scholarly journals Case Report: ALCAPA syndrome: successful repair with an anatomical and physiological alternative surgical technique

F1000Research ◽  
2016 ◽  
Vol 5 ◽  
pp. 1680
Author(s):  
Luis Gustavo Vilá Mollinedo ◽  
Andrés Jaime Uribe ◽  
José Luis Aceves Chimal ◽  
Roberto Pablo Martínez-Rubio ◽  
Karen Patricia Hernández-Romero

Anomalous left coronary artery from the pulmonary artery, or ALCAPA syndrome, is a rare congenital cardiac disease that can cause myocardial infarction, heart failure and even death in paediatric patients. Only few untreated patients survive until adult age. Here we present the case of a 33-year-old female patient with paroxysmal tachycardia, syncope and mild exertional dyspnoea. She was diagnosed with ALCAPA syndrome and underwent surgical correction with an alternative technique of left main coronary artery extension to the aorta.

F1000Research ◽  
2016 ◽  
Vol 5 ◽  
pp. 1680 ◽  
Author(s):  
Luis Gustavo Vilá Mollinedo ◽  
Andrés Jaime Uribe ◽  
José Luis Aceves Chimal ◽  
Roberto Pablo Martínez-Rubio ◽  
Karen Patricia Hernández-Romero

Anomalous left coronary artery from the pulmonary artery, or ALCAPA syndrome, is a rare congenital cardiac disease that can cause myocardial infarction, heart failure and even death in paediatric patients. Only few untreated patients survive until adult age. Here we present the case of a 33-year-old female patient with paroxysmal tachycardia, syncope and little effort dyspnoea. She was diagnosed with ALCAPA syndrome and underwent surgical correction with an alternative technique of left main coronary artery extension to the aorta.


Author(s):  
Anil Baroopal ◽  
Rohit Mathur ◽  
Sanjeev Sanghvi ◽  
Swati Mahajan

Anomalous left coronary artery from the pulmonary artery (ALCAPA) is a rare congenital cardiac anomaly that can cause myocardial infarction, heart failure and even death in paediatric patients. Only few untreated patients survive till adulthood. Here we present the case of a 28-year-old lady with exertional dyspnoea and chest pain who was diagnosed to have ALCAPA.


2016 ◽  
Vol 8 (1) ◽  
pp. 101-102 ◽  
Author(s):  
Justin D. Weigand ◽  
Srinath Gowda ◽  
Richard Lorber ◽  
Nitin Madan

This case describes an infantile presentation of left main coronary artery atresia (LMCAA), which involves complete absence of the left coronary ostium and left main coronary artery. The echocardiographic features of LMCAA that assist in making this diagnosis are detailed. Important imaging features that distinguish LMCAA from anomalous left coronary artery from the pulmonary artery are highlighted.


2019 ◽  
Vol 2019 ◽  
pp. 1-3
Author(s):  
Sri Harsha Patlolla ◽  
Saraschandra Vallabhajosyula ◽  
Malcolm R. Bell

Anomalous coronary artery is an uncommon congenital cardiac anomaly that is often detected incidentally on coronary angiography. It has rarely been reported in the donor heart of patients who have undergone cardiac transplantation. Here, we report a case of a 72-year-old patient who received a second heart transplant and has been identified to have an anomalous left main coronary artery originating from the right coronary sinus on postoperative coronary angiography.


2013 ◽  
Vol 24 (3) ◽  
pp. 397-402 ◽  
Author(s):  
Justin Georgekutty ◽  
Russell R. Cross ◽  
Joanna B. Rosenthal ◽  
Deneen M. Heath ◽  
Pranava Sinha ◽  
...  

AbstractIn the United States, hypertrophic cardiomyopathy and coronary artery anomalies account for the leading two causes of sudden death in athletes. We present a case of a patient with an anomalous origin of the left main from the right coronary sinus with associated gene-confirmed hypertrophic cardiomyopathy. The patient underwent surgical repair with unroofing of the intramural portion of the left main coronary artery with a good result. We also review the reported cases in the medical literature describing this uncommon association between anomalous coronary artery origin and hypertrophic cardiomyopathy.


2019 ◽  
Vol 12 (7) ◽  
pp. e229815
Author(s):  
Santosh Kumar Sinha ◽  
Puneet Aggarwal ◽  
Mahmodula Razi ◽  
Vinay Krishna

Coronary artery anomalies are usually an incidental finding on coronary angiogram. Most of them are benign, although few of them are malignant which may cause sudden cardiac death. A 64-year-old diabetic, hypertensive man underwent coronary angiography for evaluation of exertional dyspnoea, and angina which revealed an anomalous left main coronary artery (LMCA) arising from right coronary sinus which was unduly long (79 mm) but free from any disease. To the best of our knowledge after extensive search in literature, this is the longest LMCA to be ever reported. The patient was managed conservatively.


2013 ◽  
Vol 24 (4) ◽  
pp. 732-734 ◽  
Author(s):  
Ram N. Bishnoi ◽  
Kristen N. McMillan ◽  
William R. Thompson

AbstractA left coronary artery arising from the right sinus of Valsalva is a rare congenital coronary anomaly. We report a case of a 5-year-old boy with an anomalous left coronary artery from the right sinus of Valsalva whose presenting sign was cardiac arrest. There is no reported instance of a child <9 years of age without other congenital cardiac defects having died suddenly with this coronary anomaly. The transthoracic echocardiogram demonstrated normal origins of the coronary arteries, but on autopsy, an anomalous origin of the left main coronary artery from the right sinus of Valsalva was found.


2018 ◽  
Vol 2018 ◽  
pp. 1-4
Author(s):  
Shantanu Patil ◽  
Mahek Shah ◽  
Brijesh Patel ◽  
Lohit Garg ◽  
Larry Jacobs ◽  
...  

Anomalous origin of the left main coronary artery from the pulmonary artery (ALCAPA) is a rare congenital coronary anomaly with high mortality. It is associated with cardiovascular complications and is usually diagnosed soon after birth. Those who survive into adulthood can present with signs of myocardial infarction, heart failure, mitral regurgitation, severe pulmonary hypertension, or sudden cardiac death. We present a 53-year-old female presenting with atrial fibrillation and found to have an incidental diagnosis of ALCAPA who refused surgical correction. We also review the epidemiology, diagnosis, age-based clinical presentations, and treatment options for ALCAPA.


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