scholarly journals Single Coronary Artery, a Coronary Anatomy Anomaly

2020 ◽  
Vol 6 (2) ◽  
pp. 153-158
Author(s):  
Arzia Pramadi Rahman ◽  
Nahar Taufiq ◽  
Hariadi Hariawan
Keyword(s):  
Congenital Anomaly ◽  
Coronary Artery ◽  
Treatment Options ◽  
Clinical Manifestations ◽  
Coronary Artery Anomaly ◽  
Clinical Approach ◽  
Single Coronary Artery ◽  
Coronary Anatomy ◽  
Non Invasive ◽  
Whole Heart

Coronary artery anomaly and variation is a group of congenital abnormality of the coronary artery with a wide variety of clinical manifestations. The cases are rare and usually found incidentally, but they become interesting because they are the second most causes for sudden cardiac death (SCD) in young adults participating in competitive sports. The number of cases of coronary artery anomaly is starting to rise as the number of cases undergoing invasive and non-invasive diagnosis procedure. Single coronary artery is a very rare congenital anomaly where there is only one coronary ostium to supply the whole heart. This anomaly usually occurs with other congenital anomaly. The symptoms may be unspecific from asymptomatic until SCD. This case report discusses about a patient with single coronary artery, its clinical approach, and the treatment options.

Single Coronary Artery Anomaly: Case Report

2021 ◽  
Vol 05 (02) ◽  
Author(s):  
Firas Ajam ◽  
Ndausung Udongwo ◽  
Vandan Updahyaya ◽  
Bharath Sathya ◽  
Daniel Kiss
Keyword(s):  
Case Report ◽  
Coronary Artery ◽  
Coronary Artery Anomaly ◽  
Single Coronary Artery ◽  
Single Coronary Artery Anomaly

Hermansky–Pudlak Syndrome

2020 ◽  
Vol 41 (02) ◽  
pp. 238-246
Author(s):  
Wilfredo De Jesus Rojas ◽  
Lisa R. Young
Keyword(s):  
Protein Trafficking ◽  
Health Management ◽  
Treatment Options ◽  
Clinical Manifestations ◽  
Autosomal Recessive Disorder ◽  
Oculocutaneous Albinism ◽  
Clinical Approach ◽  
Recessive Mutations ◽  
Hermansky Pudlak Syndrome ◽  
Traction Bronchiectasis

AbstractHermansky–Pudlak syndrome (HPS) is a multisystemic autosomal recessive disorder characterized by oculocutaneous albinism, bleeding diathesis, and lethal pulmonary fibrosis (PF) in some HPS subtypes. During middle adulthood, ground-glass opacities, reticulation, and traction bronchiectasis develop with progression of PF. HPS is an orphan disease occurring in 1 in 500,000 to 1,000,000 individuals worldwide, though the prevalence is 1 in 1,800 in individuals with Puerto Rican heritage. Recessive mutations or disruptions in HPS genes alter the function of HPS proteins which are components of biogenesis of lysosome-related organelle complexes and are critical for intracellular protein trafficking. Diagnosis and management of HPS-related comorbidities represent a challenge to physicians, and a multidisciplinary clinical approach is necessary for early detection, health management, and surveillance of PF in patients with HPS types 1, 2, and 4. Treatment options for individuals with HPS-PF include pirfenidone and lung transplantation. In this article, we describe the epidemiology, genetics, clinical manifestations, and management of HPS.

scholarly journals Prevalence, Spectrum, and Outcomes of Single Coronary Artery Detected on Coronary Computed Tomography Angiography (CCTA)

2019 ◽  
Vol 2019 ◽  
pp. 1-7 ◽  
Author(s):  
Rashid Al Umairi ◽  
Maryam Al-khouri
Keyword(s):  
Computed Tomography ◽  
Congenital Anomaly ◽  
Coronary Artery ◽  
Computed Tomography Angiography ◽  
Coronary Computed Tomography Angiography ◽  
Single Coronary Artery ◽  
Female Ratio ◽  
Rare Congenital Anomaly ◽  
Coronary Computed Tomography ◽  
Different Types

Background. Single coronary artery (SCA) is a rare congenital anomaly in which there is an isolated coronary artery that arises from a single coronary ostium and provides coronary blood supply to the entire myocardium. SCA is classified into different types based on the origin, branching pattern, and course. Although the majority of patients with SCA are asymptomatic, some patients can present with life-threatening symptoms. Aim. To examine the prevalence, anatomical distribution, and outcome of the single coronary artery anomaly detected on coronary computed tomography angiography (CCTA) in a single center in Oman. Methods. Retrospectively, we reviewed 4,445 patients who underwent coronary computed tomography angiography between September 2012 and August 2018 at the National Heart Center, Muscat, Oman. We identified patients with a single coronary artery, and we evaluated the origin, course, and outcome of SCA. Results. We found 12 patients with single coronary artery among 4,445 patients with a mean age of 56.4 years (age range: 34 to 71 years; male : female ratio: 5 : 7). The most common class was RIII-C seen in 4 patients. Other SCA included RII-C, RII-A, and RII-S, two in each class. One patient had RI and one had LII-P. Two patients had coronary artery bypass graft. No major adverse cardiac events were reported over a mean follow-up of 25.3 months. Conclusion. Single coronary artery (SCA) is a rare congenital anomaly classified into different types. In our study, the prevalence of SCA was 0.27% that is higher than the figures from previous reports.

Single coronary artery : A rare congenital coronary artery anomaly

2016 ◽  
Vol 4 (2) ◽  
pp. 45
Author(s):  
J Narendra ◽  
BH Lokesh ◽  
Harish ◽  
Praveen
Keyword(s):  
Coronary Artery ◽  
Coronary Artery Anomaly ◽  
Single Coronary Artery

Single coronary artery anomaly and chest pain

2017 ◽  
Vol 18 (12) ◽  
pp. 983-984
Author(s):  
Giuseppe Gatti ◽  
Manuel Belgrano ◽  
Maria Assunta Cova ◽  
Gianfranco Sinagra
Keyword(s):  
Chest Pain ◽  
Coronary Artery ◽  
Coronary Artery Anomaly ◽  
Single Coronary Artery ◽  
Single Coronary Artery Anomaly

scholarly journals Transcatheter Coil Embolization of a Coronary Artery-Left Ventricular Fistula Associated with Single Coronary Artery Anomaly

2014 ◽  
Vol 2014 ◽  
pp. 1-2
Author(s):  
Ozlem Ozcan Celebi ◽  
Alper Canbay ◽  
Erdem Diker ◽  
Barbaros Çil ◽  
Kudret Aytemir ◽  
...  
Keyword(s):  
Coronary Artery ◽  
Coil Embolization ◽  
Left Ventricular ◽  
Coronary Artery Anomaly ◽  
Single Coronary Artery ◽  
Rare Entity ◽  
Coronary Fistula ◽  
Coronary Artery Fistulas ◽  
Transcatheter Coil Embolization ◽  
Single Coronary Artery Anomaly

Single coronary artery anomaly associated with coronary fistula is a rare entity. Transcatheter coil embolization is the treatment of choice for coronary artery fistulas. In this case report, we describe a patient with both single coronary artery anomaly and coronary fistula who was successfully treated with coil embolization.

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