scholarly journals Adult spindle cell/ sclerosing rhabdomyosarcoma of the buccal maxillary gingiva: Unique entity, a rare case report

2021 ◽  
Vol 6 (3) ◽  
pp. 217-221
Author(s):  
Shikha Chopra ◽  
Richa Jindal ◽  
Molly Joseph ◽  
Bhumika Gupta ◽  
Lipakshi Lakhiani ◽  
...  

Rhabdomyosarcoma is a malignant neoplasm of mesenchymal cells, which shows varying degrees of striated muscle cell differentiation. It predominantly occurs in children while rarely found in adults. Involvement of the oral cavity accounts for only 10-12% of all head and neck cases. Herewith, we report a rare case of oral spindle cell / sclerosing rhabdomyosarcoma in a 47-year-old male presented with a small mass involving the gingiva of right upper incisor. The mass was excised with a preoperative diagnosis of gingival epulis and subjected to histopathological and immunohistochemical examination which confirmed it to be spindle cell / sclerosing rhabdomyosarcoma. Data regarding its clinical course, genetic abnormalities and prognosis as a combined subtype is scant.

2020 ◽  
Vol 0 ◽  
pp. 1-3
Author(s):  
Sneha Jatan Bothra ◽  
Mansi Sharma ◽  
Parveen Jain ◽  
Divya Bansal ◽  
Ullas Batra

Rhabdomyosarcoma (RMS) is an unusual sarcoma in adults. There are four main types of RMS described in the literature, including embryonal, alveolar, pleomorphic, and spindle cell type. Epithelioid RMS is a relatively newer form of RMS described in the literature, with little information regarding the natural course and management. We present a rare case of a young woman with metastatic epithelioid RMS, with an atypical presentation with bilateral large breast lumps, large ovarian mass progressing rapidly to metastasize, involving multiple sites. It has an aggressive clinical course with poor response to therapy.


2020 ◽  
Vol VOLUME 8 (ISSUE 1) ◽  
pp. 47-51
Author(s):  
Vineet Narula

ABSTRACT Spindle Cell Lipoma (SCL) is an uncommon benign tumor of adipose tissue that is usually super􀃶cially located in the posterior neck, back and shoulder region. We report a rare case of SCL in a 39 years old male presenting as neck swelling with c/o stridor and dysphagia. The contrast enhanced computed tomographic scan of neck showed an external and internal part of the swelling traversing through the thyrohyoid membrane suggestive of Mixed Pyolaryngocele. The tumor was excised by a trans-cervical approach but the post operative histopathology was found to be spindle cell Lipoma. We report this case due to its atypical presentation and location. Keywords: Lipoma, Spindle cell, Pyolaryngocele


1995 ◽  
Vol 62 (1_suppl) ◽  
pp. 94-96 ◽  
Author(s):  
P. Tognoni ◽  
R. Banchero ◽  
U. Repetto ◽  
C. Caviglia ◽  
M. Cussotto ◽  
...  

— We present a rare case report of a non-Hodgkin primary prostatic lymphoma. In the article we focus on the increasing number of primary urologic lymphomas, the usual indolent clinical course of such a neoplasm and the combination of surgery and chemotherapy that we performed in this case.


2012 ◽  
Vol 02 (01) ◽  
pp. 45-47
Author(s):  
Shetty K. Padma ◽  
Harish S. Permi ◽  
C.N. Patil ◽  
Michelle Mathias

AbstractSarcomatoid carcinoma occurring in the small intestine is very rare. They can be monophasic or biphasic. We report a rare case of monophasic Sarcomatoid carcinoma of the small intestine in a 60 year old male patient. The tumor was an ulceronodular mass involving the ileum circumferentially. The tumor infiltrated the full thickness of the intestinal wall and the serosa of an adjacent loop of ileum. Microscopically, the tumor was composed of sheets of malignant spindle cells. The carcinomatous nature of the tumor was evident only after Immunohistochemistry. The diagnosis of sarcomatoid carcinoma should be considered in the differential diagnosis of malignant spindle cell tumor of small intestine and immunohistochemical stains are required for the correct diagnosis.


2020 ◽  
Vol 9 (10) ◽  
pp. e1519108461
Author(s):  
Rani Iani Costa Gonçalo ◽  
Cristiane Kalinne Santos Medeiros ◽  
Humberto Pereira Chaves Neto ◽  
Janaina Lessa de Moraes dos Santos ◽  
Adriano Rocha Germano ◽  
...  

Background: Osteosarcoma is a malignant neoplasm that occurs most often in long bones, with the head and neck region being rarely affected, accounting for less than 1% of all cancers in this region. Objective: To report a rare case of a large-extension osteosarcoma with emphasis on its clinical and diagnostic aspects. Case presentation: A 43-year-old woman presenting an intraoral exophytic lesion with involvement of other maxillofacial structures, such as nostril, zygoma and orbit. Despite the initial clinical diagnosis of actinomycosis, an incisional biopsy confirmed the histopathological diagnosis of osteosarcoma, showing a wide morphological variety. Conclusion: This case highlights the importance of clinical and histopathological findings for the correct diagnosis of osteosarcoma. Moreover, it shows that, although surgical resection is the primary treatment for this neoplasia, depending on the extent of the tumor and its proximity to vital anatomical structures, the most appropriate conduct is not always feasible.


2020 ◽  
Vol 7 (11) ◽  
pp. C164-168
Author(s):  
Anusha Ganapathi ◽  
Thanka J ◽  
Lawrence D'Cruze ◽  
Barathi G ◽  
Natarajan K ◽  
...  

Paratesticular rhabdomyosarcomas (RMS) are very rare malignant tumors arising from the mesenchymal tissues of tunica, epididymis or spermatic cord. They present as painless hard masses in inguinoscrotal region, and large tumors can be mistaken for testicular tumors. They can spread to retroperitoneal lymph nodes or hematogenously metastasize to lung, bones and bone marrow. Here, we report a case of Embryonal RMS with spindle cell component presenting with painless scrotal mass and lung metastasis at initial diagnosis.


2014 ◽  
Vol 7 (1) ◽  
pp. 28-30
Author(s):  
Varsha Varshney ◽  
Gaurav Gupta ◽  
Mohnish Grover ◽  
Vikas Devra

ABSTRACT Burkitt's lymphoma is a malignant neoplasm rarely found in paranasal sinuses and skull base. We report a rare case of Burkitt's lymphoma of anterior skull base associated with acute loss of vision. A 10 years old boy presented with history of headache, diminution of vision in right eye since 15 days. Biopsy showed diffuse NHL of Burkitt's type. After treatment with chemotherapy there was complete recovery in vision. How to cite this article Gupta G, Devra V, Grover M, Varshney V. Burkitt's Lymphoma of Anterior Skull Base associated with Acute Loss of Vision: A Rare Case Report. Clin Rhinol An Int J 2014;7(1):28-30.


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