):  
James Ramsden
Keyword(s):  
Hearing Loss ◽  
Facial Nerve ◽  
Middle Ear ◽  
Cranial Nerve ◽  
Nerve Palsy ◽  
Facial Nerve Palsy ◽  
Conductive Hearing Loss ◽  
Ear Canal ◽  
Eighth Cranial Nerve ◽  
Conductive Hearing

Hearing loss must be divided into conductive hearing loss (CHL) and sensorineural hearing loss (SNHL). CHL is caused by sound not reaching the cochlear (abnormality of the ear canal, tympanic membrane, middle ear, or ossicles), whereas SNHL is a condition affecting the cochlear or auditory (eighth cranial) nerve. Hearing loss may be accompanied by other cardinal signs of ear disease, such as pain or discharge from the ear, vertigo, facial nerve palsy, and tinnitus, which guide the diagnosis. This chapter describes the approach to the patient with hearing loss.

scholarly journals Kawasaki disease manifesting as bilateral facial nerve palsy and meningitis: a case report and literature review

2019 ◽  
Vol 47 (8) ◽  
pp. 4014-4018 ◽  
Author(s):  
Bo Zhang ◽  
Yunpeng Hao ◽  
Yanfeng Zhang ◽  
Nuo Yang ◽  
Hang Li ◽  
...  
Keyword(s):  
Case Report ◽  
Kawasaki Disease ◽  
Facial Nerve ◽  
Nerve Palsy ◽  
Facial Nerve Palsy ◽  
Brain Magnetic Resonance Imaging ◽  
Neurological Complications ◽  
Appropriate Treatment ◽  
History Of ◽  
The Right

Background Kawasaki disease (KD) is an acute multisystem vasculitic syndrome that predominantly affects infants and young children. Neurological complications are rare in patients with KD and the diagnosis is challenging. We report a case of KD that manifested as bilateral facial nerve palsy and meningitis. Case report A 6-month-old boy presented with a 10-day history of fever. Four days before admission, the patient developed a rash, conjunctival injection, perioral and perianal excoriation, and bilateral facial nerve palsy. Brain magnetic resonance imaging was normal. Echocardiography showed dilated coronary arteries and coronary artery aneurysms. A cerebrospinal fluid examination showed an elevated leukocyte count. A diagnosis of KD was made, and the patient was treated with gamma globulin and aspirin. The patient’s fever subsided on the following day and the right-sided facial nerve palsy was relieved 1 month later. An 18-month follow-up showed that the left-sided facial nerve palsy persisted and the patient’s condition remained stable. Conclusion KD manifesting as bilateral facial nerve palsy and meningitis is extremely rare. Clinicians should be aware of this condition, and early diagnosis and appropriate treatment should be emphasized.

The Impact of Tinnitus and Vertigo on Patient-Perceived Quality of Life After Cerebellopontine Angle Surgery

Neurosurgery ◽  
2010 ◽  
Vol 67 (3) ◽  
pp. 601-610 ◽  
Author(s):  
Juergen Grauvogel ◽  
Jan Kaminsky ◽  
Steffen K. Rosahl
Keyword(s):  
Quality Of Life ◽  
Hearing Loss ◽  
Facial Nerve ◽  
Cerebellopontine Angle ◽  
Nerve Palsy ◽  
Facial Nerve Palsy ◽  
Classification Systems ◽  
Hearing Function ◽  
The Impact

Abstract BACKGROUND Quality of life (QOL) has come into focus after treatment for cerebellopontine angle (CPA) lesions. OBJECTIVE This study compared subjective (tinnitus, vertigo) and objective (hearing loss, facial palsy) results of CPA surgery with patient-perceived impairment of QOL. METHODS A retrospective analysis of a consecutive series of 48 patients operated on for either a vestibular schwannoma or a meningioma in the CPA was performed. Patient's subjective impairment of QOL by tinnitus, vertigo, hearing loss, and facial nerve palsy was assessed by a visual analog scale (VAS). Objective facial nerve and hearing function were determined using House-Brackmann and Gardner-Robertson classification systems, respectively. RESULTS The return rate of questionnaires was 64.4%, with mean follow-up time of 417.2 (± 46.4) days. Mean preoperative tinnitus score was 2.5 (± 0.5) and increased to 4.6 (± 0.7) postoperatively (P < .01). The vertigo score increased from 2.0 (± 0.3) to 5.8 (± 0.6) (P < .001). Pre- and postoperative values for hearing loss were 3.4 (± 0.6) and 5.9 (± 0.7), respectively (P < .01), and for facial nerve palsy 0.7 (± 0.4) compared with 3.1 (± 0.6) postoperatively (P < .01). House-Brackmann grade 1 or 2 was determined in 87.1% of patients before and in 80.6% after surgery. Serviceable hearing (Gardner-Robertson classes I-III) was found in 75% before and in 64.3% after surgery. CONCLUSION Preservation of facial nerve and hearing function are not the only important criteria defining QOL after CPA surgery. Tinnitus and vertigo may have a significant underestimated impact on the patient's postoperative course and QOL.

Mobius syndrome: a case report

2003 ◽  
Vol 26 (2) ◽  
pp. 207-209
Author(s):  
G. Aren
Keyword(s):  
Case Report ◽  
Facial Expression ◽  
Facial Nerve ◽  
Nerve Palsy ◽  
Facial Nerve Palsy ◽  
Dental Treatment ◽  
Tooth Decay ◽  
Möbius Syndrome ◽  
The Right

Mobius Syndrome is characterized by showing unilateral facial nerve palsy of the sixth and seventh nerves, lack of facial expression, inability to smile and to tightly close the right eyelids. In this report, a 7-year-old-boy with Mobius syndrome is presented. He had asymmetry of facial expression, anomalies of fingers and severe tooth decay. After dental treatment, the periodic re-care visits should be done according to the eruption pattern.

Primary middle-ear lymphoma in a child

2003 ◽  
Vol 117 (3) ◽  
pp. 205-207 ◽  
Author(s):  
Emer E. Lang ◽  
Rory M. Walsh ◽  
Mary Leader
Keyword(s):  
Hearing Loss ◽  
Facial Nerve ◽  
Temporal Bone ◽  
Middle Ear ◽  
Nerve Palsy ◽  
Facial Nerve Palsy ◽  
Conductive Hearing Loss ◽  
Motor Neurone ◽  
Hodgkin's Lymphoma ◽  
Conductive Hearing

The case of a five year old boy who presented with a lower motor neurone facial nerve palsy secondary to primary non-Hodgkin’s lymphoma (NHL) of the middle ear is discussed. Any child who presents with a facial nerve palsy and conductive hearing loss requires thorough evaluation to exclude the possibility of temporal bone malignancy.

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