DESMOPLASTIC SMALL ROUND CELL TUMOR: A CASE REPORT

2021 ◽  
pp. 7-8
Author(s):  
Bhuwan Kumar ◽  
Rajde Singh ◽  
Anurag Mishra
Keyword(s):  
Young Adults ◽  
Case Report ◽  
Poor Prognosis ◽  
Malignant Neoplasm ◽  
Cell Tumor ◽  
Round Cell ◽  
Round Cell Tumor ◽  
Small Round Cell Tumor ◽  
Small Round Cell ◽  
Mesenchymal Tissue

Desmoplastic small round cell tumor is a rare, highly malignant neoplasm originating from mesenchymal tissue which was initially described in 1 1991 by Gerald and Rosai. It is composed of small round tumor cells of uncertain histogenesis associated with prominent stromal desmoplasia and 2 polyphenotypic differentiation. It typically occurs in adolescents and young adults. Usually presents with widespread abdominal, serosal, and mesenteric involvement with poor prognosis.

scholarly journals Desmoplastic small round cell tumor: A case report of a rare differential diagnosis of solid tumors of the pleura

2015 ◽  
Vol 10 (5) ◽  
pp. 2991-2995 ◽  
Author(s):  
YUAN CAO ◽  
YING CHEN ◽  
LI YANG ◽  
ZI-HUA QIAN ◽  
SHU-GAO HAN ◽  
...  
Keyword(s):  
Differential Diagnosis ◽  
Case Report ◽  
Solid Tumors ◽  
Cell Tumor ◽  
Round Cell ◽  
Round Cell Tumor ◽  
Small Round Cell Tumor ◽  
Small Round Cell ◽  
Rare Differential Diagnosis

scholarly journals Desmoplastic small round cell tumor of the abdomen: A case report and literature review of therapeutic options

Health ◽  
2012 ◽  
Vol 04 (04) ◽  
pp. 207-211 ◽  
Author(s):  
Hafida Benhammane ◽  
Leila Chbani ◽  
Abdelmalek Ousadden ◽  
Ouadii Mouquit ◽  
Siham Tizniti ◽  
...  
Keyword(s):  
Case Report ◽  
Literature Review ◽  
Cell Tumor ◽  
Therapeutic Options ◽  
Round Cell ◽  
Round Cell Tumor ◽  
Small Round Cell Tumor ◽  
Small Round Cell

scholarly journals Paraneoplastic secondary hypertension due to a renin-secreting desmoplastic small round cell tumor: A case report

2014 ◽  
Vol 8 (5) ◽  
pp. 1986-1992 ◽  
Author(s):  
HEE-JEONG LEE ◽  
JIN-SOO HYUN ◽  
HOE-SOO JANG ◽  
HYOUNG SUL ◽  
SANG-GON PARK
Keyword(s):  
Case Report ◽  
Secondary Hypertension ◽  
Cell Tumor ◽  
Round Cell ◽  
Round Cell Tumor ◽  
Small Round Cell Tumor ◽  
Small Round Cell

scholarly journals Desmoplastic Small Round Cell Tumor of the Ovary: A Case Report with a New Modality of Treatment and Review of the Literature

2020 ◽  
Vol 42 (05) ◽  
pp. 297-302
Author(s):  
Goran Vujić ◽  
Mislav Mikuš ◽  
Luka Matak ◽  
Aleksandra Bonevski ◽  
Ivan Babić ◽  
...  
Keyword(s):  
Case Report ◽  
English Literature ◽  
Large Population ◽  
Population Based ◽  
Cell Tumor ◽  
Round Cell ◽  
Round Cell Tumor ◽  
Small Round Cell Tumor ◽  
Small Round Cell ◽  
Chemotherapy Protocol

Abstract Objective Desmoplastic small round cell tumor (DSRCT) is a rare intraabdominal neoplasm that grows along serosal surfaces and is primarily found in young men. To date, only 16 cases of ovarian DSRCT have been previously reported in women in the English literature, and no large population-based studies on this topic exist. Case Report We report the case of a 19-year-old virgo with unremarkable past medical history, initially presented with abdominal fullness. After being treated with the optimal treatment modality (primary and secondary surgical debulking, unique chemotherapy, protocol and adjuvant radiotherapy), the patient has remained without tumor disease for 40 months. Conclusion Although the best therapy for patients with DSRCT has yet to be determined, combining complete surgical resection, adjuvant chemotherapy, and radiotherapy is required to prolong survival and to achieve proper quality of life.

Desmoplastic Small Round Cell Tumor: A Rare but Aggressive Tumor in Young Women

2016 ◽  
Vol 8 (3) ◽  
pp. 239-242
Author(s):  
K Harish ◽  
G Nandini ◽  
K Padma ◽  
ACV Swamy ◽  
Murali Subramanian
Keyword(s):  
Young Women ◽  
Abdominal Cavity ◽  
Malignant Neoplasm ◽  
Cell Tumor ◽  
Round Cell ◽  
Female Ratio ◽  
Round Cell Tumor ◽  
Small Round Cell Tumor ◽  
Small Round Cell ◽  
Aggressive Tumor

ABSTRACT Desmoplastic small round cell tumor (DSRCT) is a rare malignant neoplasm. It is primarily found in young men, with a reported male to female ratio of 4:1. The tumor typically develops in the abdominal cavity, invading the omentum with multiple peritoneal implants involving the diaphragm, splenic hilum, mesentery of the small and large bowel, and the pelvic peritoneum. Most of them have widespread disease at presentation, with an organ of origin difficult to ascertain. We report a case of desmoplastic round cell tumor in a 17-year-old teenage girl. Immunohistochemistry helped in the diagnosis. She received multimodality treatment. How to cite this article Nandini G, Harish K, Swamy ACV, Subramanian M, Padma K. Desmoplastic Small Round Cell Tumor: A Rare but Aggressive Tumor in Young Women. J South Asian Feder Obst Gynae 2016;8(3):239-242.

scholarly journals Removal of an intra-abdominal desmoplastic small round cell tumor by repetitive debulking surgery: A case report and literature review

2014 ◽  
Vol 7 (5) ◽  
pp. 1464-1468 ◽  
Author(s):  
JIRO SHIMAZAKI ◽  
GYO MOTOHASHI ◽  
KIYOTAKA NISHIDA ◽  
TAKANOBU TABUCHI ◽  
HIDEYUKI UBUKATA ◽  
...  
Keyword(s):  
Case Report ◽  
Literature Review ◽  
Cell Tumor ◽  
Round Cell ◽  
Debulking Surgery ◽  
Round Cell Tumor ◽  
Small Round Cell Tumor ◽  
Small Round Cell
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