Cystic Fibrosis in Childhood and Adolescence
Keyword(s):
Although cystic fibrosis (CF) has historically been considered a pulmonary disease, with the increasing life expectancy of these patients, gastrointestinal manifestations are becoming more important. Moreover, nutritional status is closely linked to pulmonary function and, thus, overall mortality. This review discusses gastrointestinal (including nutritional, pancreatic, and hepatobiliary) manifestations of CF and their management. It also discusses studies that have been critical to our understanding of these manifestations of CF. This review contains 1 figure, 1 table, and 36 references. Key words: body mass index, constipation, cystic fibrosis transmembrane regulator, distal intestinal obstruction syndrome, pancreatic insufficiency
2017 ◽
Keyword(s):
1995 ◽
Vol 269
(1)
◽
pp. C226-C233
◽
1994 ◽
Vol 269
(7)
◽
pp. 5336-5345
2005 ◽
Vol 16
(5)
◽
pp. 2154-2167
◽