scholarly journals Cochlear Otosclerosis: An Undiagnosed Cause of Progressive Sensorineural Hearing Loss

2020 ◽  
Vol 28 (2) ◽  
pp. 127-137
Author(s):  
Asish Kumar Lahiri ◽  
Anandita Gupta ◽  
Rakesh Vohra ◽  
Shalabh Sharma ◽  
Satinder Singh
Keyword(s):  
Hearing Loss ◽  
High Resolution ◽  
Ct Scan ◽  
Sensorineural Hearing Loss ◽  
Temporal Bone ◽  
Young Patients ◽  
Oval Window ◽  
Sensorineural Hearing ◽  
Unknown Etiology ◽  
High Resolution Ct

Introduction Otosclerosis presents as conductive or mixed hearing loss depending upon the stage of the disease. Isolated sensorineural hearing loss though known to occur has been rarely reported. Pure cochlear otosclerosis presenting as sensorineural hearing loss should be considered as a differential diagnosis in young patients presenting with progressive hearing loss. The aim of this article is to note the prevalence of cochlear otosclerosis in young patients presenting with progressive sensorineural hearing loss.  Materials and Methods Retrospective chart analysis of 19 patients who presented with progressive SNHL with unknown etiology was done. Results Otosclerosis involving the pericochlear region was diagnosed in 27 ears which was identified by high resolution CT scan of temporal bone. In four ears, in addition, there was demineralization just anterior to oval window without clinical evidence of stapes fixation. Conclusion In young patients with progressive SNHL, high resolution CT scan of temporal bone should be done to identify progressive cochlear otosclerosis. Medical management should be initiated in these patients to halt the progression of disease.

Congenital internal auditory canal stenosis

2003 ◽  
Vol 117 (10) ◽  
pp. 784-787 ◽  
Author(s):  
Seung Kuk Baek ◽  
Sung Won Chae ◽  
Hak Hyun Jung
Keyword(s):  
Hearing Loss ◽  
High Resolution ◽  
Facial Nerve ◽  
Ct Scan ◽  
Sensorineural Hearing Loss ◽  
Temporal Bone ◽  
Nerve Palsy ◽  
Facial Nerve Palsy ◽  
Internal Auditory Canal ◽  
Canal Stenosis

Congenital internal auditory canal stenosis is a rare cause of sensorineural hearing loss in children. A retrospective analysis including clinical manifestation and radiological findings was made for seven patients who were diagnosed with congenital internal auditory canal stenosis from 1996 to 2002. Chief presenting symptoms were hearing loss, facial nerve palsy, dizziness, and tinnitus. Hearing loss including deafness was found in five cases, vestibular function loss in four cases, and profound functional loss of facial nerve in two cases. In all cases, the diameter of the internal auditory canal was less than 2 mm on high-resolution temporal bone computed tomography (CT) scan. Two cases revealed bilateral internal auditory canal stenosis, and others were unilaterally involved cases. Congenital internal auditory canal stenosis can be an important cause of sensorineural hearing loss, facial nerve palsy, and vestibular dysfunction. High resolution temporal bone CT scan and magnetic resonance (MR) imaging were important tools for diagnosis.

A comparison of high resolution CT scan of temporal bone and operative findings in middle ear cholesteatoma

1993 ◽  
Vol 29 (5) ◽  
pp. 896
Author(s):  
Tae Beom Kweon ◽  
Hun Seong ◽  
Mal Soon Cheon ◽  
Hack Jin Kim ◽  
Keung Jae Jang ◽  
...  
Keyword(s):  
High Resolution ◽  
Ct Scan ◽  
Temporal Bone ◽  
Middle Ear ◽  
High Resolution Ct ◽  
Middle Ear Cholesteatoma ◽  
Operative Findings

scholarly journals Radiological diagnosis of round and oval window niches with high resolution CT scanning of the temporal bone.

1988 ◽  
Vol 81 (6) ◽  
pp. 811-814
Author(s):  
Kiyotaka Murata ◽  
Michio Isono ◽  
Hiroyuki Oiki ◽  
Fumihiko Ohta ◽  
Akio Yoshida ◽  
...  
Keyword(s):  
High Resolution ◽  
Temporal Bone ◽  
Ct Scanning ◽  
Oval Window ◽  
Radiological Diagnosis ◽  
High Resolution Ct

Speech intelligibility in patients of different ages with chronic sensorineural hearing loss

2021 ◽  
Vol 20 (4) ◽  
pp. 8-14
Author(s):  
M. Yu. Boboshko ◽  
◽  
E. V. Zhilinskaya ◽  
◽  
Keyword(s):  
Hearing Loss ◽  
Sensorineural Hearing Loss ◽  
Speech Intelligibility ◽  
Comprehensive Evaluation ◽  
Young Patients ◽  
Sensorineural Hearing ◽  
Speech Audiometry ◽  
Similar Degree ◽  
Different Ages ◽  
Monosyllabic Words

Deterioration in speech intelligibility, the most common complaint of people with hearing loss, leads to social isolation and dramatically reduces the quality of life. The correction of peripheral hearing loss by hearing aid fitting does not always solve this problem in patients with chronic sensorineural hearing loss (SNHL). That is why in the process of audiological examination of patients with complaints of hearing loss, it is necessary to include methods of speech audiometry, which make it possible to comprehensively assess the functioning of the auditory system. The aim of the study: assessment of speech intelligibility in patients of different ages with SNHL. 94 people from 20 to 74 years of age were examined: 54 patients with SNHL (14 young and 40 elderly) and 40 people with normal hearing thresholds (20 young and 20 elderly). Besides the standard audiological examination, speech audiometry testing was conducted: evaluation of monosyllabic words intelligibility in quiet, binaural rapidly alternating speech test, dichotic digits test, Russian matrix sentence test (RuMatrix). Results: Speech intelligibility in elderly patients with SNHL was shown to be significantly worse than in young patients with a similar degree of hearing loss. The RuMatrix test in noise was proved to be the most sensitive test for comprehensive evaluation of the hearing system functioning.

Imaging case study: enlarged superior vestibular nerve canal with sensorineural hearing loss

2008 ◽  
Vol 123 (5) ◽  
pp. 572-574 ◽  
Author(s):  
M I Redleaf ◽  
J M Pinto ◽  
J J Klemens
Keyword(s):  
Computed Tomography ◽  
Hearing Loss ◽  
Case Report ◽  
Sensorineural Hearing Loss ◽  
Temporal Bone ◽  
Male Infant ◽  
Vestibular Nerve ◽  
Sensorineural Hearing ◽  
Inferior Vestibular Nerve

AbstractObjective:We report a new temporal bone anomaly – an enlarged superior vestibular nerve canal – associated with sensorineural hearing loss.Case report:A 10-month-old male infant presented with sensorineural hearing loss together with bilaterally enlarged superior vestibular nerve canals. Compared with published temporal bone computed tomography measurements, our patient's canals were normal in length but approximately double the normal width. In addition, careful review of the imaging did not clearly identify a bony wedge between the superior and inferior vestibular nerve canals.Conclusion:Enlarged superior vestibular nerve canal malformation may be a marker for sensorineural hearing loss. Increased vigilance amongst otologists may establish the prevalence of this anomaly and its possible effects on hearing.

scholarly journals Perilymphatic fistula and pneumolabyrinth without temporal bone fracture: a rare entity

2019 ◽  
Vol 12 (3) ◽  
pp. e228457 ◽  
Author(s):  
Ana Sousa Menezes ◽  
Daniela Ribeiro ◽  
Daniel Alves Miranda ◽  
Sara Martins Pereira
Keyword(s):  
Hearing Loss ◽  
Sensorineural Hearing Loss ◽  
Temporal Bone ◽  
Bone Fracture ◽  
Round Window ◽  
Sensorineural Hearing ◽  
Temporal Bone Fracture ◽  
Perilymphatic Fistula ◽  
Hearing Thresholds ◽  
Post Traumatic

Post-traumatic pneumolabyrinth is an uncommon clinical entity, particularly in the absence of temporal bone fracture. We report the case of a patient who presented to our emergency department with a headache, sudden left hearing loss and severe dizziness which began after a traumatic brain injury 3 days earlier. On examination, the patient presented signs of left vestibulopathy, left sensorineural hearing loss and positive fistula test, normal otoscopy and without focal neurological signs. The audiometry confirmed profound left sensorineural hearing loss. Cranial CT revealed a right occipital bone fracture and left frontal subdural haematoma, without signs of temporal bone fracture. Temporal bone high-resolution CT scan revealed left pneumolabyrinth affecting the vestibule and cochlea. Exploratory tympanotomy revealed perilymphatic fistula at the location of the round window. The sealing of defect was performed using lobule fat and fibrin glue. He presented complete resolution of the vestibular complaints, though the hearing thresholds remained stable.

Sign in / Sign up

Export Citation Format

Share Document