UNUSUAL PRESENTATION OF PRIMARY PLEOMORPHIC RHABDOMYOSARCOMA OF HEART: COMPLETE ATRIOVENTRICULAR BLOCK AND SEVERE MITRAL REGURGITATION

2021 ◽  
pp. 69-70
Author(s):  
G.Sandeep Kumar* ◽  
G. Pranoy ◽  
A. Ashok Raju ◽  
K.C. Karthik Naidu ◽  
P.Sampath Kumar

Primary cardiac tumours are rare and difcult to diagnose because most are asymptomatic or have varied non-specic presentations. This report describes a 29-year-old man presenting with complete heart block, primary cardiac tumour in the left atrium, and severe mitral regurgitation. In view of the primary severe mitral regurgitation and complete heart block, mitral valve repair and pacemaker insertion were planned. Mitral valve repair was done with 29mm St Jude tailor annuloplasty ring, and the biopsy was taken from the nodules noted in the left atrium; temporary right ventricular epicardial pacemaker implantation and CABG with SVG to PDA graft were done to look for the recovery of complete heart block. Histopathological examination revealed pleomorphic rhabdomyosarcoma. The patient developed renal failure and liver failure during the postoperative period and expired after 10 days

2012 ◽  
Vol 93 (6) ◽  
pp. e165
Author(s):  
Mohammad Q. Najib ◽  
Hari P. Chaliki ◽  
Satya S. Vittala ◽  
Amol Raizada ◽  
Roger L. Click

2020 ◽  
Vol 47 (3) ◽  
pp. 207-209
Author(s):  
Anil Ozen ◽  
Ertekin Utku Unal ◽  
Hamdi Mehmet Ozbek ◽  
Gorkem Yigit ◽  
Hakki Zafer Iscan

Determining the optimal length of artificial chordae tendineae and then effectively securing them is a major challenge in mitral valve repair. Our technique for measuring and stabilizing neochordae involves tying a polypropylene suture loop onto the annuloplasty ring. We used this method in 4 patients who had moderate-to-severe mitral regurgitation from degenerative posterior leaflet (P2) prolapse and flail chordae. Results of intraoperative saline tests and postoperative transesophageal echocardiography revealed only mild insufficiency. One month postoperatively, echocardiograms showed trivial regurgitation in all 4 patients. We think that this simple, precise method for adjusting and stabilizing artificial chordae will be advantageous in mitral valve repair.


Author(s):  
Abu Ghosh Z ◽  
◽  
Beeri R ◽  
Falah B ◽  
Pertz A ◽  
...  

Oncology patients with Heart Failure (HF) and severe Mitral Regurgitation (MR) are often considered to have a prohibitive risk for surgical mitral valve repair/replacement. We describe a patient with active multiple myeloma and significant HF and MR who was treated with MitraClip, which improved symptoms and allowed delivery of optimal oncological treatment.


2019 ◽  
Vol 14 (1) ◽  
Author(s):  
Daisuke Kaneyuki ◽  
Hiroyuki Nakajima ◽  
Toshihisa Asakura ◽  
Akihiro Yoshitake ◽  
Chiho Tokunaga ◽  
...  

Abstract Background Good mid-term durability of mitral valve repair of bileaflet lesions has been reported; however, patients may develop failure during follow-up. This study assessed late outcomes and mechanisms of failure associated with mitral valve repair of bileaflet lesions. Methods Fifty-six patients (mean age 67 ± 12 years) underwent mitral valve repair of bileaflet lesions due to degenerative disease in 2011–2018. Mitral annuloplasty was added to all procedures except for 1 patient with annular calcification. Mitral valve lesions were identified by surgical inspection. Mean clinical and echocardiography follow-up occurred at 2.7 ± 2.1 and 2.5 ± 1.9 years, respectively. Results Additional mitral valve repair techniques involved triangular resection (n = 15 patients), quadrangular resection with sliding plasty (n = 12), neochordoplasty (n = 52), and commissural plication (n = 26). Prolapse of ≥2 anterior and posterior leaflet scallops occurred in 22 (39%) and 30 (54%) patients, respectively. During follow-up, 10 (17.8%) patients developed moderate or severe mitral regurgitation. Whereas prolapse or tethering was observed early after neochordoplasty or quadrangular resection, recurrent regurgitation occurred late after commissural repair. Five-year freedom from recurrent moderate or severe mitral regurgitation rates was 71.1 ± 11.0%. Conclusions Seventeen percent of patients developed recurrent mitral regurgitation during follow-up. Repair failure in the early phase occurred owing to aggressive resection of the posterior mitral leaflet or maladjustment of the artificial neochordae. Recurrent mitral regurgitation might occur in the late phase even after acceptable commissural repair. A sequential approach may be useful to improve the quality of mitral valve repair in bileaflet lesions.


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