scholarly journals Isolated Cor Triatriatum Sinister: A Case Report

2020 ◽  
Vol 18 (1) ◽  
pp. 28-30
Author(s):  
Zanda Grīnberga ◽  
Pauls Sīlis ◽  
Elīna Ligere ◽  
Ingūna Lubaua ◽  
Inta Bergmane ◽  
...  
Keyword(s):  
Left Atrium ◽  
Pulmonary Veins ◽  
Surgical Excision ◽  
Venous Drainage ◽  
Treatment Method ◽  
Cor Triatriatum ◽  
Cardiac Anomaly ◽  
Congenital Cardiac Anomaly ◽  
Cor Triatriatum Sinister ◽  
The Right

SummaryCor triatriatum sinister is a rare congenital cardiac anomaly that has been identified in 0.1% of children with congenital heart disease. It is defined as a fibromuscular membrane that divides the left atrium into two chambers: a superior (proximal) that in most cases receives drainage from the pulmonary veins and an inferior (distal) chamber that communicates with the mitral valve and the left atrium. Cor triatriatum sinister can be an isolated lesion (approximately 25% of cases), but in many cases it is associated with other congenital cardiovascular anomalies, the most common one being – atrial septal defect(3). Symptoms in patients with cor triatriatum sinister are related to obstruction of pulmonary venous drainage, pressure loading of the right side of the heart and congestive cardiac failure. Depending on the severity of the obstruction and presence of associated cardiac anomalies it can be diagnosed at any age. Diagnosis is usually achieved by echocardiography in early infancy. Elective treatment method is surgical excision of the membrane. Here we present a pediatric patient (4 months old) presenting in cardiogenic shock with a successful correction of isolated cor triatriatum sinister. To confirm diagnosis and success of surgical repair, transthoracic and transesophageal echocardiography were used.

scholarly journals Cardioembolic stroke in a young male with cor triatriatum sinister: a case report

2020 ◽  
Vol 4 (3) ◽  
pp. 1-6
Author(s):  
Richard S Amara ◽  
Rakhee Lalla ◽  
Jean Jeudy ◽  
Susie Nam Hong
Keyword(s):  
Left Atrium ◽  
Protein C ◽  
Blood Stasis ◽  
Young Male ◽  
Cardioembolic Stroke ◽  
Cor Triatriatum ◽  
Cardiac Anomaly ◽  
Protein C Deficiency ◽  
Congenital Cardiac Anomaly ◽  
Cor Triatriatum Sinister

Abstract Background Cor triatriatum sinister (CTS) is a rare congenital cardiac anomaly defined by a fibromuscular membrane which bisects the left atrium. Cor triatriatum sinister has been associated with cardioembolic stroke through mechanisms including stagnation of blood flow within the left atrium, an association with atrial fibrillation (AF), and/or an accompanying atrial septal defect (ASD) or patent foramen ovale. We describe a case highlighting the role that CTS may play in cardioembolic stroke, provide high-quality computed tomography angiography and two- and three-dimensional echocardiography of the CTS membrane, and outline management strategies for this uncommon clinical scenario. Case summary A 35-year-old man with no prior medical history presented with acute onset weakness and aphasia. He was found to have an embolic stroke with left M1 and A1 occlusions and received tissue plasminogen activator followed by mechanical thrombectomy with successful recanalization. A thorough stroke workup revealed CTS with an associated ASD as well as potential protein C deficiency. He was managed with indefinite anticoagulation with apixaban. Discussion This is the 13th reported case of CTS associated with stroke. In most previous cases evidence of blood stasis or frank thrombus was associated with the CTS membrane, and/or existing AF was noted. In this case, none of these were identified, particularly highlighting the surreptitious risk of CTS. In addition, the presence of potential protein C deficiency in this case compounded the risk for thromboembolism and factored into multidisciplinary management decisions.

scholarly journals Multislice Computed Tomography Imaging of Total Anomalous Pulmonary Venous Circulation: Three Rare Case Reports

2018 ◽  
Vol 6 (1-2) ◽  
pp. 73-77
Author(s):  
Nusrat Ghafoor ◽  
Md Rokonujjaman Selim ◽  
Nawshin Siraj
Keyword(s):  
Computed Tomography ◽  
Ct Scan ◽  
Left Atrium ◽  
Case Reports ◽  
Pulmonary Veins ◽  
Cardiac Anomaly ◽  
Congenital Cardiac Anomaly ◽  
Venous Circulation ◽  
The Right ◽  
Anomalous Pulmonary Venous Connection

Total anomalous pulmonary venous connection is a rare congenital cardiac anomaly in which the pulmonary veins have no connection with the left atrium and connect directly to the right atrium or to one of the systemic veins. In the diagnosis of total anomalous pulmonary venous connection, the presence and severity of the venous obstruction is important. Computed Tomography (CT) imaging is known to be a useful method for the evaluation of total anomalous pulmonary venous connection. Here we report 3 cases of total anomalous pulmonary venous circulation (TAPVC) where 32 slice CT scan played an important role in pre-operative diagnosis and management. Age of the patients ranged from seven months to sixteen years. Symptoms of the patients’ varied from fatigue, shortness of breath, mild cyanosis and reduced growth for their age. Echocardiography done revealed dilated right cardiac chambers and atrial septal defect (ASD) with suspicion of TAPVC. CT scan was performed and it provided detailed information about intra-cardiac anatomy, pulmonary veins and their confluence, route, drainage and most importantly their distance and relation with the left atrium. It also provided information about coronary sinus and its drainage. This information is very important for surgical mapping and planning. Ibrahim Card Med J 2016; 6 (1&2): 73-77

scholarly journals Cor Triatriatum Sinister Identified after New Onset Atrial Fibrillation in an Elderly Man

2014 ◽  
Vol 2014 ◽  
pp. 1-5 ◽  
Author(s):  
Ignacio A. Zepeda ◽  
Peter Morcos ◽  
Luis R. Castellanos
Keyword(s):  
Atrial Fibrillation ◽  
Left Atrium ◽  
Treatment Options ◽  
Pulmonary Veins ◽  
Cor Triatriatum ◽  
Cardiac Anomaly ◽  
Venous Flow ◽  
Cor Triatriatum Sinister ◽  
Onset Atrial Fibrillation ◽  
New Onset

A 73-year-old man with new onset atrial fibrillation with rapid ventricular response underwent transthoracic echocardiography that revealed an echogenic linear structure along the left atrium, suggestive of cor triatriatum sinister (CTS). CTS was confirmed with transesophageal echocardiography which demonstrated a proximal accessory atrium receiving pulmonary venous flow separated from a distal true atrium by a fibromuscular membrane with a large fenestration allowing flow between the chambers. In CTS, the left atrium is divided into proximal and distal chambers by a fenestrated fibromuscular septum. This cardiac anomaly accounts for 0.1% of cases of congenital heart disease and rarely presents in adults. CTS is primarily diagnosed with echocardiography and is associated with left atrial enlargement and development of atrial fibrillation. Treatment options depend on size of the communication between proximal and distal chambers, the gradient across the membrane, and the position of pulmonary veins. In some instances, surgical resection of the membrane that divides the left atrium is warranted.

scholarly journals Cor Triatriatum Sinister in a 25 Year Old Patient - A Case Report

2020 ◽  
Vol 2020 ◽  
Author(s):  
Ketak Nagare
Keyword(s):  
Balloon Dilatation ◽  
Cor Triatriatum ◽  
Cardiac Anomaly ◽  
Early Age ◽  
Corrective Surgery ◽  
Emergency Case ◽  
Adult Age ◽  
Congenital Cardiac Anomaly ◽  
Choice Of Treatment ◽  
Cor Triatriatum Sinister

Cor triatriatum sinister is a rare congenital cardiac anomaly in which a fibromuscular membrane divides the left atria into 2 chambers. It is even rarer when present at an adult age. Symptoms and presentation of the patient depend on the size of the opening into the membrane through which 2 chambers of left atrium communicate with each other. Cor triatriatum sinister rarely remains asymptomatic till adulthood. In adults symptoms of Cor triatriatum sinister mimic the symptoms of mitral stenosis. Corrective surgery is the choice of treatment, but when it present as an emergency case especially at an early age, balloon dilatation of the membrane opening is done. Elective balloon dilatation of membrane opening at an early age diagnosed with Cor triatriatum sinister followed by corrective surgery at an adult age can be a safer option compared to direct corrective surgery at an early age.  We present a case of a 25-year-old female who was diagnosed first time at this age as cor triatriatum sinister and treated successfully with corrective surgery.

Cor Triatriatum in Association With a Unique Form of Partial Anomalous Pulmonary Venous Connection

2021 ◽  
pp. 215013512110469
Author(s):  
Lou Capecci ◽  
Richard D. Mainwaring ◽  
Inger Olson ◽  
Frank L. Hanley
Keyword(s):  
Superior Vena Cava ◽  
Superior Vena ◽  
Pulmonary Veins ◽  
Vena Cava ◽  
Venous Drainage ◽  
Cor Triatriatum ◽  
Unique Form ◽  
Elective Repair ◽  
The Right ◽  
Anomalous Pulmonary Venous Connection

Cor triatriatum may be associated with abnormalities of pulmonary venous anatomy. This case report describes a unique form of partial anomalous pulmonary venous connection. The patient presented at 5 weeks of age with symptoms of tachypnea and poor feeding. Echocardiography demonstrated cor triatriatum and partial anomalous pulmonary venous drainage of the right upper lung. The patient underwent urgent repair of cor triatriatum. It was elected to not address the partial anomalous pulmonary venous connection at that time. The patient returned at age 19 months for elective repair of the anomalous pulmonary venous connection. There was also a large vein connecting the right lower pulmonary veins to the superior vena cava. This was repaired by dividing the superior vena cava along a vertical axis to redirect the flow of the anomalous pulmonary veins through the connecting vein to the left atrium. This report describes the anatomy and surgical approach to a unique form of anomalous pulmonary venous connection.

Cor Triatriatum Dexter: A Rare Cause of Aneurysmal Right Atrium

2021 ◽  
pp. 215013512110366
Author(s):  
Mrinal Patel ◽  
Nikunj Vaidhya ◽  
Kartik Patel ◽  
Megha Sheth ◽  
Amit Mishra
Keyword(s):  
Right Atrium ◽  
Surgical Excision ◽  
Cor Triatriatum ◽  
Cardiac Anomaly ◽  
Age Group ◽  
Congenital Cardiac Anomaly ◽  
Cor Triatriatum Dexter

Cor triatriatum dexter (CTD) is a rare congenital cardiac anomaly with a diverse presentation in every age group. We report a case of CTD in a 36-year-old female who presented with palpitations due to giant right atrium (RA), which we managed successfully with surgical excision of the membrane and RA reduction.

Totally Endoscopic Robotic Correction of Cor Triatriatum Sinister Coexisting with Atrial Septal Defect

2016 ◽  
Vol 11 (6) ◽  
pp. 451-452 ◽  
Author(s):  
Changqing Gao ◽  
Ming Yang ◽  
Cangsong Xiao ◽  
Huajun Zhang ◽  
Gang Wang
Keyword(s):  
Surgical Technique ◽  
Atrial Septal Defect ◽  
Septal Defect ◽  
Cor Triatriatum ◽  
Cardiac Anomaly ◽  
Safe Alternative ◽  
Congenital Cardiac Anomaly ◽  
Cor Triatriatum Sinister ◽  
Da Vinci Si ◽  
Surgical System

Cor triatriatum sinister (CTS) is a rare congenital cardiac anomaly and is mainly corrected through conventional surgery through sternotomy. We described our successful novel surgical technique of totally robotic correction of CTS in one case of CTS with concomitant repair of atrial septal defect using da Vinci SI Surgical System (Intuitive Surgical, Inc, Sunnyvale, CA USA) with excellent surgical outcome. We conclude that robotic correction of CTS is a feasible and safe alternative to conventional surgical technique.

scholarly journals A Rare Cause of Pulmonary Hypertension in a 4-Year-Old Toddler: Association of Cor Triatriatum Sinister and Pulmonary Arteriovenous Malformation

2020 ◽  
Vol 2020 ◽  
pp. 1-3
Author(s):  
Can Yilmaz Yozgat ◽  
Erkan Cakir ◽  
Hakan Yazan ◽  
Hafize Otcu Temur ◽  
Kahraman Yakut ◽  
...  
Keyword(s):  
Pulmonary Hypertension ◽  
Arteriovenous Malformation ◽  
Pulmonary Arteries ◽  
Venous Hypertension ◽  
Pulmonary Arteriovenous Malformation ◽  
Cor Triatriatum ◽  
Cardiac Anomaly ◽  
Congenital Cardiac Anomaly ◽  
Cor Triatriatum Sinister ◽  
Arteries And Veins

Cor triatriatum sinister is a rare congenital cardiac anomaly. The anomaly is caused by a fibromuscular membrane that divides the left atrium into two cavities. This membrane can lead to the obstruction of left atrial flow and also create pulmonary venous hypertension. Pulmonary arteriovenous malformation (PAVM) is notorious for its aberrant blood flow between the pulmonary arteries and veins. Herein, we report a case of a 4-year-old toddler who had a unique form of pulmonary hypertension presenting with cor triatriatum sinister and diffuse PAVM. After the surgical treatment of cor triatriatum sinister, both pulmonary arteriovenous malformation and pulmonary hypertension disappeared.

Divided left atrium with obstruction of pulmonary venous return in the setting of hypoplasia of the left heart

2004 ◽  
Vol 14 (5) ◽  
pp. 553-556 ◽  
Author(s):  
Sara E. Monaco ◽  
Welton M. Gersony ◽  
Harshwardhan M. Thaker
Keyword(s):  
Left Atrium ◽  
Venous Return ◽  
Pulmonary Veins ◽  
Postmortem Examination ◽  
Cor Triatriatum ◽  
Pulmonary Venous Obstruction ◽  
Left Heart ◽  
Venous Obstruction ◽  
Cor Triatriatum Sinister

We describe an infant with hypoplasia of the left heart diagnosed prenatally who, at birth, had signs of severe pulmonary venous obstruction. Echocardiography indicated normally connecting pulmonary veins, and showed a paradoxical right-to-left shunt across a patent oval foramen. Postmortem examination revealed that the obstruction was due to a divided left atrium, or cor triatriatum sinister, with an imperforate muscular diaphragm separating completely the two components of the divided atrium.

scholarly journals Báo cáo các ca bệnh tim ba buồng nhĩ trái ở trẻ em tại Bệnh viện Trung ương Huế

2020 ◽  
Author(s):  
Việt Tuấn Thái
Keyword(s):  
Left Atrium ◽  
Venous Return ◽  
Short Review ◽  
Systolic Murmur ◽  
Cor Triatriatum ◽  
Cardiac Anomaly ◽  
Central Hospital ◽  
Congenital Cardiac Anomaly

SHORT REVIEW OF COR TRIATRIATUM IN CHILDREN AT HUE CENTRAL HOSPITAL Cor triatriatum is a rare congenital cardiac anomaly in which the left atrium is divided into two compartments by an abnormal fibromuscular septum with an opening, producing varying degrees of obstruction of pulmonary venous return. During 7 years from 2012 to 2019, we met 5 cases of children with Cor triatriatum. All of them addmited with dyspnea, a loud S2 and a nonspecific systolic murmur. The patients were correctly diagnosed by echocardiography and successfully operated. Keywords: Cor triatriatum, congenital cardiac anomaly

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