scholarly journals Primitive neuroectodermal tumor of ulnar nerve: A rare case

2021 ◽  
Author(s):  
Mohammadreza Emamhadi ◽  
Sama Noroozi Guilandehi ◽  
Nooshin Zaresharifi ◽  
Iraj Baghi ◽  
Alireza Mehrvarz ◽  
...  
Keyword(s):  
Young Adults ◽  
Ulnar Nerve ◽  
Peripheral Nerves ◽  
Rare Case ◽  
Primitive Neuroectodermal Tumor ◽  
Neuroectodermal Tumor ◽  
Children And Young Adults ◽  
Aggressive Tumor

Primitive neuroectodermal tumor (PNET) is a highly aggressive tumor and mostly develops in children and young adults. PNETs of peripheral nerves are uncommon. Ulnar nerve, in particular, is an extremely peculiar origin for PNET and to the best of our knowledge only few well-documented cases have been yet reported.

Primitive Neuroectodermal Tumor of the Stomach

2005 ◽  
Vol 129 (1) ◽  
pp. 107-110 ◽  
Author(s):  
Raoulin Soulard ◽  
Valère Claude ◽  
Philippe Camparo ◽  
Jean-Philippe Dufau ◽  
Patrick Saint-Blancard ◽  
...  
Keyword(s):  
Polymerase Chain Reaction ◽  
Young Adults ◽  
Soft Tissue ◽  
Ewing Sarcoma ◽  
Primitive Neuroectodermal Tumor ◽  
Neuron Specific Enolase ◽  
Neuroectodermal Tumor ◽  
Chain Reaction ◽  
Children And Young Adults ◽  
Polymerase Chain

Abstract Ewing sarcoma/primitive neuroectodermal tumor is classically a tumor of the soft tissue or bone in children and young adults, but several cases have been described in patients of all ages. Within the last decade, the clinicopathologic spectrum of Ewing sarcoma/primitive neuroectodermal tumor has been markedly expanded by recognition that the tumor may also have a visceral origin. We describe a case of primitive neuroectodermal tumor arising in the stomach of a 66-year-old woman. The neoplasm was excised using a radical surgical procedure. Microscopically, the tumor was made up of solid nests and sheets of round cells. Immunohistochemically, the tumor cells showed immunoreactivity for CD99, S100, neuron-specific enolase, and vimentin. A multiplex real-time polymerase chain reaction assay detected an EWS-ERG fusion. To our knowledge, this is the first description of a primitive neuroectodermal tumor arising in the stomach.

#47 Primitive neuroectodermal tumor of the chest wall in children and young adults

1999 ◽  
Vol 21 (4) ◽  
pp. 309
Author(s):  
K. Klopfenstein ◽  
K. Mutabagani ◽  
S. Teich ◽  
J. Groner ◽  
A. Rauck ◽  
...  
Keyword(s):  
Young Adults ◽  
Chest Wall ◽  
Primitive Neuroectodermal Tumor ◽  
Neuroectodermal Tumor ◽  
Children And Young Adults

scholarly journals Renal Peripheral Neuroectodermal Tumor Presenting at Age 78: Case Report

2008 ◽  
Vol 8 ◽  
pp. 830-834 ◽  
Author(s):  
Michelle E. Koski ◽  
Jason M. Tedesco ◽  
Peter E. Clark
Keyword(s):  
Young Adults ◽  
Case Report ◽  
Clinical Management ◽  
Primitive Neuroectodermal Tumor ◽  
Neuroectodermal Tumor ◽  
Advanced Age ◽  
Advanced Stages ◽  
Aggressive Tumor ◽  
Renal Pnet

Primitive neuroectodermal tumor (PNET) of the kidney is a rare and aggressive tumor, often presenting in advanced stages and progressing rapidly. Renal PNET (rPNET) may affect a wide age spectrum, but the majority of cases are in young adults. We present a case of advanced rPNET in a 78-year-old woman. To our knowledge, this is the most advanced age of presentation of this neoplasm to date. We report on her presentation and management, and discuss the current clinical management of this tumor.

scholarly journals Peripheral primitive neuroectodermal tumor of the small bowel mesentery: Report of a case

2015 ◽  
Vol 143 (9-10) ◽  
pp. 619-622
Author(s):  
Helena Maric ◽  
Radovan Cvijanovic ◽  
Igor Ivanov ◽  
Ljiljana Gvozdenovic ◽  
Dejan Ivanov ◽  
...  
Keyword(s):  
Young Adults ◽  
Small Intestine ◽  
Primitive Neuroectodermal Tumor ◽  
Soft Tissues ◽  
Clinical Presentation ◽  
Neuroectodermal Tumor ◽  
Small Bowel Mesentery ◽  
Peripheral Primitive Neuroectodermal Tumor ◽  
Neural Origin ◽  
Children And Young Adults

Introduction. Primitive neuroectodermal tumor or Ewing?s sarcoma is a tumor of undifferentiated small round cells that arise from the soft tissues, and is believed to be of neural origin. It occurs most often in children, followed by adolescents and young adults. Case Outline. A case of a 24-year-old patient with ulcerostenosans Ewing?s sarcoma of the initial part of the small intestine is presented in our paper. Reviewing the literature and using as an example the case of a female patient with signs of sideropenic anemia caused by primitive neuroectodermal tumor of the small intestine, an attempt was made to clarify the etiology, clinical presentation, diagnosis and therapy with the aim of its rapid detection and treatment. Conclusion. Mesenteric primitive neuroectodermal tumor is a rare neoplasm in adults, while it usually occurs in children and young adults. Surgical resection of the lesions with the application of chemotherapy is the main form of treatment of patients suffering from this disease.

scholarly journals Systemic congenital lymphangiomatosis

1996 ◽  
Vol 114 (5) ◽  
pp. 1278-1281 ◽  
Author(s):  
Ligia Maria Suppo de Souza ◽  
Maria Regina Bentlin ◽  
Eliana Souto de Abreu ◽  
Carlos Eduardo Bacchi
Keyword(s):  
Young Adults ◽  
Respiratory Failure ◽  
Rare Disease ◽  
Poor Prognosis ◽  
Rare Case ◽  
Soft Tissues ◽  
Lymphatic Channel ◽  
Autopsy Findings ◽  
Children And Young Adults ◽  
Cervical Area

Systemic lymphangiomatosis is a rare disease characterized by the exageration of lymphatic channel proliferation, occurring in children and young adults. We describe an extremely rare case of congenital systemic lymphangiomatosis in a newborn who had ascitis and respiratory failure develop immediately after delivery. Death occurred during the first hour of life. Autopsy findings showed numerous cysts in soft tissues of the cervical area, mediastinum and diaphragm, and several other organs including the liver, spleen, thyroid and kidneys. The severe and diffuse involvement with cysts in both lungs by lymphangiomatosis was associated with poor prognosis and death in our case.

scholarly journals A rare case of primitive neuroectodermal tumor of the right lung.

1996 ◽  
Vol 35 (5) ◽  
pp. 460-465 ◽  
Author(s):  
Mayumi UENO ◽  
Junzo FUJIYAMA ◽  
Tadashi IDEI ◽  
Kunishi KAWAMATA ◽  
Yukitoshi SATOH ◽  
...  
Keyword(s):  
Rare Case ◽  
Primitive Neuroectodermal Tumor ◽  
Neuroectodermal Tumor ◽  
The Right

scholarly journals Dysembryoplastic neuropithelial tumor: a rare case report

2017 ◽  
Vol 5 (5) ◽  
pp. 2270
Author(s):  
Shailesh Thanvi ◽  
Hemant Jangid ◽  
Yogi Raj Joshi
Keyword(s):  
Young Adults ◽  
Case Report ◽  
Rare Case ◽  
Male Child ◽  
Adjuvant Chemoradiotherapy ◽  
Rare Entity ◽  
Intractable Seizures ◽  
Rare Case Report ◽  
Children And Young Adults ◽  
Space Occupying Lesion

Dysembryoplastic neuropithelial tumor (DNET) is a rare recently described, benign glioneural tumor frequently associated with intractable seizures in children and young adults which is important to recognise clinically and radiologically as it is surgically curable without need for adjuvant chemoradiotherapy. We hereby present a case report of a 10year old male child who presented with intractable seizures and right parietal space occupying lesion which was diagnosed DNET radiologically, treated by microsurgical excision and confirmed histopathologically as DNET, thus emphasising multidisciplinary role in management of this rare entity.

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