scholarly journals Short-term succinic acid treatment mitigates cerebellar mitochondrial OXPHOS dysfunction, neurodegeneration and ataxia in a Purkinje-specific spinocerebellar ataxia type 1 (SCA1) mouse model

PLoS ONE ◽  
2017 ◽  
Vol 12 (12) ◽  
pp. e0188425 ◽  
Author(s):  
Austin Ferro ◽  
Emily Carbone ◽  
Jenny Zhang ◽  
Evan Marzouk ◽  
Monica Villegas ◽  
...  
Keyword(s):  
Mouse Model ◽  
Succinic Acid ◽  
Spinocerebellar Ataxia ◽  
Acid Treatment ◽  
Spinocerebellar Ataxia Type ◽  
Spinocerebellar Ataxia Type 1 ◽  
Short Term

scholarly journals Aminopyridines Correct Early Dysfunction and Delay Neurodegeneration in a Mouse Model of Spinocerebellar Ataxia Type 1

2011 ◽  
Vol 31 (33) ◽  
pp. 11795-11807 ◽  
Author(s):  
R. Hourez ◽  
L. Servais ◽  
D. Orduz ◽  
D. Gall ◽  
I. Millard ◽  
...  
Keyword(s):  
Mouse Model ◽  
Spinocerebellar Ataxia ◽  
Spinocerebellar Ataxia Type ◽  
Spinocerebellar Ataxia Type 1

scholarly journals Partial loss of Tip60 slows mid-stage neurodegeneration in a spinocerebellar ataxia type 1 (SCA1) mouse model

2011 ◽  
Vol 20 (11) ◽  
pp. 2204-2212 ◽  
Author(s):  
Kristin M. Gehrking ◽  
J. Michael Andresen ◽  
Lisa Duvick ◽  
John Lough ◽  
Huda Y. Zoghbi ◽  
...  
Keyword(s):  
Mouse Model ◽  
Spinocerebellar Ataxia ◽  
Spinocerebellar Ataxia Type ◽  
Spinocerebellar Ataxia Type 1 ◽  
Partial Loss

scholarly journals Non-invasive detection of neurochemical changes prior to overt pathology in a mouse model of spinocerebellar ataxia type 1

2013 ◽  
Vol 127 (5) ◽  
pp. 660-668 ◽  
Author(s):  
Uzay E. Emir ◽  
Howard Brent Clark ◽  
Manda L. Vollmers ◽  
Lynn E. Eberly ◽  
Gülin Öz
Keyword(s):  
Mouse Model ◽  
Spinocerebellar Ataxia ◽  
Spinocerebellar Ataxia Type ◽  
Spinocerebellar Ataxia Type 1 ◽  
Non Invasive ◽  
Neurochemical Changes
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