scholarly journals Ewing's sarcoma of the mandible in a young child

2010 ◽  
Vol 21 (1) ◽  
pp. 74-79 ◽  
Author(s):  
Marco Túllio Brazão-Silva ◽  
Alexandre Vieira Fernandes ◽  
Paulo Rogério de Faria ◽  
Sérgio Vitorino Cardoso ◽  
Adriano Mota Loyola
Keyword(s):  
Ewing’S Sarcoma ◽  
Ewing's Sarcoma ◽  
Neck Region ◽  
Radiographic Examination ◽  
Review Of The Literature ◽  
Head And Neck Region ◽  
Dental Abscess ◽  
Radiolucent Lesion ◽  
Malignant Lesions ◽  
Multiagent Chemotherapy

Ewing's sarcoma (ES) is a malignancy primarily affecting bone tissue that is commonly diagnosed in adolescents and young adults. Its occurrence in the head and neck region is unusual and generally involves the mandible and maxilla. An extensive review of the literature shows only few cases of the oral ES in patients under the age of 5. This paper reports a rare case of ES of the mandible in a 4-year-old girl, which had been previously misdiagnosed and treated as a dental abscess. In the clinical examination, a hard immobile expansive mass of 5 cm in diameter was observed on the left side of the mandible. Radiographic examination revealed a radiolucent lesion with ill-defined borders and wide vestibular bone plate destruction. Microscopically, the tumor was composed by monotonous small round cells that exhibited immunoreactivity for CD99, vimentin and pancytokeratin. The patient was subjected to multiagent chemotherapy with ifosfamide, carboplatin, etoposide, vincristine, cyclophosfamide and doxorrubycin (VAC/ICE regimen). However, after the first chemotherapeutic cycle, the patient died due to disseminated infection. This case elucidates the importance of professional knowledge of the relevant aspects of malignant lesions such as ES.

scholarly journals Ewing’s Sarcoma of the Mandible-A Rare Case Report

JMS SKIMS ◽  
2011 ◽  
Vol 14 (2) ◽  
pp. 68-70
Author(s):  
Shahid Hassan ◽  
BH Sripathi Rao ◽  
Gunachandra Rai
Keyword(s):  
Rare Case ◽  
Ewing’S Sarcoma ◽  
Ewing's Sarcoma ◽  
Radiographic Examination ◽  
Neural Tissues ◽  
Rare Case Report ◽  
Radiolucent Lesion ◽  
Children And Young Adults ◽  
Multiagent Chemotherapy ◽  
Ewing’S Tumor

Ewing’s sarcoma is a malignant tumor of bones that primarily affects children and young adults. The true origin of this small round cell lesion still remains controversial.It was originally described by James Ewing in 1921 as arising from undifferentiated osseous mesenchymal cells, however, recent studies suggests that Ewing’s tumor might be neuroectodermally derived from various degrees of differentiation of the primitive neural tissues. This paper reports a rare case of ES of the mandible in a 11-year-old girl, which had been previously misdiagnosed and treated as a dental abscess. In the clinical examination, a hard immobile expansive mass of 2cm diameter was observed on the left side of the mandible. Radiographic examination revealed a diffuse radiolucent lesion with ill-defined borders and wide vestibular bone plate destruction. Microscopically, the tumor was composed by monotonous small round cells that exhibited immunoreactivity for CD99, vimentin and desmin. Surgical resection of mandible followed by mandibular reconstruction was adopted. The patient was subjected to multiagent chemotherapy with Vincristine [VC],Dactinomycin [AC],Cyclophosphamide [CP] and Doxorubicin [AD]). JMS 2011;14(2):68-70

Primary nasal cavity Ewing’s sarcoma in pediatric practice: A clinical case

2021 ◽  
Vol 59 (1) ◽  
pp. 39-42
Author(s):  
А. Bekisheva ◽  
A. Makhneva ◽  
E. Satbaeva ◽  
G. Abyov ◽  
M. Remkulova
Keyword(s):  
Nasal Cavity ◽  
Clinical Case ◽  
Ewing’S Sarcoma ◽  
Ewing's Sarcoma ◽  
Histopathological Examination ◽  
Neck Region ◽  
Diagnostic Techniques ◽  
Tumor Type ◽  
Head And Neck Region ◽  
Tumor Remission

Ewing’s sarcoma is an aggressive tumor rarely found in the head and neck region and extremely rare in the nasal cavity or paranasal sinuses (2-3% of all Ewing’s sarcomas). Purpose: The article presents a clinical diagnostic case of nasal cavity Ewing’s sarcoma finally verified only by IHC test. Results: The presented clinical case describes Ewing’s sarcoma of the nasal cavity in a 14-year-old girl and presents the clinical picture, the results of MRI and CT examination of the sinuses, histopathological and IHC tests. Adequate diagnostical tools made it possible to establish a diagnosis. Timely determined treatment tactics, taking into account the tumor localization and possible postoperative complications, led to tumor remission. At present, the patient is under dynamic observation. Conclusion: The presented clinical case confirms that a primary nasal cavity Ewing’s sarcoma diagnostic largely depends on histopathological examination since visual diagnostic techniques do not provide reliable information on the tumor type.

Ewing's sarcoma of the retropharynx

1994 ◽  
Vol 108 (4) ◽  
pp. 363-366 ◽  
Author(s):  
Janet E. O'Connell ◽  
Caroline Calder ◽  
Faro Raafat ◽  
David Proops
Keyword(s):  
Differential Diagnosis ◽  
Young Child ◽  
Head And Neck ◽  
Ewing’S Sarcoma ◽  
Ewing's Sarcoma ◽  
Neck Region ◽  
Unusual Presentation ◽  
Pathological Features ◽  
Head And Neck Region

AbstractEwing's sarcoma arising in the head and neck region is very rare. A case arising from C2 in a young child is presented. The unusual presentation, differential diagnosis and pathological features are discussed.

Extraskeletal Ewing’s sarcoma of the larynx

2004 ◽  
Vol 118 (1) ◽  
pp. 62-64 ◽  
Author(s):  
Yoon Soo Yang ◽  
Ki Hwan Hong
Keyword(s):  
Head And Neck ◽  
Rare Disease ◽  
Surgical Resection ◽  
Ewing’S Sarcoma ◽  
Ewing's Sarcoma ◽  
Neck Region ◽  
Elderly Male ◽  
Head And Neck Region ◽  
Primitive Neuroectodermal Tumour ◽  
Extraskeletal Ewing’S Sarcoma

Primitive neuroectodermal tumour/extraskeletal Ewing’s sarcoma (PNET/EES) is a rare disease of the head and neck region. We report a case of a 74-year-old man with a laryngeal Ewing’s sarcoma. This is the first reported case of extraskeletal Ewing’s sarcoma of the larynx in an elderly male patient. The patient was successfully treated with surgical resection and post-operative radiotherapy.

scholarly journals Primary Ewing’s sarcoma of the temporal bone: a rare entity and review of the literature

2019 ◽  
Vol 12 (10) ◽  
pp. e230768
Author(s):  
Jeewan Ram Vishnoi ◽  
Vijay Kumar ◽  
Kirti Srivastava ◽  
Sanjeev Misra
Keyword(s):  
Temporal Bone ◽  
Ewing’S Sarcoma ◽  
Ewing's Sarcoma ◽  
Bone Tumour ◽  
Rare Entity ◽  
Review Of The Literature ◽  
Radiological Features ◽  
Primary Bone Tumour ◽  
Primary Bone ◽  
Multiagent Chemotherapy

Ewing’s sarcoma (ES) is the second most common malignant primary bone tumour in children and adolescents. It primarily affects the diaphysis of long bones and pelvis. ES arising from temporal bone is extremely rare. To date, 43 such cases have been described in the literature. Clinical and radiological features are non-specific. Diagnosis is based mainly on immunohistochemistry. The present article presents an extremely rare case of ES of the temporal bone in a 20-year young man, and he was successfully treated with multiagent chemotherapy and radiotherapy.

scholarly journals Multimodality Treatment in Ewing’s Sarcoma Family Tumors of the Maxilla and Maxillary Sinus: Review of the Literature

Sarcoma ◽  
2016 ◽  
Vol 2016 ◽  
pp. 1-15 ◽  
Author(s):  
David Thorn ◽  
Christoph Mamot ◽  
Fatime Krasniqi ◽  
Frank Metternich ◽  
Sven Prestin
Keyword(s):  
Soft Tissue ◽  
Maxillary Sinus ◽  
Ewing’S Sarcoma ◽  
Ewing's Sarcoma ◽  
Case Reports ◽  
Neck Region ◽  
Multimodality Treatment ◽  
Malignant Neoplasms ◽  
Review Of The Literature ◽  
Small Series

The Ewing sarcoma family of tumors (ESFT) encompasses a group of highly aggressive, morphologically similar, malignant neoplasms sharing a common spontaneous genetic translocation that affect mostly children and young adults. These predominantly characteristic, small round-cell tumors include Ewing’s sarcoma of the bone and soft tissue, as well as primitive neuroectodermal tumors (PNETs) involving the bone, soft tissue, and thoracopulmonary region (Askin’s tumor). Extraosseous ESFTs are extremely rare, especially in the head and neck region, where literature to date consists of sporadic case reports and very small series. We hereby present a review of the literature published on ESFTs reported in the maxilla and maxillary sinus region from 1968 to 2016.

scholarly journals Ewing's Sarcoma of Maxilla: A Rare Presentation

2015 ◽  
Vol 6 (2) ◽  
pp. 96-98
Author(s):  
Azeem Mohiyuddin ◽  
Ravindra P Deo ◽  
A Sagayaraj ◽  
Divya N jyothi ◽  
Harendra ML Kumar
Keyword(s):  
Ewing’S Sarcoma ◽  
Ewing's Sarcoma ◽  
Neck Region ◽  
Multimodality Treatment ◽  
First Line ◽  
Rare Presentation ◽  
Head And Neck Region ◽  
Jaw Bones ◽  
Rare Site ◽  
Head Neck

ABSTRACT Ewing's sarcoma is a rare malignant small cell tumor occurring in the first and second decades of life and usually involving the long bones of the limb. Literature shows that less than 3% of the tumor originates in the maxillofacial region of which 1% occurs in jaw bones with higher predilection for mandible. Mean age of presentation of this tumor in bones of head and neck region is 10.9 years. Surgery is the first line of treatment and considering the aggressive behavior of the tumor multimodality treatment is preferred to reduce recurrence rate. Due to small number of cases affecting the jaws, there are no definite protocols in treatment of Ewing's sarcoma of maxilla. We are presenting a case of Ewing's sarcoma of maxilla in a 60 years old patient, as it is involving a rare site and has occurred in an uncommon age group. How to cite this article Mohiyuddin SMA, Deo RP, Jyothi DN, Kumar HML, Sagayaraj A. Ewing's Sarcoma of Maxilla: A Rare Presentation. Int J Head Neck Surg 2015;6(2):96-98.

Extra-Skeletal Ewing's sarcoma of the nasal fossa

1990 ◽  
Vol 104 (7) ◽  
pp. 570-573 ◽  
Author(s):  
S. Lane ◽  
J. W. Ironside ◽  
M.R.C. Path
Keyword(s):  
Differential Diagnosis ◽  
Young Child ◽  
Head And Neck ◽  
Unusual Case ◽  
Ewing’S Sarcoma ◽  
Ewing's Sarcoma ◽  
Neck Region ◽  
Nasal Fossa ◽  
Head And Neck Region ◽  
Extraskeletal Ewing’S Sarcoma

AbstractExtraskeletal Ewing's sarcoma is rarely found arising in the head and neck region. An unusual case arising in the nasal fossa in a young child is reported and the differential diagnosis, pathology and treatment discussed.

scholarly journals Primary nasal cavity Ewing’s sarcoma in pediatric practice: A clinical case

2021 ◽  
Vol 59 (1) ◽  
pp. 39-42
Author(s):  
Aigul Bekisheva ◽  
Anna Makhneva ◽  
Galymzhan Abyov ◽  
Makhabbat Remkulova ◽  
Elvira Satbaeva
Keyword(s):  
Nasal Cavity ◽  
Clinical Case ◽  
Ewing’S Sarcoma ◽  
Ewing's Sarcoma ◽  
Histopathological Examination ◽  
Neck Region ◽  
Diagnostic Techniques ◽  
Tumor Type ◽  
Head And Neck Region ◽  
Tumor Remission

Relevance: Ewing’s sarcoma is an aggressive tumor rarely found in the head and neck region and extremely rare in the nasal cavity or paranasal sinuses (2-3% of all Ewing’s sarcomas). Purpose: To presents a clinical diagnostic case of nasal cavity Ewing’s sarcoma finally verified only by IHC test. Results: The presented clinical case describes Ewing’s sarcoma of the nasal cavity in a 14-year-old girl and presents the clinical picture, the results of MRI and CT examination of the sinuses, histopathological and IHC tests. Adequate diagnostical tools made it possible to establish a diagnosis. Timely determined treatment tactics, taking into account the tumor localization and possible postoperative complications, led to tumor remission. At present, the patient is under dynamic observation. Conclusion: The presented clinical case confirms that a primary nasal cavity Ewing’s sarcoma diagnostic largely depends on histopathological examination since visual diagnostic techniques do not provide reliable information on the tumor type.

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