Faculty Opinions recommendation of Pulmonary arterial hypertension: a rare complication of primary Sjögren syndrome: report of 9 new cases and review of the literature.

2007 ◽  
Author(s):  
Jay H Ryu
Keyword(s):  
Pulmonary Arterial Hypertension ◽  
Arterial Hypertension ◽  
Rare Complication ◽  
Sjögren Syndrome ◽  
Sjogren Syndrome ◽  
Review Of The Literature ◽  
Primary Sjögren Syndrome ◽  
Pulmonary Arterial ◽  
Syndrome Report

Pulmonary Arterial Hypertension: A Rare Complication of Primary Sjögren Syndrome

Medicine ◽  
2007 ◽  
Vol 86 (5) ◽  
pp. 299-315 ◽  
Author(s):  
David Launay ◽  
Eric Hachulla ◽  
Pierre-Yves Hatron ◽  
Xavier Jais ◽  
Gérald Simonneau ◽  
...  
Keyword(s):  
Pulmonary Arterial Hypertension ◽  
Arterial Hypertension ◽  
Rare Complication ◽  
Sjögren Syndrome ◽  
Sjogren Syndrome ◽  
Primary Sjögren Syndrome ◽  
Pulmonary Arterial

THU0294 Pulmonary Arterial Hypertension Complicating Primary Sjogren Syndrome: A Rare Association

2013 ◽  
Vol 72 (Suppl 3) ◽  
pp. A265.2-A265
Author(s):  
B. M. Lynch ◽  
V. Sobanski ◽  
C. E. Handler ◽  
B. E. Schreiber ◽  
C. P. Denton ◽  
...  
Keyword(s):  
Pulmonary Arterial Hypertension ◽  
Arterial Hypertension ◽  
Sjögren Syndrome ◽  
Sjogren Syndrome ◽  
Rare Association ◽  
Primary Sjögren Syndrome ◽  
Pulmonary Arterial

scholarly journals Left main coronary artery compression by pulmonary artery aneurism in patients with long standing pulmonary arterial hypertension

Kardiologiia ◽  
2018 ◽  
Vol 58 (11S) ◽  
pp. 22-32 ◽  
Author(s):  
M. A. Simakova ◽  
N. V. Marukyan ◽  
K. D. Gukov ◽  
D. A. Zverev ◽  
O. M. Moiseeva
Keyword(s):  
Coronary Artery ◽  
Pulmonary Arterial Hypertension ◽  
Pulmonary Artery ◽  
Arterial Hypertension ◽  
Rare Complication ◽  
Oral Anticoagulants ◽  
Clinical Manifestations ◽  
Concomitant Treatment ◽  
Coronary Syndrome ◽  
Pulmonary Arterial

This review focuses on a rare complication of pulmonary arterial hypertension (PAH), extravasation compression of the left coronary artery (LCA) dilated by the pulmonary artery. The review described clinical manifestations and methods for diagnostics of LCA compression, and advantages of the endovascular correction of this complication in patients with pulmonary hypertension. Selection of a device to be implanted during the endovascular intervention in these patients was discussed with due account for concomitant treatment with oral anticoagulants. As an illustration of the issue under discussion, a clinical case of acute coronary syndrome in a female patient from the PAH Registry of the V. A. Almazov National Medical Research Center was provided.

scholarly journals Central airway compression by massively dilated pulmonary artery in a patient with pulmonary arterial hypertension: a rare entity

2019 ◽  
Vol 12 (11) ◽  
pp. e232468
Author(s):  
Biplab Kumar Saha ◽  
Scott Beegle
Keyword(s):  
Pulmonary Arterial Hypertension ◽  
Pulmonary Artery ◽  
Arterial Hypertension ◽  
Left Main Coronary Artery ◽  
Rare Complication ◽  
Unexpected Death ◽  
Pulmonary Arterial ◽  
Central Airway ◽  
Ventilatory Limitation

Patients with pulmonary arterial hypertension (PAH) usually die from progressive right ventricular failure. Mechanical complications due to pulmonary artery (PA) enlargement are rare and include tracheobronchial and left main coronary artery compression, and PA dissection. A 62-year-old female with PAH was seen in our office for follow-up. During the evaluation, spirometry was performed, which revealed a severe obstructive ventilatory limitation. Subsequent workup identified compression of bilateral mainstem bronchi from the dilated PA as the aetiology for the abnormal spirometry. Very few cases of this rare complication have been reported in the literature. A significant dilation of the PA is necessary (>4 cm) for the occurrence of these complications. Dilation of PA is an independent risk factor for sudden unexpected death in patients with PAH.

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