scholarly journals Resolution of syringomyelia in ten cases of "up-and-down Chiari malformation" after posterior fossa decompression

2010 ◽  
Vol 68 (5) ◽  
pp. 694-699 ◽  
Author(s):  
José Alberto Gonçalves da Silva ◽  
Luiz Ricardo Santiago Melo ◽  
Antônio Fernandes de Araújo ◽  
Adailton Arcanjo dos Santos Jr

The authors describe ten cases of syringomyelia without hindbrain herniation depicted by preoperative magnetic resonance imaging (MRI) in supine position. However, the herniation was observed in all cases during the operation with the patient in sitting position. The postoperative MRI revealed an intense reduction of the syrinx in all patients, as well as it was also observed a clinical amelioration in all cases. The surgical treatment was based on a large craniectomy with the patient in sitting position, tonsillectomy, large opening of the fourth ventricle and duraplasty with creation of a large cisterna magna.

1998 ◽  
Vol 89 (2) ◽  
pp. 212-216 ◽  
Author(s):  
Bermans J. Iskandar ◽  
Gary L. Hedlund ◽  
Paul A. Grabb ◽  
W. Jerry Oakes

Object. To provide more information about this rare condition, the authors describe five cases of syringohydromyelia without hindbrain herniation. Preoperative magnetic resonance imaging with and without gadolinium—diethylenetriamine pentaacetic acid revealed no evidence of spinal cord tumor, arachnoiditis, or spinal dysraphism. Methods. Craniocervical decompression was performed in all patients, after which there was resolution of the symptoms in the four symptomatic patients, and all five showed marked reduction in the size of the syrinx. Conclusions. The authors hypothesize the rare occurrence of syringohydromyelia resulting from a Chiari-like pathophysiological condition but lacking a hindbrain hernia. Patients with this condition may benefit from craniocervical decompression.


2018 ◽  
Vol 15 (1) ◽  
pp. 23-26 ◽  
Author(s):  
Prakash Kafle ◽  
Sushil Krishna Shilpakar ◽  
Mohan Raj Sharma ◽  
Gopal Sedain ◽  
Amit K Pradhanang ◽  
...  

Joubert syndrome (JS) isa rare autosomal recessive neuro developmental disorder involving cerebellar vermis and brainstem, marked by agenesis of cerebellar vermis, ataxia, hypotonia, oculomotor apraxia, neonatal breathing problems and mental retardation. Magnetic Resonance Imaging (MRI) reveals the characteristic Molar tooth sign of midbrain and Batwing appearance of rostral fourth ventricle. Nepal Journal of Neuroscience 15:23-26, 2018


2000 ◽  
Vol 8 (3) ◽  
pp. 1-5 ◽  
Author(s):  
Bermans J. Iskandar ◽  
Gary L. Hedlund ◽  
Paul A. Grabb ◽  
W. Jerry Oakes

Object To provide more information about this rare condition, the authors describe five cases of syringohydromyelia without hindbrain herniation. Preoperative magnetic resonance imaging with and without gadolinium-diethylenetriamine pentaacetic acid revealed no evidence of spinal cord tumor, arachnoiditis, or spinal dysraphism. Methods Craniocervical decompression was performed in all patients, after which there was resolution of the symptoms in the four symptomatic patients, and all five showed marked reduction in the size of the syrinx. Conclusions The authors hypothesize the rare occurrence of syringohydromyelia resulting from a Chiari-like pathophysiological condition but lacking a hindbrain hernia. Patients with this condition may benefit from craniocervical decompression.


1995 ◽  
Vol 9 (2) ◽  
pp. 109-114
Author(s):  
Michael J. Sillers ◽  
Glenn E. Peters

Meningioma of the frontal sinus is a rare entity. Only nine cases of primary frontal sinus meningioma are reported in the literature. Two cases of frontal sinus meningioma, one primary and one secondary, are herein described. Each patient presented with headache and a frontal mass. Neither patient had fever or signs of meningeal irritation. Computerized tomography (CT) of the paranasal sinuses demonstrated frontal sinus opacification, posterior table bone erosion, and inferolateral displacement of the orbital contents in both patients. One patient underwent preoperative magnetic resonance imaging (MRI) that was officially interpreted as a frontal sinus mucocele and a small epidural abscess. Patients underwent unsuccessful endoscopic decompression for presumed mucoceles. Subsequent MRI in the second patient showed a large intracranial mass with extension into the frontal sinus. Treatment included frontal sinus obliteration and frontal craniotomy for removal of tumor, respectively. Meningioma was confirmed histologically in each patient. Although meningioma of the frontal sinus is rare, thorough evaluation, including MRI, should be considered for frontal sinus opacification in association with posterior table bone erosion.


Neurosurgery ◽  
1987 ◽  
Vol 20 (4) ◽  
pp. 599-605 ◽  
Author(s):  
Jack E. Wilberger ◽  
Joseph C. Maroon ◽  
Richard E. Prostko ◽  
Parviz Baghai ◽  
Irwin Beckman ◽  
...  

Abstract Treatment of syringomyelia remains a difficult and controversial problem. However, the recent advent of magnetic resonance imaging (MRI) and intraoperative ultrasound allows a more precise approach to the diagnosis and management of this disorder. Experience with 27 cases of syringomyelia has shown that MRI is superior to all other forms of diagnostic imaging for the exact anatomical delineation of syrinxes and other spinal cord cavities. One-third of the syrinxes demonstrated by MRI were either not adequately visualized or missed by myelography and/or computed tomographic scanning. Intraoperative ultrasound has been used to allow more precise operative approaches to the syrinx as well as to guide the exact placement of shunt tubes into syrinx cavities. A method has also been developed to allow intraoperative ultrasound of the spinal cord with patients in the sitting position.


Sign in / Sign up

Export Citation Format

Share Document