Mucormycosis of the temporal bone with facial nerve palsy: A rare case report

Paragangliomas are rare, most commonly non-malignant tumors of the autonomic nervous system. Their location within the head is rather an exception than a rule, similarly as their multifocal prevalence. The authors of this paper present a case of a patient with bi-focal paraganglioma. The first symptom of illness was facial nerve palsy, diagnosed for the period of about 3 years. After making the initial diagnosis of tympanic paraganglioma, the tumor was operated. During the next 7 years, there was a reccurence within the temporal bone. What is more, periodic imaging examination showed a second foci within the neck, moreover asymptomatic. The authors discuss the natural development of paragangliomas in the region of head and neck and present the current knowledge about management of patients with a suspicion, diagnosis and treatment of this disease.

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Recurrent phosphaturic mesenchymal tumour of the temporal bone causing deafness and facial nerve palsy

The Journal of Laryngology & Otology ◽

10.1017/s0022215112000989 ◽

2012 ◽

Vol 126 (7) ◽

pp. 721-724 ◽

Cited By ~ 5

Author(s):

M I Syed ◽

M Chatzimichalis ◽

M Rössle ◽

A M Huber

Keyword(s):

Case Report ◽

Connective Tissue ◽

Facial Nerve ◽

Temporal Bone ◽

Nerve Palsy ◽

Facial Nerve Palsy ◽

Early Recognition ◽

Mesenchymal Tumour ◽

Radiological Investigation ◽

Phosphaturic Mesenchymal Tumour

AbstractObjective:We describe the first reported case of a phosphaturic mesenchymal tumour, mixed connective tissue variant, invading the temporal bone.Case report:A female patient presented with increasing deafness. On examination there appeared to be a mass behind an intact tympanic membrane. Further radiological investigation showed a vascular mass occupying the middle ear, mastoid and internal auditory meatus. This was surgically resected and revealed to be a benign phosphaturic mesenchymal tumour, mixed connective tissue variant. The tumour recurred a year later, presenting as facial nerve palsy. A revision procedure was carried out; the tumour was excised with the sacrifice of a segment of the facial nerve, and a facial-hypoglossal nerve anastomosis was performed.Conclusion:This case report highlights the occurrence of this benign but sometimes aggressive tumour, of which both clinicians and pathologists should be aware. Early recognition of the condition remains of utmost importance to minimise the debilitating consequences of long-term osteomalacia in affected patients, and to prevent extracranial and intracranial complications caused by the tumour.

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Case Report: Case report: A rare case of middle-ear Rhabdomyosarcoma in a 4-year-old boy

F1000Research ◽

10.12688/f1000research.20558.1 ◽

2019 ◽

Vol 8 ◽

pp. 1734

Author(s):

Richard Menzies-Wilson ◽

Gentle Wong ◽

Prodip Das

Keyword(s):

Case Report ◽

Facial Nerve ◽

Middle Ear ◽

Rare Case ◽

Nerve Palsy ◽

Facial Nerve Palsy ◽

Excisional Biopsy ◽

Embryonal Rhabdomyosarcoma ◽

Aural Polyp ◽

The Right

We present a rare case of a four-year-old boy with a botyroid embryonal rhabdomyosarcoma of the right middle ear. Rhabdomyosarcoma is a soft tissue malignancy which is thought to originate from embryonic mesenchymal cells of striated skeletal muscle. It is a disease primarily of children and is exceptionally rare in parameningeal regions. The diagnosis is often delayed and easily misdiagnosed as aural polyp. Therefore, advanced disease is common at the time of diagnosis. A four-year-old boy presented with a four-month history of recurrent left ear blood and pus discharge, otalgia and fevers. He attended his GP three times and paediatric A&E 13 times where he received antibiotics for presumed otitis media and externa. He was eventually referred to the otolaryngology department and underwent an examination under anaesthesia of ear and excisional biopsy of a suspicious aural polyp. Staging chest CT and PET scan showed no loco-regional spread or distal metastasis. Magnetic resonance imaging demonstrated absence of invasion into adjacent organs. Histology confirmed embryonal rhabdomyosarcoma, botryoid subtype. Subsequent to the initial excision of the polyp, he was started on an ifosfamine, vincristine and actinomycin (IVA) chemotherapy regime in three weekly cycles for nine cycles with concomitant radiotherapy. Two weeks subsequent to his first chemotherapy dose he presented with a House-Brackmann II-III facial nerve palsy but no other middle ear complications. He was started on intravenous antibiotics and dexamethasone. The facial nerve palsy incompletely resolved with treatment.

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Case Report: Case report: A rare case of middle-ear Rhabdomyosarcoma in a 4-year-old boy

F1000Research ◽

10.12688/f1000research.20558.2 ◽

2019 ◽

Vol 8 ◽

pp. 1734

Author(s):

Richard Menzies-Wilson ◽

Gentle Wong ◽

Prodip Das

Keyword(s):

Case Report ◽

Facial Nerve ◽

Middle Ear ◽

Rare Case ◽

Nerve Palsy ◽

Facial Nerve Palsy ◽

Excisional Biopsy ◽

Embryonal Rhabdomyosarcoma ◽

Aural Polyp ◽

The Right

We present a rare case of a four-year-old boy with a botyroid embryonal rhabdomyosarcoma of the right middle ear. Rhabdomyosarcoma is a soft tissue malignancy which is thought to originate from embryonic mesenchymal cells of striated skeletal muscle. It is a disease primarily of children and is exceptionally rare in parameningeal regions. The diagnosis is often delayed and easily misdiagnosed as aural polyp. Therefore, advanced disease is common at the time of diagnosis. A four-year-old boy presented with a four-month history of recurrent left ear blood and pus discharge, otalgia and fevers. He attended his GP three times and paediatric A&E 13 times where he received antibiotics for presumed otitis media and externa. He was eventually referred to the otolaryngology department and underwent an examination under anaesthesia of ear and excisional biopsy of a suspicious aural polyp. Staging chest CT and PET scan showed no loco-regional spread or distal metastasis. Magnetic resonance imaging demonstrated absence of invasion into adjacent organs. Histology confirmed embryonal rhabdomyosarcoma, botryoid subtype. Subsequent to the initial excision of the polyp, he was started on an ifosfamine, vincristine and actinomycin (IVA) chemotherapy regime in three weekly cycles for nine cycles with concomitant radiotherapy. Two weeks subsequent to his first chemotherapy dose he presented with a House-Brackmann II-III facial nerve palsy but no other middle ear complications. He was started on intravenous antibiotics and dexamethasone. The facial nerve palsy incompletely resolved with treatment.

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A Case of Recurrent Facial Palsy Associated with Anti-GM2: is it anyway Guillain-barré syndrome?

International Journal of Case Reports ◽

10.28933/ijcr-2021-04-0505 ◽

2021 ◽

pp. 215

Author(s):

Keyword(s):

Case Report ◽

Family History ◽

Facial Nerve ◽

Rare Case ◽

Nerve Palsy ◽

Facial Nerve Palsy ◽

Neurological Diseases ◽

Facial Paresis ◽

Her Family ◽

Autoimmune Neuropathy

Objective: A rare case of possible hereditary predisposition to autoimmune neuropathy Background: This case report is of a patient who presented two episodes of Facial paresis in her live without ascertained apparent causes. Bell’s palsy is commonly known as peripheral idiopathic facial nerve palsy, because in the most cases the triggers remain unknown (1). Case Report: I want to present a case of a 34 year old woman who we will call A.B. and who came to us to evaluate the severity of the sequelae of a Bell´s palsy and any eventual need for cosmetic measure. But she had another Bell´s Palsy 9 years ago, so I started to investigate the most common and treatable causes of Facial paresis. I found a significate increase of anti-bodies against ganglioside GM2. When I explained to her that these anti-bodies is commonly related with several neurological diseases, she started to investigate her family history and she found that his father’s brother died of GuillainBarré syndrome about 40 years ago.

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