Pediatric malignant perivascular epitheloid cell tumour with unusual immunophenotype

Author(s):  
Ita Hadzisejdic
Keyword(s):  
2013 ◽  
Vol 51 (09) ◽  
pp. 1096-1100 ◽  
Author(s):  
A. Jafari ◽  
H. Fischer ◽  
M. von Websky ◽  
G. Hong ◽  
J. Kalff ◽  
...  

2009 ◽  
Vol 3 (1) ◽  
Author(s):  
Alexandra M Koenig ◽  
Alexander Quaas ◽  
Thorsten Ries ◽  
Emre F Yekebas ◽  
Karim A Gawad ◽  
...  

2017 ◽  
Vol 2 (1) ◽  
pp. 39-42
Author(s):  
Amitabha Chakrabarti ◽  
Manujesh Bandyopadhyay ◽  
Biswarup Purkayastha

AbstractMalignant Perivascular Epitheloid Cell Tumour (PEComa) of the lung is very rare, with only six cases reported in literature. This case presented with a large mass originating from right upper lobe of the lung with dilemma in its histopathological diagnosis and management. Postoperative histopathology after a right upper and middle lobectomy describes a tumour with an alveolar/nested pattern of growth and epitheloid morphology with expression of TFE-3 and diagnosed as PEComa. After 6 months the patient had a local recurrence inside the thorax & chest wall.This case qualifies it as a rare type of malignant PEComa with younger age of presentation, aggressive clinical behaviour & malignant histological features along with TFE3 positivity on immunohistochemistry. This case is probably the first of its kind with the largest reported size involving two lobes of the lung.


1960 ◽  
Vol XXXV (IV) ◽  
pp. 513-517
Author(s):  
W. P. Plate

ABSTRACT The hormone-producing mesenchymomas of the ovaries can be divided into androblastomas and gynaecoblastomas. The former are derived from »male« elements, and consist of Sertoli-cell tumours and Leydig-cell tumours. The latter arise from »female« elements and consist of granulosacell tumours and theca-cell tumours. Sertoli-cell tumours and granulosacell tumours produce oestrogens, while Leydig-cell tumours and theca-cell tumours produce oestrogens or androgens. Histologically, androblastomas and gynaecoblastomas are often difficult to distinguish. Since no »female« elements occur in a testicle, a granulosa-cell tumour in a testicle is improbable. Gynandroblastomas, therefore, can only be found in an ovary.


2014 ◽  
Author(s):  
Dhanya Kalathil ◽  
Simon Roughneen ◽  
Momin Shah ◽  
Ali Akram ◽  
Reza Zaidi ◽  
...  

2019 ◽  
Author(s):  
Suhaniya Samarasinghe ◽  
Rebecca Scott ◽  
Michael J Seckl ◽  
Mike Gonzalez ◽  
Richard Harvey ◽  
...  

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