Recurrent Left Atrial Botyroid Rhabdomyosarcoma

2016 ◽  
Vol 19 (3) ◽  
pp. 097
Author(s):  
Günseli Abay ◽  
Cemal Kocaaslan ◽  
Rafet Günay ◽  
Meryem Doğan ◽  
Mahmut Murat Demirtaş
Keyword(s):  
Left Atrial ◽  
Malignant Tumors ◽  
Benign Tumors ◽  
Cardiac Tumors ◽  
Cardiac Symptoms ◽  
Systemic Embolization ◽  
Left Atrial Tumor ◽  
Heart Tumors ◽  
Atrial Tumor ◽  
Primary Cardiac Tumors

Primary heart tumors are extremely rare and their frequency ranges from approximately 0.01-0.3% in autopsy series. Nearly one quarter of all primary cardiac tumors are malignant tumors such as sarcoma. Rhabdomyosarcoma is the second most common malignant primary tumor of the heart following angiosarcoma.<br />Primary cardiac tumors present with one or more of the symptoms of the classic triad: cardiac symptoms and signs resulting from intracardiac obstruction; signs of systemic embolization; and systemic or constitutional symptoms. The prognosis after surgery is usually excellent in case of benign tumors, but is unfortunately still limited in localized malignant diseases [Butany 2005].<br />In this case report we present a 45-year-old female patient operated three times in 9 years because of left atrial tumor.

Surgical Treatment of Primary Cardiac Tumors—Experience with 45 Patients

1995 ◽  
Vol 3 (2) ◽  
pp. 49-52
Author(s):  
Lin Jue Yi ◽  
Chu Shu Hsun ◽  
Lee Yuan Teh ◽  
Wang Shoei Shen ◽  
Lin Fang Yue ◽  
...  
Keyword(s):  
Surgical Treatment ◽  
Left Atrium ◽  
Malignant Tumors ◽  
Thyroid Tissue ◽  
University Hospital ◽  
Benign Tumors ◽  
Cardiac Tumors ◽  
Incomplete Resection ◽  
Long Term Result ◽  
Primary Cardiac Tumors

Primary cardiac tumors are very rare and the majority of them are histologically benign and surgically curable. During a 30-year period from 1963 to January 1993, 45 cases of primary cardiac tumors were surgically excised at the National Taiwan University Hospital, representing 0.52% of 8,695 open heart surgical cases during the same period. In this series, 42 cases (94%) were benign tumors; 39 (88%) were myxoma (30 female, 9 male), and 32 (82%) originated in the left atrium. None were discovered in the left ventricle. In all but the first 6 cases, tumors in patients with myxoma in the left atrium were successfully excised by the transseptal approach. There were 3 patients with rare benign tumors: intracardiac goiter, rhabdomyoma, and hemangioma respectively. The intracardiac goiter was completely excised with no ectopic thyroid tissue after operation and the other 2 received palliative resection. The latter 2 patients suffered no recurrence. Rhabdomyosarcoma, leiomyosarcoma and malignant lymphoma were noted in one patient each, all of whom died of low cardiac output in the early postoperative course. In our experience, the majority of primary cardiac tumors were benign and located in the left atrium. The long-term result of surgical treatment of benign cardiac tumors is excellent, even incases of incomplete resection, while the results from surgical treatment of malignant tumors is poor.

scholarly journals Primary Cardiac Rhabdomyosarcoma in a child -- A case report

2020 ◽  
Author(s):  
KRISHNA PRASAD MARAM ◽  
Vikram Kudumula ◽  
Dilip Ratti
Keyword(s):  
Case Report ◽  
Left Ventricle ◽  
Right Ventricle ◽  
Malignant Tumor ◽  
Right Atrium ◽  
Malignant Tumors ◽  
Benign Tumors ◽  
Cardiac Tumors ◽  
Cardiac Rhabdomyosarcoma ◽  
Primary Cardiac Tumors

Primary cardiac tumors are rare in children, usually consist of benign tumors like rhabdomyomas and fibromas that may spontaneously regress. Primary malignant tumors are extremely rare even in adults and very few paediatric cases were reported in literature. Rhabdomyosarcoma is a rare primary malignant tumor in children and most of the reported cases occur in right ventricle, left atrium and right atrium. We report a 15 month old child with primary rhabdomyosarcoma of left ventricle presenting in cardiac tamponade and circulatory failure.

Surgical Treatment of Primary Cardiac Tumors

1997 ◽  
Vol 5 (2) ◽  
pp. 101-103 ◽  
Author(s):  
Gu Chun Jiu ◽  
Bao Wei Ke ◽  
Guo Bin Xun ◽  
Yuan Hong ◽  
Xiu Zhong Yi
Keyword(s):  
Surgical Treatment ◽  
Malignant Tumors ◽  
Right Atrial ◽  
Benign Tumors ◽  
Cardiac Tumors ◽  
Long Term Result ◽  
The Right ◽  
Medical University ◽  
Primary Cardiac Tumors

During a 16-year period from 1980 to 1996, 101 patients with primary cardiac tumors underwent surgery at the 1st Affiliated Hospital of China Medical University, which represented 2.44% of 4142 open-heart surgical cases during this period. Most tumors were benign; 94 were myxomas, 2 were fibromas, and 1 was a hemangioma. Three myxomas were in the right atrium and 91 were in the left atrium. The 4 malignant tumors comprised 2 mesothelioma, 1 histiocytoma, and 1 right atrial malignant myxoma. All benign tumors were completely excised with 4.95% mortality. Only 1 malignant tumor was completely excised. In our experience, the long-term result of surgical treatment of benign cardiac tumors is excellent, whereas the prognosis for patients with malignant cardiac tumors is very poor. The incidence of malignant tumors was lower than in other studies.

scholarly journals Case Report: 3D Printing Guided Cardiac Autotransplantation for Treatment of a Giant Complex Primary Left Atrial Tumor

2021 ◽  
Vol 8 ◽  
Author(s):  
Yang-zhao Zhou ◽  
Tao Tang ◽  
Cheng Luo ◽  
Xin-min Zhou ◽  
Xian-ming Fu
Keyword(s):  
3D Printing ◽  
Surgical Resection ◽  
Left Atrial ◽  
Cardiac Tumors ◽  
Posterior Aspect ◽  
3 Dimensional ◽  
Successful Case ◽  
Safe Technique ◽  
Left Atrial Tumor ◽  
Atrial Tumor

Primary cardiac tumors are rare and complete surgical resection is the optimal treatment. However, it is a great challenge to resect some malignant or complex benign left-sided cardiac tumors situated on the posterior aspect of the heart using conventional surgical resection techniques. Previous studies reported that cardiac autotransplantation is a feasible and safe technique for resection of such cardiac tumors. We report a successful case of cardiac autotransplantation with 3-dimensional (3D) printing technique for complete resection of a giant complex primary left atrial tumor.

Primary Cardiac Tumors: A Retrospective Study

2019 ◽  
Vol 15 (1) ◽  
pp. 57-61
Author(s):  
Mona Mlika ◽  
Nouha Daoud ◽  
Emna Braham ◽  
Adel Marghli ◽  
Faouzi El Mezni
Keyword(s):  
Surgical Resection ◽  
Microscopic Examination ◽  
Malignant Tumors ◽  
Ultra Sound ◽  
Benign Tumors ◽  
Cardiac Tumors ◽  
Postoperative Arrhythmia ◽  
Cardiac Lesions ◽  
The Right ◽  
Primary Cardiac Tumors

Objectives:Primary cardiac tumors are rare and account for 0.001 to 0.03% of cardiac lesions. The authors aim to describe the clinical, the microscopic and the therapeutic characteristics of these tumors through a 13-year-experience in order to highlight the diagnostic challenges faced.Methods:We report 10 primary cardiac tumors diagnosed in the Departments of Pathology and Thoracic Surgery of the same hospital through a 13-year-period.Results:Our study was conducted on 7 women and 3 men. The mean age of the patients was 54.22 years (average, 12 to 79 years). Dyspnea represented the most frequent symptom. Physical examination was normal in all patients. Trans-thoracic ultra-sound examination was performed in all patients. Cardiac MRI allowed localizing the tumors in 2 patients. They were located into the left auricle (6 cases), the right auricle (1 case) and the pericardium (3 cases). The microscopic examination was concluded to myxoma (7 cases), haemangioma (2 cases) and hemangioendothelioma (1 case). Surgical resection was possible in 9 patients. It was impossible in the case of hemangioendothelioma because of the adherence. One death was recorded secondary to postoperative arrhythmia. The other patients presented no complications after a follow-up period ranging from 2 months to 5 years.Conclusion:Cardiac tumors are challenging in their diagnosis and management. A positive diagnosis is based on microscopic examination. Surgical treatment plays a key role and is possible in the majority of benign tumors. The prognosis of malignant tumors remains poor even if a complete surgical resection is possible.

scholarly journals Primary Intimal Sarcoma of the Left Atrium: An Incidental Finding on Routine Echocardiography

Rare Tumors ◽  
2016 ◽  
Vol 8 (4) ◽  
pp. 109-112 ◽  
Author(s):  
Gautam Valecha ◽  
Dhaval Pau ◽  
Nikhil Nalluri ◽  
Ying Liu ◽  
Farhan Mohammad ◽  
...  
Keyword(s):  
Left Atrial ◽  
Malignant Tumors ◽  
Incidental Finding ◽  
Pathological Examination ◽  
Cardiac Tumors ◽  
Disease Entity ◽  
Resonance Imaging ◽  
Intimal Sarcoma ◽  
Left Atrial Myxoma ◽  
Primary Cardiac Tumors

Cardiac sarcomas are extremely rare primary malignant tumors of the heart. In this article, we present the case of a 70-year-old female, who was found to have a left atrial mass during a routine outpatient transthoracic echocardiography. Further investigation with cardiac magnetic resonance imaging confirmed the presence of a bilobulated mass with heterogeneous enhancement. Left atrial myxoma was the first diagnostic consideration, followed by other primary cardiac tumors, and thrombus. The patient subsequently underwent resection of the mass, utilizing cardiopulmonary bypass. Upon pathological examination, the mass was found to be an intimal sarcoma. The objective of this report is to describe a case of this rare disease entity, and to discuss its presentation, pathological findings and management.

scholarly journals A Giant Left Atrial Myxoma

2014 ◽  
Vol 2014 ◽  
pp. 1-3 ◽  
Author(s):  
Medhat F. Zaher ◽  
Sharad Bajaj ◽  
Mirette Habib ◽  
Emile Doss ◽  
Michael Habib ◽  
...  
Keyword(s):  
Blood Flow ◽  
Bronchial Asthma ◽  
Left Atrial ◽  
Atrial Myxoma ◽  
Cardiac Tumors ◽  
Mechanical Obstruction ◽  
Left Atrial Myxoma ◽  
Systemic Embolization ◽  
Primary Cardiac Tumors

Atrial myxomas are the most common primary cardiac tumors. Patients with left atrial myxomas generally present with mechanical obstruction of blood flow, systemic embolization, and constitutional symptoms. We present a case of an unusually large left atrial myxoma discovered incidentally in a patient with longstanding dyspnea being managed as bronchial asthma.

Comparison of Endoscopic Robotic versus Sternotomy Approach for the Resection of Left Atrial Tumors

2016 ◽  
Vol 11 (4) ◽  
pp. 274-277 ◽  
Author(s):  
Emmanuel Moss ◽  
Michael E. Halkos ◽  
Jeffrey S. Miller ◽  
Douglas A. Murphy
Keyword(s):  
Blood Transfusion ◽  
Left Atrial ◽  
Tumor Resection ◽  
Cardiac Tumors ◽  
Robotic Approach ◽  
Robotic Group ◽  
Robotic Assisted ◽  
Left Atrial Tumor ◽  
Atrial Tumor ◽  
Perioperative Blood Transfusion

Objective Primary cardiac tumors most commonly occur in the left atrium. The aim of this study was to compare outcomes among patients undergoing isolated left atrial tumor resection via sternotomy or robotic approach. Methods From 2003 to 2013, 69 patients underwent isolated left atrial tumor resection at 3 affiliated hospitals with either a sternotomy (n = 39) or robotic approach (n = 30). A retrospective review of prospectively collected data was performed, and outcomes were compared between the sternotomy and robotic groups. Univariate and multivariate analyses controlling for pertinent preoperative characteristics were performed. Results Patients’ characteristics in the 2 groups were similar, with the exception of a history of chronic obstructive pulmonary disease (sternotomy, 12.8% vs robotic, 0%; P < 0.04) and elective surgical status (sternotomy, 64.1% vs robotic, 93.3%; P < 0.02). On univariate analysis, robotic-assisted surgery was associated with significantly shorter postoperative mechanical ventilation, intensive care unit (ICU) length of stay (LOS), hospital LOS, and a lower rate of perioperative blood transfusion. After controlling for patient comorbidity in a multiple logistic regression model, there remained a trend toward decreased blood transfusions (adjusted odds ratio, 0.33; CI, 0.09–1.20; P = 0.09), shorter ICU (16.3 fewer hours; P = 0.11), and hospital LOS (1.1 fewer days; P = 0.17) in the robotic group. There was one postoperative stroke in the sternotomy group and none in the robotic group (P = 0.21). Conclusions Robotic-assisted left atrial tumor resection is feasible and may be associated with a lower incidence of perioperative blood transfusion as well as shorter ventilation time, and shorter ICU and hospital LOS.

scholarly journals Intimal Sarcoma: An Extremely Rare Case of a Left Atrial Tumor with Partial Obstruction of the Mitral Orifice

CASE ◽  
2021 ◽  
Author(s):  
Tamami Nakagawa-Kamiya ◽  
Mika Mori ◽  
Miho Ohira ◽  
Kenji Iino ◽  
Masa-aki Kawashiri ◽  
...  
Keyword(s):  
Left Atrial ◽  
Rare Case ◽  
Partial Obstruction ◽  
Intimal Sarcoma ◽  
Mitral Orifice ◽  
Left Atrial Tumor ◽  
Atrial Tumor

scholarly journals Left Atrial Myxoma Hypervascularized from the Right Coronary Artery: An Interesting Cath Lab Finding

2016 ◽  
Vol 2016 ◽  
pp. 1-3 ◽  
Author(s):  
Marcos Danillo Peixoto Oliveira ◽  
Adriano Ossuna Tamazato ◽  
Fernando Roberto de Fazzio ◽  
Luiz J. Kajita ◽  
Expedito E. Ribeiro ◽  
...  
Keyword(s):  
Coronary Artery ◽  
Right Coronary Artery ◽  
Left Atrial ◽  
Rare Case ◽  
Vascular Supply ◽  
Atrial Myxoma ◽  
Cardiac Tumors ◽  
Left Atrial Myxoma ◽  
The Right ◽  
Primary Cardiac Tumors

Primary cardiac tumors are rare and approximately half of them are atrial myxomas. They rarely remain asymptomatic, especially if large. The imaging of a myxoma by contrast dye during coronary angiography is an infrequent sign, which clarifies the vascular supply of the tumor. We report herein an interesting and rare case of a left atrial myxoma hypervascularized from the right coronary artery.

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