scholarly journals Co-Existence of a Rudimentary Non-Communicating Horn with a Unicornuate Uterus in Association with 2 Components of the VACTERL Association: A Case Report

2021 ◽  
pp. 1-4
Author(s):  
Jose D Roman ◽  
Jose D Roman
Keyword(s):  
High Risk ◽  
Anorectal Malformations ◽  
Uterine Horn ◽  
Vacterl Association ◽  
Renal Anomalies ◽  
Rudimentary Horn ◽  
Unicornuate Uterus ◽  
Rudimentary Uterine Horn ◽  
Uterine Anomalies ◽  
Vertebral Anomalies

The prevalence of congenital uterine anomalies has been reported as 6.7% in the general population. The unicornuate uterus accounts for 2.4-13% of all Mullerian anomalies and has a prevalence of 1:1000. A unicornuate uterus may be present alone or with a rudimentary horn and 75-90% of rudimentary horns are non-communicating. A pregnancy in the rudimentary horn may lead to uterine rupture, haemoperitoneum with a high risk of maternal mortality. The association of a unicornuate uterus with a non-communicating uterine horn to the VACTERL association of defects (vertebral anomalies, anorectal malformations, cardiovascular anomalies, tracheoesophageal fistula, esophageal atresia, renal anomalies and limb defects) has been described only twice in the literature. We report a patient who was born with an extra thumb and had a trachea-bronchial remnant with oesophageal stenosis that were both operated on earlier, and they were associated with a non-communicating rudimentary uterine horn. To the best of our knowledge, this is the third case reported in the literature of a VACTERL association to a unicornuate uterus with a non-communicating functional rudimentary horn. Given the high risk for the patient if pregnant an early diagnosis is paramount. This case highlights the importance of considering Mullerian defects in the young patient born with components of the VACTERL association.

Unicornuate Uterus with NonCommunicating Non-Cavitated Rudimentary Uterine Horn: An Unusual Case with Adenomyosis Managed with Total Hysterectomy

2015 ◽  
Vol 1 (1) ◽  
Keyword(s):  
Medical Treatment ◽  
Unusual Case ◽  
Uterine Bleeding ◽  
Uterine Horn ◽  
Rudimentary Horn ◽  
Total Hysterectomy ◽  
Unicornuate Uterus ◽  
Ultrasound Evaluation ◽  
Rudimentary Uterine Horn

A 45-year-old woman admitted to our hospital complaining of perimenopausal uterine bleeding not responding to medical treatment. Ultrasound evaluation revealed unicornuate uterus with adenomyosis and it was so difficult to see the distant small left rudimentary horn on ultrasound. The patient underwent laparotomy with total hysterectomy for both horns and was sent to pathologist that indicated adenomyosis and non-communicating non-cavitated left rudimentary horn.

scholarly journals Unicornuate uterus with functional non communicating rudimentary horn: a refractory cause of dysmenorrhea

2020 ◽  
Vol 9 (2) ◽  
pp. 874
Author(s):  
Manju Agarwal ◽  
Rakhee Soni ◽  
Madhureema Verma
Keyword(s):  
Uterine Cavity ◽  
Signs And Symptoms ◽  
Uterine Horn ◽  
Mullerian Duct ◽  
Rare Type ◽  
Müllerian Duct ◽  
Rudimentary Horn ◽  
Unicornuate Uterus ◽  
Rudimentary Uterine Horn ◽  
Müllerian Duct Anomaly

Mullerian duct anomalies are rare. Unicornuate uterus with a non-communicating rudimentary horn is a rare type of mullerian duct anomaly which occurs due to defective fusion of malformed duct with contralateral duct. The incidence is approximately 1:100000. Patient usually remain asymptomatic due to the absence of functional endometrium in most of the cases. If the rudimentary uterine horn has an endometrium lined uterine cavity and doesn’t communicate externally then the signs and symptoms of obstructed menstruation appears, as soon as menarche begins. It will be associated with severe dysmennorhoea and hematometra. Other complications may be abdominal lump, chronic pelvic pain, infertility, endometriosis, adenomyosis and ectopic pregnancy in rudimentary horn. Authors are presenting a case of refractory dysmenorrhea with lump abdomen in a patient with unicornuate uterus with functional non communicating horn. In a patient with refractory dysmenorrhea mullerian duct anomaly should be kept as differential diagnosis.

scholarly journals An Unexpected Near Term Pregnancy in a Rudimentary Uterine Horn

2013 ◽  
Vol 2013 ◽  
pp. 1-4 ◽  
Author(s):  
Elisabete Gonçalves ◽  
João Pedro Prata ◽  
Sandra Ferreira ◽  
Rita Abreu ◽  
Jorge Mesquita ◽  
...  
Keyword(s):  
Clinical Presentation ◽  
Uterine Cavity ◽  
Clinical Importance ◽  
Uterine Horn ◽  
Second Trimester ◽  
Review Of Literature ◽  
Rudimentary Horn ◽  
Unicornuate Uterus ◽  
Rudimentary Uterine Horn ◽  
Near Term

Unicornuate uterus occurs due to a complete or partial nondevelopment of one Mullerian duct; sometimes it is associated with a rudimentary horn, which can communicate or not with uterine cavity or contain functional endometrium. Pregnancy in a rudimentary horn is rare and the outcome almost always unfavorable, usually ending in rupture during the first or second trimester with significant morbidity and mortality. Despite the availability and advances on imagiologic procedures, recognition of this ectopic pregnancy is frequently made at laparotomy after abdominal pain and collapse. The authors describe a case of a primigravida with 34 weeks of gestation admitted with a preeclampsia with severity criteria. A cesarean for fetal malpresentation was done and, unexpectedly, a rudimentary horn pregnancy was found with a live newborn. In the literature, few reports of a horn pregnancy reaching the viability with a live newborn are described, enhancing the clinical importance of this case. A review of literature concerning the epidemics, clinical presentation, and appropriate management of uterine horn pregnancies is made.

scholarly journals Successful pregnancy and term delivery after treatment of unicornuate uterus with non-communicating rudimentary horn pregnancy with local methotrexate injection followed by laparoscopic resection: a case report and literature review

2021 ◽  
Vol 21 (1) ◽  
Author(s):  
Makiko Ueda ◽  
Kuniaki Ota ◽  
Toshifumi Takahashi ◽  
Satoshi Suzuki ◽  
Daisuke Suzuki ◽  
...  
Keyword(s):  
Blood Flow ◽  
Laparoscopic Surgery ◽  
Ectopic Pregnancy ◽  
Uterine Horn ◽  
Elective Cesarean Section ◽  
Rudimentary Horn ◽  
Unicornuate Uterus ◽  
Rudimentary Uterine Horn ◽  
Gestational Sac ◽  
The Right

Abstract Background Pregnancy in a rudimentary horn is an extremely rare type of ectopic pregnancy. A rudimentary uterine horn pregnancy is associated with a risk of spontaneous rupture and bleeding during surgery due to the increased uterine blood flow. Recent advances in imaging modalities have enabled laparoscopic surgery to be performed in cases without rupture in the early stages of pregnancy. However, there are few reports of successful pregnancies and deliveries after treatment of rudimentary horn pregnancies. We report the successful management of a case of non-communicating rudimentary horn pregnancy by local injection of methotrexate followed by complete laparoscopic excision along with a review of the literature. Case presentation The patient was a 29-year-old Japanese woman, gravida 2, nullipara. She was diagnosed with a left unicornuate uterus with a right non-communicating rudimentary horn on hysterosalpingography and magnetic resonance imaging. A gestational sac with a heartbeat was observed in the right rudimentary uterine horn at 6 weeks of gestation. A diagnosis of ectopic pregnancy in a non-communicating rudimentary horn was made. Color Doppler detected multiple blood flow signals around the gestational sac, which were clearly increased compared to the left unicornuate uterus. Her serum human chorionic gonadotropin level was 104,619 mIU/ml. A 100 mg methotrexate injection into the gestational sac was administered, and laparoscopic surgery was performed on day 48 after the methotrexate treatment. The right rudimentary horn and fallopian tube were successfully excised with minimal bleeding. A spontaneous normal pregnancy was established 6 months after the surgery. The pregnancy was uneventful, and a baby girl was born by elective cesarean section at 38w0d. Conclusion Combined local methotrexate injection and laparoscopic surgery are safe treatment options for patients with a unicornuate uterus with a non-communicating rudimentary horn pregnancy.

scholarly journals A Case of Rare Mullerian Anomaly—Functional Rudimentary Uterine Horn: As an Unusual Cause of Unilateral Dysmenorrhea in Postmenarchal Adolescent Girl

2012 ◽  
Vol 4 (1) ◽  
pp. 56-58
Author(s):  
Rekha Choudhary ◽  
Suniti Verma ◽  
Asha Meena ◽  
Sitaram Gothwal
Keyword(s):  
South Asian ◽  
Adolescent Girl ◽  
Chronic Pelvic Pain ◽  
Pelvic Mass ◽  
Exploratory Laparotomy ◽  
Uterine Horn ◽  
Rudimentary Horn ◽  
Unicornuate Uterus ◽  
Rudimentary Uterine Horn ◽  
Mullerian Anomaly

ABSTRACT An 18-year-old girl presented with progressively increasing dysmenorrhea. A pelvic mass was suspected which on exploratory laparotomy was found to be a rudimentary horn (hematometra, hematosalpinx). We report a case of unicornuate uterus with functioning rudimentary horn to highlight that mullerian duct anomalies should be considered in the differential diagnosis of severe dysmenorrhea even in normally menstruating girls. Unicornuate uterus with a rudimentary horn is susceptible to many gynecologic and obstetric complications. Hematometra, chronic pelvic pain, endometriosis, infertility are some of the complaints in women with unicornuate uterus. How to cite this article Choudhary R, Verma S, Meena A, Gothwal S. A Case of Rare Mullerian Anomaly—Functional Rudimentary Uterine Horn: As an Unusual Cause of Unilateral Dysmenorrhea in Postmenarchal Adolescent Girl. J South Asian Feder Obst Gynae 2012;4(1):56-58.

Uterine rupture of a non-communicating rudimentary horn pregnancy with resultant successful outcome of an extremely premature baby born at 24 weeks of gestation

2018 ◽  
Vol 7 (1) ◽  
Author(s):  
Satyaranjan Pegu ◽  
Bakul Deb ◽  
Tara Peters ◽  
Darrien Rattray
Keyword(s):  
High Risk ◽  
Uterine Rupture ◽  
Premature Baby ◽  
Uterine Horn ◽  
Successful Outcome ◽  
Mullerian Anomalies ◽  
Rudimentary Horn ◽  
Müllerian Anomalies ◽  
Unicornuate Uterus ◽  
Reproductive Aged Women

Abstract Mullerian anomalies occur in about 0.5% of reproductive-aged women; many remain asymptomatic only being discovered during surgery or on imaging done for unrelated reasons. These result from the abnormal formation, fusion or resorption of the mullerian duct during development. A unicornuate uterus with a rudimentary horn is one of the rarer subtypes, with such anomalies making up about 5% of all mullerian anomalies. Pregnancy in a non-communicating uterine horn (NCUH) is extremely rare, with an incidence between 1:100,000 and 1:140,000. There is a high risk of uterine rupture if pregnancy occurs in a non-communicating uterine horn. We present here a case of a non-communicating rudimentary horn pregnancy, with a successful outcome.

scholarly journals Non-communicating Rudimentary Uterine Horn Pregnancy

2011 ◽  
Vol 51 (184) ◽  
Author(s):  
I Upadhyaya
Keyword(s):  
High Risk ◽  
Acute Abdomen ◽  
Maternal Death ◽  
Uterine Cavity ◽  
Uterine Horn ◽  
Rare Form ◽  
Rudimentary Horn ◽  
Ectopic Gestation ◽  
Rudimentary Uterine Horn ◽  
Period Of Gestation

Pregnancy in a non-communicating rudimentary horn is an extremely rare form of ectopic gestation. The rudimentary horn may or may not communicate with the uterine cavity with the majority of cases being non-communicating. The patient exhibits features of acute abdomen and carries a high risk of maternal death. Even modern scans remain elusive whereas laparatomy remains the confi rmatory procedure for the diagnosis. Because of the varied muscular constitution in the thickness and distensibility of the wall of the rudimentary horn, pregnancy is accommodated for a variable period of gestation. Here, we report three cases of pregnancy in a non-communicating rudimentary horn of the uterus in different periods of gestation, their outcome and a review of the available literature. Keywords: Mullerian anomalies, non-communicating rudimentary horn pregnancy, surgical management.

scholarly journals A rare form of Mayer–Rokitansky–Küster–Hauser syndrome associated with ovarian endometrioma: a case report

2020 ◽  
Vol 2020 (9) ◽  
Author(s):  
Antoine Naem ◽  
Anwar Shamandi ◽  
Bashar AL-Kurdy
Keyword(s):  
Ovarian Cancer ◽  
Uterine Horn ◽  
Primary Amenorrhea ◽  
Rare Form ◽  
Live Births ◽  
Unicornuate Uterus ◽  
Ovarian Endometrioma ◽  
Rudimentary Uterine Horn ◽  
Ovarian Endometriomas ◽  
Exploratory Laparoscopy

Abstract Mayer–Rokitansky–Küster–Hauser syndrome is a congenital malformation that affects the uterus and upper two-thirds of the vagina. Its prevalence is estimated to be 1 in 4500 live births. We present the case of a 19-year-old patient that presented with primary amenorrhea and cyclic abdominal pain. Upon the exploratory laparoscopy, a right rudimentary uterine horn and left unicornuate uterus were found. These two entities were completely separated from each other and from the vaginal vault. In addition, a left ovarian endometrioma was also found. The unicornuate uterus was resected with an intent to resolve the pain. Endometriosis is known to raise the risk of ovarian cancer by 50%. Therefore, a left salpingo-oophorectomy was performed to minimize the risk of ovarian cancer and endometriosis recurrence. In conclusion, ovarian endometriomas should be suspected when obstructive malformations are present with active endometrial remnants. These lesions should be managed appropriately to optimize the postoperative outcomes.

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