Cor Triatriatum Dexter: A Rare Cause of Aneurysmal Right Atrium

2021 ◽  
pp. 215013512110366
Author(s):  
Mrinal Patel ◽  
Nikunj Vaidhya ◽  
Kartik Patel ◽  
Megha Sheth ◽  
Amit Mishra
Keyword(s):  
Right Atrium ◽  
Surgical Excision ◽  
Cor Triatriatum ◽  
Cardiac Anomaly ◽  
Age Group ◽  
Congenital Cardiac Anomaly ◽  
Cor Triatriatum Dexter

Cor triatriatum dexter (CTD) is a rare congenital cardiac anomaly with a diverse presentation in every age group. We report a case of CTD in a 36-year-old female who presented with palpitations due to giant right atrium (RA), which we managed successfully with surgical excision of the membrane and RA reduction.

scholarly journals Isolated Cor Triatriatum Sinister: A Case Report

2020 ◽  
Vol 18 (1) ◽  
pp. 28-30
Author(s):  
Zanda Grīnberga ◽  
Pauls Sīlis ◽  
Elīna Ligere ◽  
Ingūna Lubaua ◽  
Inta Bergmane ◽  
...  
Keyword(s):  
Left Atrium ◽  
Pulmonary Veins ◽  
Surgical Excision ◽  
Venous Drainage ◽  
Treatment Method ◽  
Cor Triatriatum ◽  
Cardiac Anomaly ◽  
Congenital Cardiac Anomaly ◽  
Cor Triatriatum Sinister ◽  
The Right

SummaryCor triatriatum sinister is a rare congenital cardiac anomaly that has been identified in 0.1% of children with congenital heart disease. It is defined as a fibromuscular membrane that divides the left atrium into two chambers: a superior (proximal) that in most cases receives drainage from the pulmonary veins and an inferior (distal) chamber that communicates with the mitral valve and the left atrium. Cor triatriatum sinister can be an isolated lesion (approximately 25% of cases), but in many cases it is associated with other congenital cardiovascular anomalies, the most common one being – atrial septal defect(3). Symptoms in patients with cor triatriatum sinister are related to obstruction of pulmonary venous drainage, pressure loading of the right side of the heart and congestive cardiac failure. Depending on the severity of the obstruction and presence of associated cardiac anomalies it can be diagnosed at any age. Diagnosis is usually achieved by echocardiography in early infancy. Elective treatment method is surgical excision of the membrane. Here we present a pediatric patient (4 months old) presenting in cardiogenic shock with a successful correction of isolated cor triatriatum sinister. To confirm diagnosis and success of surgical repair, transthoracic and transesophageal echocardiography were used.

Divided right atrium (‘cor triatriatum dexter’) with azygous drainage of the superior caval vein

1996 ◽  
Vol 6 (1) ◽  
pp. 80-83
Author(s):  
Eberhard G. Mühler ◽  
Andreas Franke ◽  
Bruno J. Messmer
Keyword(s):  
High Pressure ◽  
Cerebrospinal Fluid ◽  
Transesophageal Echocardiography ◽  
Right Atrium ◽  
Surgical Excision ◽  
Cor Triatriatum ◽  
Caval Vein ◽  
Superior Caval Vein ◽  
Cor Triatriatum Dexter ◽  
The Right

SummaryWe describe the symptoms, the techniques for imaging and the surgical therapy in a patient with divided right atrium (‘cor triatriatum dexter’) combined with atresia of the superior caval vein. In addition to peripheral venous congestion and cyanosis, macrocephaly was the most prominent sign, the high pressure in the superior caval vein disturbing the circulation of cerebrospinal fluid. Transesophageal echocardiography was the optimal technique for imaging the dividing shelf in the right atrium. Cardiac catheterization after surgical excision of the shelf and reconstruction of the junction between the superior caval vein and the right atrium excluded any residual gradient or shunt.

scholarly journals Cor Triatriatum Sinistrum

2021 ◽  
Vol 21 (2) ◽  
pp. e324-326
Author(s):  
Al Rumitha Al Sabri ◽  
Niranjan Joshi ◽  
Hamood Al Kindi ◽  
Khalfan S Al Senaidi
Keyword(s):  
Heart Failure ◽  
Pulmonary Hypertension ◽  
Male Infant ◽  
Surgical Excision ◽  
University Hospital ◽  
Cor Triatriatum ◽  
Uneventful Recovery ◽  
Cardiac Anomaly ◽  
Sultan Qaboos University ◽  
Congenital Cardiac Anomaly

Cor triatriatum sinistrum (CTS) is a rare congenital cardiac anomaly characterised by an abnormal septum within the left atrium impairing blood flow to the left ventricle. We report the case of a two-month-old male infant who presented with symptoms of heart failure since the age of two weeks. He was admitted to a local hospital and was managed with antibiotics because of the impression of pneumonia. Due to persistent unresolved tachypnoea and tachycardia, he was referred to Sultan Qaboos University Hospital, Muscat, Oman, in 2019 for cardiac evaluation which confirmed a diagnosis of isolated CTS with severe stenosis and pulmonary hypertension. He underwent an urgent surgical excision of the membrane with uneventful recovery. Keywords: Cor Triatriatum Sinistrum; Congenital Heart Disease; Pulmonary Hypertension; Heart Failure; Case Report; Oman.

scholarly journals Cor Triatriatum Sinister in a 25 Year Old Patient - A Case Report

2020 ◽  
Vol 2020 ◽  
Author(s):  
Ketak Nagare
Keyword(s):  
Balloon Dilatation ◽  
Cor Triatriatum ◽  
Cardiac Anomaly ◽  
Early Age ◽  
Corrective Surgery ◽  
Emergency Case ◽  
Adult Age ◽  
Congenital Cardiac Anomaly ◽  
Choice Of Treatment ◽  
Cor Triatriatum Sinister

Cor triatriatum sinister is a rare congenital cardiac anomaly in which a fibromuscular membrane divides the left atria into 2 chambers. It is even rarer when present at an adult age. Symptoms and presentation of the patient depend on the size of the opening into the membrane through which 2 chambers of left atrium communicate with each other. Cor triatriatum sinister rarely remains asymptomatic till adulthood. In adults symptoms of Cor triatriatum sinister mimic the symptoms of mitral stenosis. Corrective surgery is the choice of treatment, but when it present as an emergency case especially at an early age, balloon dilatation of the membrane opening is done. Elective balloon dilatation of membrane opening at an early age diagnosed with Cor triatriatum sinister followed by corrective surgery at an adult age can be a safer option compared to direct corrective surgery at an early age.  We present a case of a 25-year-old female who was diagnosed first time at this age as cor triatriatum sinister and treated successfully with corrective surgery.

Cor triatriatum dexter masquerading as Ebstein's anomaly

2011 ◽  
Vol 21 (3) ◽  
pp. 354-356 ◽  
Author(s):  
Souheir Salam ◽  
David Gallacher ◽  
Orhan Uzun
Keyword(s):  
Tricuspid Valve ◽  
Transthoracic Echocardiography ◽  
Right Atrium ◽  
Cor Triatriatum ◽  
Ebstein’S Anomaly ◽  
Ebstein's Anomaly ◽  
Cor Triatriatum Dexter ◽  
The Right

AbstractWe report the case of a child with cor triatriatum dexter masquerading as Ebstein's anomaly on transthoracic echocardiography. This was attributed to a floppy membrane arising from the right atrium, protruding into the tricuspid valve and pushing the leaflets downwards, giving an impression of Ebstein's anomaly. The importance of recognising this pitfall will prevent misdiagnosis of Ebstein's anomaly.

scholarly journals Unexpected Echocardiographic Findings: Accessory Mitral Valve Tissue in Adults

2020 ◽  
Author(s):  
Ying Rao ◽  
Wei Chen ◽  
Yu Wang ◽  
wenjuan Song
Keyword(s):  
Mitral Valve ◽  
Heart Diseases ◽  
Incidental Finding ◽  
Surgical Excision ◽  
Ventricular Outflow Tract ◽  
Left Ventricular ◽  
Cardiac Anomaly ◽  
Congenital Cardiac Anomaly ◽  
Valve Tissue ◽  
Accessory Mitral Valve Tissue

Abstract Background: Accessory mitral valve tissue (AMVT) is a rare congenital cardiac anomaly, which is associated with other congenital heart diseases. It is diagnosed in neonates or childhood and rarely in adulthood. Nevertheless, AMVT is an incidental finding or described as isolated. Echocardiography, especially three-dimensional(3D) echocardiography is considered as an optimal imaging technique for AMVT diagnosis.Case presentation: We herein presented the two asymptomatic adult cases with AMVT, who presented with varying degrees of symptomatic left ventricular outflow tract (LVOT) obstruction. One presented with mild LVOT obstruction and no surgery was required, and another one with significant LVOT obstruction was recommended for surgical excision.Conclusions: We emphasized the usefulness of echocardiography in the morphology detection of AMVT, and the importance of operation guidance and follow-up.

scholarly journals P1464 A case of cortriatriatum dexter accidentally discovered in an adult

2020 ◽  
Vol 21 (Supplement_1) ◽  
Author(s):  
H S A Abdelgawad ◽  
M Abdelnabi ◽  
A Almaghrabi ◽  
M Shehata ◽  
M A Abdelhay
Keyword(s):  
Transesophageal Echocardiography ◽  
Right Atrium ◽  
Vena Cava ◽  
Interatrial Septum ◽  
Right Atrial ◽  
Cor Triatriatum ◽  
Free Wall ◽  
3D Transesophageal Echocardiography ◽  
Cor Triatriatum Dexter ◽  
The Right

Abstract Introduction Cor triatriatum dexter, or partitioning of the right atrium (RA) to form a triatrial heart, is an extremely rare congenital anomaly that is caused by the persistence of the right valve of the sinus venosus. The incidence of cor triatriatum is approximately 0.1% of congenital heart malformation. Typically, the right atrial partition is due to exaggerated fetal eustachian and the besian valves, which together form an incomplete septum across the lower part of the atrium. This septum may range from a reticulum to a substantial sheet of tissue Case report: 45-years old female patient with history of surgical closure of an atrial septal defect at the age of 14 years .She presented to our medical facility complaining of exertional dyspnea and bilateral lower limb edema for 4 years. On clinical examination, she had bilateral congested neck veins, a pansystolic murmur over the tricuspid area and a tender hepatomegaly. 2D Transthoracic Echocardiography revealed an unusual membranous structure that stretched across the right atrium with attachments superiorly at the free wall and inferiorly at the inter-atrial septum with a severe tricuspid regurgitation (Panel A)Intravenous agitated saline injection revealed an incomplete membrane. (Panel B).2D Transesophageal echocardiography showed an unusually prominent eustachian valve arose normally from the ostium of the inferior vena cava (IVC) and was pointing towards the interatrial septum just below the level of the fossa ovalis and no residual ASD could be seen. (Panel C) . 3D transesophageal echocardiography with zoomed mode from right atrial perspective confirmed the presence of an incomplete membrane extending transversely from the ostium of IVC and interatrial septum immediately below the fossa ovalis but not reaching RA free wall (arrow), no obstruction to the flow of the IVC, superior vena cava (SVC) , coronary sinus (CS) and the tricuspid valve (TV) was seen .(Panels D,E,F). Conclusion Since many patients are asymptomatic, the diagnosis of cor triatriatum dexter often is determined at postmortem examination. Antemortem diagnosis can be determined by echocardiography. 3D transesophageal echocardiography was able to detect cor triatriatum dexter that can be easily missed by 2D echocardiography. Abstract P1464 Figure.

Totally Endoscopic Robotic Correction of Cor Triatriatum Sinister Coexisting with Atrial Septal Defect

2016 ◽  
Vol 11 (6) ◽  
pp. 451-452 ◽  
Author(s):  
Changqing Gao ◽  
Ming Yang ◽  
Cangsong Xiao ◽  
Huajun Zhang ◽  
Gang Wang
Keyword(s):  
Surgical Technique ◽  
Atrial Septal Defect ◽  
Septal Defect ◽  
Cor Triatriatum ◽  
Cardiac Anomaly ◽  
Safe Alternative ◽  
Congenital Cardiac Anomaly ◽  
Cor Triatriatum Sinister ◽  
Da Vinci Si ◽  
Surgical System

Cor triatriatum sinister (CTS) is a rare congenital cardiac anomaly and is mainly corrected through conventional surgery through sternotomy. We described our successful novel surgical technique of totally robotic correction of CTS in one case of CTS with concomitant repair of atrial septal defect using da Vinci SI Surgical System (Intuitive Surgical, Inc, Sunnyvale, CA USA) with excellent surgical outcome. We conclude that robotic correction of CTS is a feasible and safe alternative to conventional surgical technique.

scholarly journals A Rare Cause of Pulmonary Hypertension in a 4-Year-Old Toddler: Association of Cor Triatriatum Sinister and Pulmonary Arteriovenous Malformation

2020 ◽  
Vol 2020 ◽  
pp. 1-3
Author(s):  
Can Yilmaz Yozgat ◽  
Erkan Cakir ◽  
Hakan Yazan ◽  
Hafize Otcu Temur ◽  
Kahraman Yakut ◽  
...  
Keyword(s):  
Pulmonary Hypertension ◽  
Arteriovenous Malformation ◽  
Pulmonary Arteries ◽  
Venous Hypertension ◽  
Pulmonary Arteriovenous Malformation ◽  
Cor Triatriatum ◽  
Cardiac Anomaly ◽  
Congenital Cardiac Anomaly ◽  
Cor Triatriatum Sinister ◽  
Arteries And Veins

Cor triatriatum sinister is a rare congenital cardiac anomaly. The anomaly is caused by a fibromuscular membrane that divides the left atrium into two cavities. This membrane can lead to the obstruction of left atrial flow and also create pulmonary venous hypertension. Pulmonary arteriovenous malformation (PAVM) is notorious for its aberrant blood flow between the pulmonary arteries and veins. Herein, we report a case of a 4-year-old toddler who had a unique form of pulmonary hypertension presenting with cor triatriatum sinister and diffuse PAVM. After the surgical treatment of cor triatriatum sinister, both pulmonary arteriovenous malformation and pulmonary hypertension disappeared.

Sign in / Sign up

Export Citation Format

Share Document