Papillon-lefevere syndrome-Consanguity as a risk factor in siblings (Case series)
2021 ◽
Vol 7
(3)
◽
pp. 210-215
Keyword(s):
Papillon-Lefevere syndrome is a very rare autosomal recessive trait characterized by palmoplantar hyperkeratosis and severe generalized early-onset periodontitis leading to premature loss of primary and permanent dentitions. Various etiopathogenesis factors are associated with syndrome. The palmoplantar keratoderma typically has its onset between the ages of 1 and 4 years and severe periodontitis starts at age of 3-4 years. A dentist plays an important role in early diagnosing and preserving remaining teeth in oral cavity. This case series describes three cases of PLS in siblings with consanguineously married parents. All siblings in the family were affected which makes this a rare case.
Keyword(s):
2021 ◽
pp. 104063872110075
Keyword(s):
1975 ◽
Vol 141
(6)
◽
pp. 1464-1469
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2018 ◽
Vol 03
(04)
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2012 ◽
Vol 44
(09)
◽
pp. 704-707
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1989 ◽
Vol 79
(9)
◽
pp. 454-458
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1987 ◽
Vol 42
(1)
◽
pp. 96-99
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2010 ◽
Vol 30
(3)
◽
pp. 245-255
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