#47 Primitive neuroectodermal tumor of the chest wall in children and young adults

1999 ◽  
Vol 21 (4) ◽  
pp. 309
Author(s):  
K. Klopfenstein ◽  
K. Mutabagani ◽  
S. Teich ◽  
J. Groner ◽  
A. Rauck ◽  
...  
Keyword(s):  
Young Adults ◽  
Chest Wall ◽  
Primitive Neuroectodermal Tumor ◽  
Neuroectodermal Tumor ◽  
Children And Young Adults

Primitive Neuroectodermal Tumor of the Stomach

2005 ◽  
Vol 129 (1) ◽  
pp. 107-110 ◽  
Author(s):  
Raoulin Soulard ◽  
Valère Claude ◽  
Philippe Camparo ◽  
Jean-Philippe Dufau ◽  
Patrick Saint-Blancard ◽  
...  
Keyword(s):  
Polymerase Chain Reaction ◽  
Young Adults ◽  
Soft Tissue ◽  
Ewing Sarcoma ◽  
Primitive Neuroectodermal Tumor ◽  
Neuron Specific Enolase ◽  
Neuroectodermal Tumor ◽  
Chain Reaction ◽  
Children And Young Adults ◽  
Polymerase Chain

Abstract Ewing sarcoma/primitive neuroectodermal tumor is classically a tumor of the soft tissue or bone in children and young adults, but several cases have been described in patients of all ages. Within the last decade, the clinicopathologic spectrum of Ewing sarcoma/primitive neuroectodermal tumor has been markedly expanded by recognition that the tumor may also have a visceral origin. We describe a case of primitive neuroectodermal tumor arising in the stomach of a 66-year-old woman. The neoplasm was excised using a radical surgical procedure. Microscopically, the tumor was made up of solid nests and sheets of round cells. Immunohistochemically, the tumor cells showed immunoreactivity for CD99, S100, neuron-specific enolase, and vimentin. A multiplex real-time polymerase chain reaction assay detected an EWS-ERG fusion. To our knowledge, this is the first description of a primitive neuroectodermal tumor arising in the stomach.

scholarly journals Primitive neuroectodermal tumor of ulnar nerve: A rare case

2021 ◽  
Author(s):  
Mohammadreza Emamhadi ◽  
Sama Noroozi Guilandehi ◽  
Nooshin Zaresharifi ◽  
Iraj Baghi ◽  
Alireza Mehrvarz ◽  
...  
Keyword(s):  
Young Adults ◽  
Ulnar Nerve ◽  
Peripheral Nerves ◽  
Rare Case ◽  
Primitive Neuroectodermal Tumor ◽  
Neuroectodermal Tumor ◽  
Children And Young Adults ◽  
Aggressive Tumor

Primitive neuroectodermal tumor (PNET) is a highly aggressive tumor and mostly develops in children and young adults. PNETs of peripheral nerves are uncommon. Ulnar nerve, in particular, is an extremely peculiar origin for PNET and to the best of our knowledge only few well-documented cases have been yet reported.

scholarly journals Peripheral primitive neuroectodermal tumor of the small bowel mesentery: Report of a case

2015 ◽  
Vol 143 (9-10) ◽  
pp. 619-622
Author(s):  
Helena Maric ◽  
Radovan Cvijanovic ◽  
Igor Ivanov ◽  
Ljiljana Gvozdenovic ◽  
Dejan Ivanov ◽  
...  
Keyword(s):  
Young Adults ◽  
Small Intestine ◽  
Primitive Neuroectodermal Tumor ◽  
Soft Tissues ◽  
Clinical Presentation ◽  
Neuroectodermal Tumor ◽  
Small Bowel Mesentery ◽  
Peripheral Primitive Neuroectodermal Tumor ◽  
Neural Origin ◽  
Children And Young Adults

Introduction. Primitive neuroectodermal tumor or Ewing?s sarcoma is a tumor of undifferentiated small round cells that arise from the soft tissues, and is believed to be of neural origin. It occurs most often in children, followed by adolescents and young adults. Case Outline. A case of a 24-year-old patient with ulcerostenosans Ewing?s sarcoma of the initial part of the small intestine is presented in our paper. Reviewing the literature and using as an example the case of a female patient with signs of sideropenic anemia caused by primitive neuroectodermal tumor of the small intestine, an attempt was made to clarify the etiology, clinical presentation, diagnosis and therapy with the aim of its rapid detection and treatment. Conclusion. Mesenteric primitive neuroectodermal tumor is a rare neoplasm in adults, while it usually occurs in children and young adults. Surgical resection of the lesions with the application of chemotherapy is the main form of treatment of patients suffering from this disease.

scholarly journals Ewing Sarcoma/Primitive Neuroectodermal Tumor of the Chest Wall

2003 ◽  
Vol 121 ◽  
pp. 256-261 ◽  
Author(s):  
Robert C. Shamberger ◽  
Michael P. LaQuaglia ◽  
Mark C. Gebhardt ◽  
James R. Neff ◽  
Nancy J. Tarbell ◽  
...  
Keyword(s):  
Chest Wall ◽  
Ewing Sarcoma ◽  
Primitive Neuroectodermal Tumor ◽  
Neuroectodermal Tumor

scholarly journals Renal Peripheral Neuroectodermal Tumor Presenting at Age 78: Case Report

2008 ◽  
Vol 8 ◽  
pp. 830-834 ◽  
Author(s):  
Michelle E. Koski ◽  
Jason M. Tedesco ◽  
Peter E. Clark
Keyword(s):  
Young Adults ◽  
Case Report ◽  
Clinical Management ◽  
Primitive Neuroectodermal Tumor ◽  
Neuroectodermal Tumor ◽  
Advanced Age ◽  
Advanced Stages ◽  
Aggressive Tumor ◽  
Renal Pnet

Primitive neuroectodermal tumor (PNET) of the kidney is a rare and aggressive tumor, often presenting in advanced stages and progressing rapidly. Renal PNET (rPNET) may affect a wide age spectrum, but the majority of cases are in young adults. We present a case of advanced rPNET in a 78-year-old woman. To our knowledge, this is the most advanced age of presentation of this neoplasm to date. We report on her presentation and management, and discuss the current clinical management of this tumor.

Paraplegia after chest wall resection for primitive neuroectodermal tumor

2009 ◽  
Vol 18 (2) ◽  
pp. 113-115 ◽  
Author(s):  
Jon Ryckman ◽  
Jean-Martin Laberge ◽  
Pramod S. Puligandla
Keyword(s):  
Chest Wall ◽  
Primitive Neuroectodermal Tumor ◽  
Neuroectodermal Tumor ◽  
Chest Wall Resection

scholarly journals Recurrent Askin`s Tumor: Ewing`s Sarcoma / Primitive Neuroectodermal Tumor of chest wall

2016 ◽  
Vol 9 (4) ◽  
Author(s):  
Muhammad Abdullah
Keyword(s):  
Soft Tissue ◽  
Local Recurrence ◽  
Soft Tissue Sarcoma ◽  
Disease Control ◽  
Chest Wall ◽  
High Frequency ◽  
Primitive Neuroectodermal Tumor ◽  
Neuroectodermal Tumor ◽  
Metastatic Spread ◽  
Local Disease Control

A care of recurrent Askin`s tumor is presented occurring in a 13 year old boy. Askin’s tumor is a rare primitive neuroectodermal tumor of chest wall and belong to Ewing family of soft tissue sarcoma. It is extremely malignant with a high frequency of both metastatic spread and local recurrence. Multi-drug chemotherapy as well as local disease control with surgery and / or radiation is indicated in the treatment of all patients

scholarly journals A CASE OF PRIMITIVE NEUROECTODERMAL TUMOR (PNET) OF THE CHEST WALL IN AN ADULT

CHEST Journal ◽  
2009 ◽  
Vol 136 (4) ◽  
pp. 32S
Author(s):  
Hari R. Reddy ◽  
Dennis G. Yick ◽  
Nader Kamangar
Keyword(s):  
Chest Wall ◽  
Primitive Neuroectodermal Tumor ◽  
Neuroectodermal Tumor

scholarly journals Peripheral Primitive Neuroectodermal Tumor of the Chest Wall of a 69-year-old Man

2004 ◽  
Vol 43 (7) ◽  
pp. 578-581 ◽  
Author(s):  
Yoko TAKAGI-TAKAHASHI ◽  
Noriharu SHIJUBO ◽  
Gen YAMADA ◽  
Eri SAITOH ◽  
Kaku SAWADA ◽  
...  
Keyword(s):  
Chest Wall ◽  
Primitive Neuroectodermal Tumor ◽  
Neuroectodermal Tumor ◽  
Peripheral Primitive Neuroectodermal Tumor

A case of peripheral primitive neuroectodermal tumor of the ovary

2004 ◽  
Vol 14 (2) ◽  
pp. 370-372 ◽  
Author(s):  
K.-J. Kim ◽  
B.-W. Jang ◽  
S.-K. Lee ◽  
B.-K. Kim ◽  
S.-L. Nam
Keyword(s):  
Primitive Neuroectodermal Tumor ◽  
Soft Tissues ◽  
Case Reports ◽  
The Body ◽  
Neuroectodermal Tumor ◽  
Pelvic Cavity ◽  
Age Group ◽  
Peripheral Primitive Neuroectodermal Tumor ◽  
Children And Young Adults ◽  
The Right

Peripheral primitive neuroectodermal tumor (PNET) belongs to the PNET/Ewing's sarcoma family. PNET is a small round cell tumor of putative neuroectoderm origin and is the second most common sarcoma among children and young adults. It may occur anywhere in the body and within any age group; however, it is most likely to occur in the bone and soft tissues. There have been a small number of case reports of PNET arising in the ovary. We presented a case of PNET arising in the right ovary of an 18-year-old woman. The tumor was metastased to the lymph nodes of the pelvis and para-aorta at surgical staging. We had persecuted Taxol/carboplatin chemotherapy, pelvic cavity radiotherapy, and Vincristine/Actinomycink, Cyclophosphamide/Doxorubicin (VACA). She died after 10 months due to septic shock.

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