scholarly journals Cor Triatriatum Sinister in a 25 Year Old Patient - A Case Report

2020 ◽  
Vol 2020 ◽  
Author(s):  
Ketak Nagare

Cor triatriatum sinister is a rare congenital cardiac anomaly in which a fibromuscular membrane divides the left atria into 2 chambers. It is even rarer when present at an adult age. Symptoms and presentation of the patient depend on the size of the opening into the membrane through which 2 chambers of left atrium communicate with each other. Cor triatriatum sinister rarely remains asymptomatic till adulthood. In adults symptoms of Cor triatriatum sinister mimic the symptoms of mitral stenosis. Corrective surgery is the choice of treatment, but when it present as an emergency case especially at an early age, balloon dilatation of the membrane opening is done. Elective balloon dilatation of membrane opening at an early age diagnosed with Cor triatriatum sinister followed by corrective surgery at an adult age can be a safer option compared to direct corrective surgery at an early age.  We present a case of a 25-year-old female who was diagnosed first time at this age as cor triatriatum sinister and treated successfully with corrective surgery.

2020 ◽  
Vol 18 (1) ◽  
pp. 28-30
Author(s):  
Zanda Grīnberga ◽  
Pauls Sīlis ◽  
Elīna Ligere ◽  
Ingūna Lubaua ◽  
Inta Bergmane ◽  
...  

SummaryCor triatriatum sinister is a rare congenital cardiac anomaly that has been identified in 0.1% of children with congenital heart disease. It is defined as a fibromuscular membrane that divides the left atrium into two chambers: a superior (proximal) that in most cases receives drainage from the pulmonary veins and an inferior (distal) chamber that communicates with the mitral valve and the left atrium. Cor triatriatum sinister can be an isolated lesion (approximately 25% of cases), but in many cases it is associated with other congenital cardiovascular anomalies, the most common one being – atrial septal defect(3). Symptoms in patients with cor triatriatum sinister are related to obstruction of pulmonary venous drainage, pressure loading of the right side of the heart and congestive cardiac failure. Depending on the severity of the obstruction and presence of associated cardiac anomalies it can be diagnosed at any age. Diagnosis is usually achieved by echocardiography in early infancy. Elective treatment method is surgical excision of the membrane. Here we present a pediatric patient (4 months old) presenting in cardiogenic shock with a successful correction of isolated cor triatriatum sinister. To confirm diagnosis and success of surgical repair, transthoracic and transesophageal echocardiography were used.


Author(s):  
Changqing Gao ◽  
Ming Yang ◽  
Cangsong Xiao ◽  
Huajun Zhang ◽  
Gang Wang

Cor triatriatum sinister (CTS) is a rare congenital cardiac anomaly and is mainly corrected through conventional surgery through sternotomy. We described our successful novel surgical technique of totally robotic correction of CTS in one case of CTS with concomitant repair of atrial septal defect using da Vinci SI Surgical System (Intuitive Surgical, Inc, Sunnyvale, CA USA) with excellent surgical outcome. We conclude that robotic correction of CTS is a feasible and safe alternative to conventional surgical technique.


2020 ◽  
Vol 2020 ◽  
pp. 1-3
Author(s):  
Can Yilmaz Yozgat ◽  
Erkan Cakir ◽  
Hakan Yazan ◽  
Hafize Otcu Temur ◽  
Kahraman Yakut ◽  
...  

Cor triatriatum sinister is a rare congenital cardiac anomaly. The anomaly is caused by a fibromuscular membrane that divides the left atrium into two cavities. This membrane can lead to the obstruction of left atrial flow and also create pulmonary venous hypertension. Pulmonary arteriovenous malformation (PAVM) is notorious for its aberrant blood flow between the pulmonary arteries and veins. Herein, we report a case of a 4-year-old toddler who had a unique form of pulmonary hypertension presenting with cor triatriatum sinister and diffuse PAVM. After the surgical treatment of cor triatriatum sinister, both pulmonary arteriovenous malformation and pulmonary hypertension disappeared.


2020 ◽  
Vol 4 (3) ◽  
pp. 1-6
Author(s):  
Richard S Amara ◽  
Rakhee Lalla ◽  
Jean Jeudy ◽  
Susie Nam Hong

Abstract Background Cor triatriatum sinister (CTS) is a rare congenital cardiac anomaly defined by a fibromuscular membrane which bisects the left atrium. Cor triatriatum sinister has been associated with cardioembolic stroke through mechanisms including stagnation of blood flow within the left atrium, an association with atrial fibrillation (AF), and/or an accompanying atrial septal defect (ASD) or patent foramen ovale. We describe a case highlighting the role that CTS may play in cardioembolic stroke, provide high-quality computed tomography angiography and two- and three-dimensional echocardiography of the CTS membrane, and outline management strategies for this uncommon clinical scenario. Case summary A 35-year-old man with no prior medical history presented with acute onset weakness and aphasia. He was found to have an embolic stroke with left M1 and A1 occlusions and received tissue plasminogen activator followed by mechanical thrombectomy with successful recanalization. A thorough stroke workup revealed CTS with an associated ASD as well as potential protein C deficiency. He was managed with indefinite anticoagulation with apixaban. Discussion This is the 13th reported case of CTS associated with stroke. In most previous cases evidence of blood stasis or frank thrombus was associated with the CTS membrane, and/or existing AF was noted. In this case, none of these were identified, particularly highlighting the surreptitious risk of CTS. In addition, the presence of potential protein C deficiency in this case compounded the risk for thromboembolism and factored into multidisciplinary management decisions.


2013 ◽  
Vol 24 (3) ◽  
pp. 546-548 ◽  
Author(s):  
Claire Galoin-Bertail ◽  
Marielle Gouton

AbstractCor triatriatum sinister is an uncommon congenital cardiac anomaly accounting for 0.1% of all congenital cardiac malformations, with an anomalous venous return being a frequently associated condition. We present the case of a 14-year-old girl misdiagnosed as having an atrial septal defect with pulmonary hypertension who actually had a cor triatriatum with a left upper anomalous pulmonary venous return to the innominate vein.


Author(s):  
Mrinal Patel ◽  
Nikunj Vaidhya ◽  
Kartik Patel ◽  
Megha Sheth ◽  
Amit Mishra

Cor triatriatum dexter (CTD) is a rare congenital cardiac anomaly with a diverse presentation in every age group. We report a case of CTD in a 36-year-old female who presented with palpitations due to giant right atrium (RA), which we managed successfully with surgical excision of the membrane and RA reduction.


2013 ◽  
Vol 15 (3) ◽  
pp. 205-210 ◽  
Author(s):  
Joshua A. Stern ◽  
Sandra P. Tou ◽  
Piers C.A. Barker ◽  
Kevin D. Hill ◽  
Andrew J. Lodge ◽  
...  

2017 ◽  
Vol 21 (2) ◽  
pp. 178-185 ◽  
Author(s):  
Ajay Kumar Jha ◽  
Neeti Makhija

Cor triatriatum is a rare congenital cardiac anomaly defined by an abnormal septation within the atrium (left or right) leading to inflow obstruction to the respective ventricles. It exists either in isolated classical form or may be associated with simple to complex congenital cardiac anomalies. Several anatomical variants exist even in the classical form, and therefore, it may require multimodal diagnostic modalities to characterize and differentiate for better percutaneous interventional or surgical planning. It commonly presents in infancy but may remain undetected till death. Symptomatology typically mimics mitral and tricuspid stenosis in sinister and dexter varieties, respectively. However, features of systemic embolization, heart failure, atrial fibrillation, cyanosis, cardiac asthma, syncope, and sudden cardiac arrest have also been reported in the literature. Surgical correction under cardiopulmonary bypass is the preferred treatment. Nevertheless, balloon dilatation may be considered in anatomically compatible variants and in special circumstances, such as heart failure, pregnancy, or as a bridge to definitive treatment.


Author(s):  
Việt Tuấn Thái

SHORT REVIEW OF COR TRIATRIATUM IN CHILDREN AT HUE CENTRAL HOSPITAL Cor triatriatum is a rare congenital cardiac anomaly in which the left atrium is divided into two compartments by an abnormal fibromuscular septum with an opening, producing varying degrees of obstruction of pulmonary venous return. During 7 years from 2012 to 2019, we met 5 cases of children with Cor triatriatum. All of them addmited with dyspnea, a loud S2 and a nonspecific systolic murmur. The patients were correctly diagnosed by echocardiography and successfully operated. Keywords: Cor triatriatum, congenital cardiac anomaly


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